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Dermatologic Differential Diagnosis.pdf. - Famona Site

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682 A CLINICIAN’S GUIDE TO DERMATOLOGIC DIFFERENTIAL DIAGNOSIS, VOLUME 1<br />

Heparin necrosis AD 132:341–346, 1996<br />

Hepatitis C – cryoglobulinemia – thrombotic and/or<br />

leukocytoclastic vasculitis AD 131:1119–1123, 1995<br />

Ischemic ulcers of hematologic origin<br />

Hereditary spherocytosis<br />

Hemolytic anemia<br />

Sickle cell SS<br />

Polycythemia vera<br />

Livedoid vasculitis<br />

Lupus anticoagulant JAAD 19:117, 1988<br />

Paroxysmal nocturnal hemoglobulinuria<br />

Protein C deficiency<br />

Protein S deficiency<br />

Purpura fulminans<br />

Sickle-cell disease<br />

Sneddon–Wilkinson disease<br />

Thrombocythemia JAAD 24:59, 1991<br />

Thrombotic thrombocytopenic purpura<br />

Waldenström’s hyperglobulinemic purpura<br />

VASCULITIS, TYPES<br />

AD 130:899–906, 1994<br />

Direct infections of vessels<br />

Bacterial vasculitis (neisserial)<br />

Fungal (mucor)<br />

Mycobacterial (tuberculosis)<br />

Rickettsial vasculitis (Rocky Mountain spotted fever)<br />

Spirochetal<br />

Viral<br />

Immunologic injury<br />

ANCA-associated or ANCA-mediated<br />

Churg–Strauss disease<br />

Some drug-induced (thiouracil)<br />

Microscopic polyarteritis nodosa<br />

Wegener’s granulomatosis<br />

Cell-mediated<br />

Direct antibody attack – mediated<br />

Goodpasture’s sydrome (anti-basement membrane<br />

antibodies)<br />

Kawasaki’s disease (?anti-endothelial antibodies)<br />

Immune complex<br />

Behçet’s disease<br />

Cryoglobulins<br />

Some drug-induced vasculitis (sulfonamides)<br />

Erythema elevatum diutinum<br />

Henoch–Schönlein purpura<br />

Infection-induced immune complex vasculitis<br />

Bacterial (Streptococcus)<br />

Viral (hepatitis B and C)<br />

Lupus erythematosus<br />

Paraneoplastic vasculitis<br />

Rheumatoid arthritis – nodules, pyoderma gangrenosumlike,<br />

digital gangrene, ulcers, petechiae, purpura,<br />

mononeurits multiplex<br />

Serum sickness vasculitis<br />

Heterologous proteins<br />

Whole serum<br />

Unknown<br />

Allograft acute cellular vascular rejection<br />

Pyoderma gangrenosum-like, nodules, erythema<br />

nodosum-like, Raynaud’s phenomenon<br />

Erythema nodosum<br />

Giant cell arteritis<br />

Polyarteritis nodosa<br />

Takayasu’s arteritis<br />

POLYMORPHONUCLEAR<br />

Allergic vasculitis<br />

Erythema elevatum diutinum – localized; HIV-associated<br />

Henoch–Schönlein purpura<br />

HIV-associated<br />

Sweet’s syndrome<br />

Zeek’s hypersensitivity vasculitis<br />

Collagen vascular disease<br />

Erythema nodosum (early)<br />

Bowel-associated dermatitis–arthritis syndrome<br />

Behçet’s syndrome<br />

Urticarial vasculitis<br />

LYMPHOCYTIC<br />

Drug reaction<br />

Erythema multiforme<br />

Erythema nodosum<br />

Pityriasis lichenoides et varioliformis acuta<br />

Dysproteinemia – macroglobulinemia<br />

Degos’ disease – idiopathic, HIV-associated JAAD 38:852–856,<br />

1998<br />

Lupus erythematosus – lymphocytic large vessel vasculitis<br />

Rook p.2156, 1998, Sixth Edition<br />

Macroglobulinemia<br />

Malignant atrophic papulosis<br />

Perniosis<br />

GRANULOMATOUS VASCULITIS<br />

SYSTEMIC<br />

Wegener’s granulomatosis<br />

Churg–Strauss disease<br />

Infections – Hansen’s disease, tuberculosis, syphilis,<br />

HIV-associated<br />

Lymphomatoid granulomatosis (angiocentric T-cell lymphoma)<br />

Polyarteritis nodosa – including HIV-associated<br />

FOCAL<br />

Lethal midline granuloma<br />

Eosinophilic and necrotizing focal granuloma<br />

Cogan’s syndrome<br />

Granuloma faciale<br />

Nodular vasculitis<br />

LARGE VESSEL VASCULITIS<br />

POLYMORPHONUCLEAR<br />

Polyarteritis nodosa<br />

Superficial migratory thrombophlebitis<br />

Lymphangitis

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