Vascular Malformations Smith 12-12-2012 - Inova Health System
Vascular Malformations Smith 12-12-2012 - Inova Health System
Vascular Malformations Smith 12-12-2012 - Inova Health System
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2/8/20<strong>12</strong><br />
Hereditary Hemorrhagic<br />
Telangiectasia<br />
>3 concurrent cerebral AVMS –Rare!<br />
An angiodyplastic disorder with AD inheritance<br />
AVM<br />
• Dysregulated<br />
angiogenesis <br />
continued vascular<br />
remodeling<br />
• Peak age: 20-40 year<br />
old<br />
• Risk of hemorrhage: 2-<br />
4%/year<br />
– ~50% present with<br />
symptoms of<br />
hemorrhage<br />
NECT<br />
AVM Grading: Spetzler -Martin<br />
Scale<br />
• Size<br />
– Small (6 cm) = 3<br />
• Location<br />
– Noneloquent = 0<br />
– Eloquent = 1<br />
• Venous drainage<br />
– Superficial = 0<br />
– Deep = 1<br />
3