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ultrasound diagnosis of fatal anomalies

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ABDOMEN

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smaller omphaloceles, vaginal delivery is

possible and here there is no indication for cesarean

delivery.

Procedure after birth: The omphalocele should

be covered immediately with a sterile plastic bag

to avoid fluid loss. A nasogastric tube should be

placed to remove stomach contents. Early surgical

intervention within the first week. The earlier

practice of smearing a sterile antiseptic solution

on the lesion and delaying surgical intervention

has ceased to be used except in rare

cases of an extremely large omphalocele.

Prognosis: This is determined by the presence of

associated anomalies and the extent of the lesion.

The overall survival lies between 30–70%.

In a small isolated case of omphalocele, the prognosis

is very good (mortality below 5%). The

mortality increases considerably ( 30%) if the

defect is large ( 5 cm in the second trimester)

and if the liver is prolapsed, even if no other

anomalies are present.

Information for the mother: Surgical correction

is very successful nowadays. If rare cases of large

lesions with liver protrusion, associated malformations

and chromosomal anomalies are excluded,

then the long-term survival of the infant

is very good, without significant long-term impairment.

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