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Pneumoniile de hipersensibilitate. Fibroza chistică.

Pneumoniile de hipersensibilitate. Fibroza chistică.

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Volumul <strong>de</strong> liq <strong>de</strong> la suprafata CAI<br />

CFTR normala inhiba si un canal <strong>de</strong> Na<br />

CFTR mutanta----canal ne-inhibat<br />

Absorbtia Na e crescuta<br />

Apa urmeaza Na<br />

Volumul liq supraf CAI sca<strong>de</strong><br />

CFTR normala --- Cl- e secretat atunci cind Vol<br />

liq supraf CAI e mic<br />

CFTR mutanta --- Cl- nu e secretat

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