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Boli endocrine, de nutritie si metabolism

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Capitolul IV<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong><br />

<strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

(E00-E89)<br />

Acest capitol contine urmatoarele<br />

blocuri:<br />

E00 - E07 Afectiunile glan<strong>de</strong>i tiroi<strong>de</strong><br />

E09 - E14 Reglementarea intolerantei la<br />

glucoza <strong>si</strong> diabetul mellitus<br />

E15 - E16 Alte tulburari ale<br />

<strong>metabolism</strong>ului glucozei <strong>si</strong> ale<br />

secretiei pancreatice interne<br />

E20 - E35 <strong>Boli</strong>le altor glan<strong>de</strong> <strong>endocrine</strong><br />

E40 - E46 Malnutritia<br />

E50 - E64 Alte carente nutritionale<br />

E65 - E68 Obezitatea <strong>si</strong> alte tulburari prin<br />

exces <strong>de</strong> aport<br />

E70 – E89 Tulburari <strong>de</strong> <strong>metabolism</strong><br />

Categoriile cu asterisc <strong>de</strong> la acest<br />

capitol sunt urmatoarele:<br />

E35* Tulburari ale glan<strong>de</strong>lor<br />

<strong>endocrine</strong> in boli cla<strong>si</strong>ficate<br />

altun<strong>de</strong>va<br />

Nota: Toate tumorile, indiferent daca sunt<br />

active sau nu in mod functional, sunt<br />

cla<strong>si</strong>ficate la Capitolul II. Codurile<br />

a<strong>de</strong>cvate din acest capitol (adica<br />

E05.8, E07.0, E16-E31, E34.-) pot fi<br />

folo<strong>si</strong>te, daca se doreste, drept coduri<br />

aditionale pentru a indica fie<br />

activitatea functionala a unei tumori<br />

maligne <strong>si</strong> tesut endocrin ectopic, fie<br />

hiperfunctia <strong>si</strong> hipofunctia glan<strong>de</strong>lor<br />

<strong>endocrine</strong> asociate cu tumorile<br />

maligne <strong>si</strong> alte afectiuni cla<strong>si</strong>ficate<br />

altun<strong>de</strong>va.<br />

Exclu<strong>de</strong>: complicatii ale sarcinii, nasterii <strong>si</strong> lauziei<br />

(O00-O99)<br />

<strong>si</strong>mptome, semne <strong>si</strong> rezultate clinice <strong>si</strong><br />

<strong>de</strong> laborator anormale, necla<strong>si</strong>ficate<br />

altun<strong>de</strong>va (R00-R99)<br />

tulburari tranzitorii <strong>endocrine</strong> <strong>si</strong><br />

metabolice specifice fatului <strong>si</strong> nounascutului<br />

(P70-P74)<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

Afectiunile glan<strong>de</strong>i tiroi<strong>de</strong><br />

(E00-E07)<br />

E00 Sindromul <strong>de</strong>ficientei congenitale <strong>de</strong><br />

iod<br />

Folo<strong>si</strong>ti codul aditional (F70-F79) pentru a<br />

i<strong>de</strong>ntifica orice intarziere mentala asociata.<br />

Inclu<strong>de</strong>: afectiuni en<strong>de</strong>mice asociate cu<br />

<strong>de</strong>ficienta <strong>de</strong> iod a mediului,<br />

fie direct, fie ca o consecinta<br />

a <strong>de</strong>ficientei <strong>de</strong> iod materne.<br />

Unele dintre afectiuni nu au o<br />

hipotiroidie curenta, dar sunt<br />

consecinta secretiei anormale<br />

a hormonului tiroidian in<br />

<strong>de</strong>zvoltarea fatului. Gusa<br />

datorita mediului poate fi<br />

asociata.<br />

Exclu<strong>de</strong>: hipotiroidie prin carenta<br />

subclinica in iod (E02)<br />

E00.0 Sindromul <strong>de</strong>ficientei congenitale <strong>de</strong> iod<br />

<strong>de</strong> tip neurologic<br />

Cretinism e<strong>de</strong>mic <strong>de</strong> tip neurologic<br />

E00.1 Sindromul <strong>de</strong>ficientei congenitale <strong>de</strong> iod<br />

<strong>de</strong> tip mixe<strong>de</strong>matos<br />

Cretinism en<strong>de</strong>mic:<br />

- hipotiroidian<br />

- tip mixe<strong>de</strong>matos<br />

E00.2 Sindromul <strong>de</strong>ficientei congenitale <strong>de</strong> iod<br />

<strong>de</strong> tip mixt<br />

Cretinism en<strong>de</strong>mic <strong>de</strong> tip mixt<br />

E00.9 Sindromul <strong>de</strong>ficientei congenitale <strong>de</strong> iod,<br />

nespecificat<br />

Hipotiroidia prin <strong>de</strong>ficienta congenitala <strong>de</strong><br />

iod NOS<br />

Cretinism en<strong>de</strong>mic NOS<br />

E01 Tulburari tiroidiene <strong>si</strong> afectiuni<br />

inrudite legate <strong>de</strong> <strong>de</strong>ficienta <strong>de</strong> iod<br />

Exclu<strong>de</strong>: <strong>si</strong>ndromul <strong>de</strong>ficientei congenitale<br />

<strong>de</strong> iod (E00.-)<br />

hipotiroidia prin carenta<br />

subclinica <strong>de</strong> iod (E02)<br />

E01.0 Gusa difuza (en<strong>de</strong>mica) legata <strong>de</strong><br />

carenta <strong>de</strong> iod<br />

E01.1 Gusa multinodulara (en<strong>de</strong>mica) legata <strong>de</strong><br />

o carenta <strong>de</strong> iod<br />

Gusa nodulara legata <strong>de</strong> carenta <strong>de</strong> iod<br />

E01.2 Gusa (en<strong>de</strong>mica) legata <strong>de</strong> carenta <strong>de</strong><br />

iod, nespecificata<br />

Gusa en<strong>de</strong>mica NOS<br />

E01.8 Alte afectiuni tiroidiene <strong>si</strong> inrudite legate<br />

<strong>de</strong> carenta <strong>de</strong> iod<br />

Hipotiroidia prin carenta <strong>de</strong> iod dobandita<br />

NOS<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 71


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E02<br />

72<br />

Hipotiroidia prin carenta subclinica<br />

<strong>de</strong> iod<br />

E03 Alte hipotiroidii<br />

Exclu<strong>de</strong>: hipotiroidia legata <strong>de</strong> o carenta<br />

<strong>de</strong> iod (E00-E02)<br />

hipotiroidia postprocedurala<br />

(E89.0)<br />

E03.0 Hipotiroidia congenitala, cu gusa difuza<br />

Gusa (nontoxica) congenitala:<br />

- NOS<br />

- parenchimatoasa<br />

Exclu<strong>de</strong>: gusa congenitala tranzitorie cu<br />

functiune normala (P72.0)<br />

E03.1 Hipotiroidia congenitala fara gusa<br />

Aplazia tiroi<strong>de</strong>i (cu mixe<strong>de</strong>m)<br />

Congenitala:<br />

- atrofia tiroi<strong>de</strong>i<br />

- hipotiroidia NOS<br />

E03.2 Hipotiroidia datorita unor medicamente <strong>si</strong><br />

altor substante exogene<br />

Folo<strong>si</strong>ti un cod <strong>de</strong> cauza externa (Capitolul<br />

XX) pentru a i<strong>de</strong>ntifica cauza.<br />

E03.3 Hipotiroidia postinfectioasa<br />

E03.4 Atrofia tiroi<strong>de</strong>i (dobandita)<br />

Exclu<strong>de</strong>: atrofia congenitala a tiroi<strong>de</strong>i<br />

(E03.1)<br />

E03.5 Coma mixe<strong>de</strong>matoasa<br />

E03.8 Alte hipotiroidii specificate<br />

E03.9 Hipotiroidia, nespecificata<br />

Mixe<strong>de</strong>m NOS<br />

E04 Alte guse netoxice<br />

Exclu<strong>de</strong>: gusa congenitala:<br />

- difuza (E03.0)<br />

- NOS (E03.0)<br />

- parenchimatoasa (E03.0)<br />

gusa legata <strong>de</strong> o carenta <strong>de</strong> iod<br />

(E00-E02)<br />

E04.0 Gusa difuza netoxica<br />

Gusa, netoxica:<br />

- difuza (coloida)<br />

- <strong>si</strong>mpla<br />

E04.1 Nodul tiroidian unic, netoxic<br />

Nodul coloid (chistic) (tiroidian)<br />

Gusa uninodulara netoxica<br />

Nodul tiroidian (chistic) NOS<br />

E04.2 Gusa multinodulara netoxica<br />

Gusa chistica NOS<br />

Gusa multinodulara (chistica) NOS<br />

E04.8 Alte guse netoxice, specificate<br />

E04.9 Gusa netoxica, nespecificata<br />

Gusa NOS<br />

Gusa nodulara (nontoxica) NOS<br />

E05 Tireotoxicoza [hipertiroidia]<br />

Exclu<strong>de</strong>: tiroidita cronica cu tireotoxicoza<br />

tranzitorie (E06.2)<br />

tireotoxicoza neonatala (P72.1)<br />

E05.0 Tireotoxicoza cu gusa difuza<br />

Gusa exoftalmica sau toxica NOS<br />

Boala Graves<br />

Gusa toxica difuza<br />

E05.1 Tireotoxicoza cu nodul unic tiroidian<br />

Tireotoxicoza cu gusa uninodulara toxica<br />

E05.2 Tireotoxicoza cu gusa multinodulara<br />

toxica<br />

Gusa nodulara toxica NOS<br />

E05.3 Tireotoxicoza datorita tesutului ectopic<br />

tiroidian<br />

E05.4 Tireotoxicoza factica<br />

E05.5 Criza acuta tireotoxica<br />

Folo<strong>si</strong>ti un cod aditional pentru a indica<br />

tipul tereotoxicozei (E05.0-E05.4, E05.8-<br />

E05.9)<br />

E05.8 Alte tireotoxicoze<br />

Supraproductia <strong>de</strong> hormon tiroido-stimulant<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica cauza.<br />

E05.9 Tireotoxicoza, nespecificata<br />

Hipertiroidism NOS<br />

Afectiunea cardiaca tireotoxica† (I43.8*)<br />

E06 Tiroidita<br />

Exclu<strong>de</strong>: tiroidita postpartum (O90.5)<br />

E06.0 Tiroidita acuta<br />

Abces al tiroi<strong>de</strong>i<br />

Tiroidita:<br />

- piogena<br />

- supurata<br />

Folo<strong>si</strong>ti un cod aditional (B95-B97) pentru a<br />

i<strong>de</strong>ntifica agentul infectios.<br />

E06.1 Tiroidita subacuta<br />

Tiroidita:<br />

- <strong>de</strong> Quervain<br />

- celule gigantice<br />

- granulomatoasa<br />

- nonsupurativa<br />

Exclu<strong>de</strong>: tiroidita autoimuna (E06.3)<br />

E06.2 Tiroidita cronica cu tireotoxicoza<br />

tranzitorie<br />

Exclu<strong>de</strong>: tiroidita autoimuna (E06.3)<br />

E06.3 Tiroidita autoimuna<br />

Tiroidita Hashimoto<br />

Hashitoxicoza (tranzitorie)<br />

Gusa limfa<strong>de</strong>noida<br />

Tiroidita limfocitica<br />

Strumita limfomatoasa<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E06.4 Tiroidita provocata <strong>de</strong> medicamente<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul.<br />

E06.5 Alte tiroidite cronice<br />

Tiroidita:<br />

- cronica:<br />

- fibroasa<br />

- NOS<br />

- lemnoasa<br />

- Rie<strong>de</strong>l<br />

E06.9 Tiroidita, nespecificata<br />

E07 Alte afectiuni ale tiroi<strong>de</strong>i<br />

E07.0 Hipersecretia <strong>de</strong> calcitonina<br />

Hiperplazia <strong>de</strong> celule C a tiroi<strong>de</strong>i<br />

Hipersecretia <strong>de</strong> tirocalcitonina<br />

E07.1 Gusa datorita unei tulburari a <strong>si</strong>ntezei<br />

hormonale<br />

Gusa familiala datorita unei tulburari a<br />

<strong>si</strong>ntezei hormonale<br />

Sindromul Pendred<br />

Exclu<strong>de</strong>: gusa congenitala tranzitorie cu<br />

functie normala (P72.0)<br />

E07.8 Alte afectiuni specificate ale tiroi<strong>de</strong>i<br />

Anomalia tiroglobulinei<br />

Hemoragia tiroi<strong>de</strong>i<br />

Infarctul tiroi<strong>de</strong>i<br />

Sindromul disfunctiei eutiroidiene<br />

E07.9 Afectiunea tiroi<strong>de</strong>i, nespecificata<br />

Reglementarea intolerantei la<br />

glucoza <strong>si</strong> diabetul mellitus<br />

(E09-E14)<br />

0401<br />

Nota: Criterii <strong>de</strong> diagnostic:<br />

Criteriile OMS pentru<br />

reglementarea intolerantei la<br />

glucoza (revizuite in 1999):<br />

Testul <strong>de</strong> toleranta bazat pe<br />

administrarea corecta a glucozei pe<br />

cale orala (glucoza plasmatica<br />

recoltata venos pe nemancate 6.1-6.9<br />

mmol/l, sau<br />

glucoza plasmatica venoasa la 2 ore<br />

dupa administarea glucozei orale 7.8-<br />

11.0 mmol/l), sau<br />

nivelul glucozei plasmatice venoase<br />

pe nemancate 6.1-6.9 mmol/l<br />

Criteriile OMS pentru diabet<br />

mellitus (revizuite in 1999):<br />

Testul <strong>de</strong> toleranta bazat pe<br />

administrarea corecta a glucozei pe<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

cale orala (glucoza plasmatica<br />

recoltata venos pe nemancate ≥ 7.0<br />

mmol/l sau glucoza plasmatica<br />

venoasa la 2 ore dupa administrarea<br />

glucozei orale, glucoza plasmatica<br />

venoasa la 2 ore dupa administrarea<br />

glucozei orale ≥ 11.1 mmol/L), sau<br />

Asociatia Americana <strong>de</strong> Diabet<br />

(ADA) - criterii:<br />

Nivelul glucozei plasmatice venoase<br />

pe nemancate ≥ 7.0 mmol/L, sau<br />

Simptomele cla<strong>si</strong>ce <strong>de</strong> sete, poliurie <strong>si</strong><br />

glucoza plasmatica venoasa<br />

randomizata ≥ 11.1 mmol/L.<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica daca este indus<br />

medicamentos sau chimic.<br />

E09<br />

<br />

0401<br />

E09.0<br />

<br />

Reglementarea intolerantei la<br />

glucoza<br />

Folo<strong>si</strong>ti un cod aditional pentru orice<br />

afectiune <strong>de</strong> baza sau <strong>si</strong>ndrom genetic<br />

asociat.<br />

Inclu<strong>de</strong>: Glucoza anormala<br />

(carbohidrati):<br />

- reglementare<br />

- toleranta<br />

Diabet, chimic<br />

Diabet, latent<br />

Intoleranta:<br />

- scazuta a glicemiei pe<br />

nemancate (IFG)<br />

- scazuta la glucoza<br />

(carbohidrati) (IGT)<br />

Prediabet<br />

Exclu<strong>de</strong>: diabet mellitus (E10-E14)<br />

nivel ridicat al glucozei in<br />

sange (R73)<br />

Reglementarea intolerantei la glucoza<br />

cu angiopatie periferica<br />

E09.01 Reglementarea intolerantei la glucoza<br />

cu angiopatie periferica fara gangrena<br />

E09.02 Reglementarea intolerantei la glucoza<br />

cu angiopatie periferica cu gangrena<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 73


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E09.1 Reglementarea intolerantei la glucoza<br />

cu caracteristici <strong>de</strong> rezistenta la<br />

insulina<br />

Reglementarea intolerantei la glucoza cu:<br />

- hiperten<strong>si</strong>une cu:<br />

- orice afectiune <strong>de</strong> mai jos<br />

- obezitate NOS<br />

- <strong>de</strong>pozit <strong>de</strong> gra<strong>si</strong>me viscerala crescut<br />

- rezistenta la insulina NOS<br />

- una sau mai multe din urmatoarele:<br />

- achanto<strong>si</strong>s nigricans<br />

- dislipi<strong>de</strong>mia<br />

- hiperinsulinism<br />

- obezitate (intrunirea criteriilor OMS<br />

sau altele recunoscute)<br />

E09.8 Reglementarea intolerantei la glucoza<br />

cu complicatii nespecificate<br />

E09.9 Reglementarea intolerantei la glucoza<br />

fara complicatii<br />

E10 Diabet mellitus tip 1<br />

Inclu<strong>de</strong>: diabet (mellitus):<br />

74<br />

- autoimun<br />

- fragil<br />

- idiopatic<br />

- insulino-<strong>de</strong>pen<strong>de</strong>nt [IDDM]<br />

- cu <strong>de</strong>but la tineri<br />

- predispus la cetoza<br />

Exclu<strong>de</strong>: diabet mellitus (datorit) (in):<br />

- neonatal (P70.2)<br />

- NOS (E14.-)<br />

- alte forme specificate<br />

(E13.-)<br />

- sarcina, nastere <strong>si</strong> lauzie<br />

(O24.-)<br />

- tip 2 (E11.-)<br />

glicozuria:<br />

- NOS (R81)<br />

- renala (E74.8)<br />

reglementarea intolerantei la<br />

glucoza (E09.-)<br />

hipoinsulinemie<br />

postprocedurala (E89.1)<br />

E10.1 Diabet mellitus tip 1 cu acidoza<br />

E10.11 Diabet mellitus tip 1 cu ketoacidoza,<br />

fara coma<br />

Diabet mellitus tip 1 cu ketoacidoza NOS<br />

E10.12 Diabet mellitus tip 1 cu ketoacidoza,<br />

cu coma<br />

Diabet mellitus tip 1cu coma<br />

hiperglicemica NOS<br />

E10.13 Diabet mellitus tip 1 cu acidoza lactica,<br />

fara coma<br />

Diabet mellitus tip 1 cu acidoza lactica<br />

NOS<br />

E10.14 Diabet mellitus tip 1 cu acidoza lactica,<br />

cu coma<br />

E10.15 Diabet mellitus tip 1 cu ketoacidoza,<br />

cu acidoza lactica, fara coma<br />

Diabet mellitus tip 1 cu ketoacidoza, cu<br />

acidoza lactica NOS<br />

E10.16 Diabet mellitus tip 1 cu ketoacidoza,<br />

cu acidoza lactica, cu coma<br />

E10.2 Diabet mellitus tip 1 cu complicatii<br />

renale<br />

E10.21 Diabet mellitus tip 1 cu nefropatie<br />

diabetica incipienta<br />

Diabet mellitus tip 1 cu:<br />

- glomerular(a):<br />

- membrana bazala ingrosata<br />

- expan<strong>si</strong>une mezangiala<br />

- nefropatie incipienta (timpurie)<br />

(rever<strong>si</strong>bila)<br />

- microalbuminuria:<br />

- constanta<br />

- per<strong>si</strong>stenta<br />

E10.22 Diabet mellitus tip 1 cu nefropatie<br />

diabetica stabilita<br />

Diabet mellitus tip 1 cu:<br />

- glomeruloscleroza:<br />

- difuza<br />

- intracapilara<br />

- nodulara<br />

- Kimmelstiel-Wilson (boala) (leziune)<br />

- macroalbuminuria<br />

- nefropatia (avansata) (NOS)<br />

(progre<strong>si</strong>va)<br />

- proteinuria (fixata) (per<strong>si</strong>stenta)<br />

E10.23 Diabet mellitus tip 1 cu boala renala<br />

stadiu final [ESRD]<br />

Diabet mellitus tip 1 cu insuficienta<br />

renala cronica sau leziune renala cronica<br />

in afectiunile cla<strong>si</strong>ficabile la E10.22<br />

E10.29 Diabet mellitus tip 1 cu alte complicatii<br />

renale specificate<br />

Diabet mellitus tip 1 cu:<br />

- insuficienta renala acuta<br />

- necroza medulara (papilara)<br />

E10.3 Diabet mellitus tip 1 cu complicatii<br />

oculare<br />

E10.31 Diabet mellitus tip 1 cu retinopatie <strong>de</strong><br />

fond<br />

Diabet mellitus tip 1 cu:<br />

- retinal(a):<br />

- hemoragie (cu puncte <strong>si</strong> pete) (sub<br />

forma <strong>de</strong> flacara)<br />

- exudat<br />

- microanevrism<br />

- dilatare venoasa<br />

- retinopatie NOS<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E10.32 Diabet mellitus tip 1 cu retinopatie<br />

preproliferativa<br />

Diabet mellitus tip 1 cu:<br />

- anormalitati microvasculare intraretinale<br />

[IRMA]<br />

- retinal(a):<br />

- pete sub forma vatoasa<br />

- hemoragii (cu pete) (rotun<strong>de</strong>) (mici)<br />

- ischemia<br />

- venos(oasa):<br />

- perlata<br />

- buclata<br />

- dublata<br />

E10.33 Diabet mellitus tip 1 cu retinopatie<br />

proliferativa<br />

Diabet mellitus tip 1 cu:<br />

- hemoragie<br />

- preretinala<br />

- sticloasa<br />

- formare <strong>de</strong> vas nou (neovascularizatie)<br />

- tractiune retinala fara <strong>de</strong>tasare<br />

E10.34 Diabet mellitus tip 1 cu alte retinopatii<br />

Diabet mellitus tip 1 cu:<br />

- macular:<br />

- e<strong>de</strong>m (focal) (generalizat)<br />

(intraretinal)<br />

- sub forma <strong>de</strong> stea<br />

- maculopatie (circinat) (ischemic)<br />

- ingrosare retinala<br />

E10.35 Diabet mellitus tip 1 cu boala oculara<br />

avansata<br />

Diabet mellitus tip 1 cu:<br />

- glaucom neovascular<br />

- rubeoza irisului [rubeo<strong>si</strong>s iridis]<br />

- tractiunea retinei <strong>de</strong>tasate<br />

E10.36 Diabet mellitus tip 1 cu cataracta<br />

diabetica<br />

Exclu<strong>de</strong>: Diabet mellitus tip 1 cu<br />

cataracta cu <strong>de</strong>but la<br />

varsta timpurie (E10.39)<br />

E10.39 Diabet mellitus tip 1 cu alte complicatii<br />

oculare specificate<br />

Diabet mellitus tip 1 cu cataracta cu<br />

<strong>de</strong>but la varsta timpurie<br />

E10.4 Diabet mellitus tip 1 cu cataracta cu<br />

complicatii neurologice<br />

E10.40 Diabet mellitus tip 1 cu neuropatie<br />

nespecificata<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E10.41 Diabet mellitus tip 1 cu<br />

mononeuropatie diabetica<br />

Diabet mellitus tip 1 cu:<br />

- amiotrofie<br />

- paralizia nervului cranian:<br />

- III (oculomotor)<br />

- VI (abductor)<br />

- neuropatie femurala<br />

- mononeurita multipla<br />

- oftalmoplegia<br />

- radiculopatie:<br />

- toracica<br />

- tronculara<br />

E10.42 Diabet mellitus tip 1 cu polineuropatie<br />

diabetica<br />

Diabet mellitus tip 1 cu:<br />

- neurita insulinica<br />

- neuropatie periferica:<br />

- distala <strong>si</strong>metrica<br />

- selectiva 'cu fibre mici'<br />

- senzo-motorie<br />

Exclu<strong>de</strong>: Diabet mellitus tip 1 cu<br />

polineuropatie diabetica<br />

autonoma (E10.43)<br />

E10.43 Diabet mellitus tip 1 cu neuropatie<br />

diabetica autonoma<br />

Diabet mellitus tip 1 cu:<br />

- secretie anormala (gustativa)<br />

- polineuropatie diabetica autonoma<br />

- diareea diabetica<br />

- disfunctie:<br />

- anorectala<br />

- esofagiana<br />

- insuficienta erectila (impotenta)<br />

- gastropareza<br />

- hipotonia, vezica urinara<br />

- e<strong>de</strong>m neuropatic<br />

- hipoten<strong>si</strong>une posturala<br />

E10.49 Diabet mellitus tip 1 cu alte complicatii<br />

neurologice specificate<br />

E10.5 Diabet mellitus tip 1 cu complicatii<br />

circulatorii<br />

E10.51 Diabet mellitus tip 1 cu angiopatie<br />

periferica, fara gangrena<br />

Exclu<strong>de</strong>: Diabet mellitus tip 1 cu<br />

angiopatie periferica, fara<br />

ulceratia piciorului (E10.73)<br />

E10.52 Diabet mellitus tip 1 cu angiopatie<br />

periferica, cu gangrena<br />

Exclu<strong>de</strong>: Diabet mellitus tip 1 cu<br />

angiopatie periferica, cu<br />

gangrena, cu ulceratia<br />

piciorului (E10.73)<br />

E10.53 Diabet mellitus tip 1 cu cardiomiopatie<br />

ischemica diabetica<br />

E10.6 Diabet mellitus tip 1 cu alte complicatii<br />

specificate<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 75


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E10.61 Diabet mellitus tip 1 cu complicatii<br />

diabetice musculoscheletale <strong>si</strong> ale<br />

tesutului conjunctiv specificate<br />

Diabet mellitus tip 1 cu:<br />

- artropatie Charchot<br />

- diabetica/e:<br />

- <strong>si</strong>ndromul mainii (cheiroartropatie)<br />

(contractura Dupuytren) (fibromatoza<br />

fasciala palmara)<br />

- osteopatie<br />

- periartrita umarului<br />

E10.62 Diabet mellitus tip 1 cu complicatii ale<br />

pielii <strong>si</strong> tesutului subcutanat specificate<br />

Diabet mellitus tip 1 cu:<br />

- diabetic(a):<br />

- buloasa [bullo<strong>si</strong>s diabeticorum]<br />

- <strong>de</strong>rmopatie (pete ale pielii)<br />

- eritem<br />

- rubeoza<br />

- sclero<strong>de</strong>rmie<br />

- ingrosarea pielii<br />

- necrobioza lipoidica diabetica [NLD]<br />

- telangiectazie periunghiala<br />

E10.63 Diabet mellitus tip 1 cu complicatii<br />

periodontale specificate<br />

Diabet mellitus tip 1 cu:<br />

- abces periodontal acut<br />

- periodontita<br />

E10.64 Diabet mellitus tip 1 cu hipoglicemie<br />

Diabet mellitus tip 1 cu hipoglicemie(ic):<br />

- coma<br />

- NOS<br />

- atac (convul<strong>si</strong>i) (criza)<br />

E10.65 Diabet mellitus tip 1 cu control slab<br />

Diabet mellitus tip 1:<br />

- pentru stabilizare<br />

- controlat slab<br />

- instabil<br />

E10.69 Diabet mellitus tip 1 cu alte complicatii<br />

specificate<br />

Diabet mellitus tip 1 cu:<br />

- gangrena (<strong>de</strong>rmala acuta) (bacteriana)<br />

(hemolitica):<br />

- Fournier<br />

- Meleney<br />

- fascita necrozanta<br />

- ulcer (extremitati inferioare)<br />

Exclu<strong>de</strong>: ulceratia piciorului la periferie<br />

cu:<br />

76<br />

- angiopatie (E10.73)<br />

- neuropatie (E10.73)<br />

E10.7 Diabet mellitus tip 1 cu complicatii<br />

multiple<br />

E10.71 Diabet mellitus tip 1 cu complicatii<br />

microvasculare multiple<br />

Doua sau mai multe dintre afectiunile<br />

cla<strong>si</strong>ficabile la E10.2, E10.3, E10.4,<br />

E10.53 sau E10.62<br />

E10.73 Diabet mellitus tip 1 cu ulceratia<br />

piciorului datorita unor cauze multiple<br />

Diabet mellitus tip 1 cu ulceratia<br />

piciorului la periferie cu:<br />

- angiopatie<br />

- neuropatie<br />

E10.8 Diabet mellitus tip 1 cu complicatii<br />

nespecificate<br />

E10.9 Diabet mellitus tip 1 fara complicatii<br />

E11 Diabet mellitus tip 2<br />

Inclu<strong>de</strong>: diabet (mellitus) (fara<br />

obezitate) (obezitate)<br />

- <strong>de</strong>but la adulti<br />

- datorit unui <strong>de</strong>fect al<br />

secretiei <strong>de</strong> insulina<br />

- rezistent la insulina<br />

- <strong>de</strong>but matur<br />

- noncetonic<br />

Exclu<strong>de</strong>: diabet mellitus (in):<br />

glicozuria:<br />

- NOS (R81)<br />

- renala (E74.8)<br />

- <strong>de</strong>but matur (la<br />

tineri)(MODY) (E13.-)<br />

- neonatal (E70.2)<br />

- NOS (E14.-)<br />

- alte forme specificate<br />

(E13.-)<br />

- sarcina, nastere <strong>si</strong> lauzie<br />

(O24.-)<br />

- Tip 1 (E10.-)<br />

reglementarea intolerantei la<br />

glucoza (E09.-)<br />

hipoinsulinemia<br />

postpreocedurala (E89.1)<br />

E11.0 Diabet mellitus tip 2 cu<br />

hiperosmolaritate<br />

E11.01 Diabet mellitus tip 2 cu<br />

hiperosmolaritate fara coma<br />

noncetotica hiperglicemicahiperosmolara<br />

[NKHHC]<br />

Diabet mellitus tip 2 cu hiperosmolaritate<br />

NOS<br />

E11.02 Diabet mellitus tip 2 cu<br />

hiperosmolaritate cu coma<br />

E11.1 Diabet mellitus tip 2 cu acidoza<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E11.11 Diabet mellitus tip 2 cu ketoacidoza,<br />

fara coma<br />

Diabet mellitus tip 2 cu ketoacidoza NOS<br />

E11.12 Diabet mellitus tip 2 cu ketoacidoza,<br />

cu coma<br />

Diabet mellitus tip 2 cu coma<br />

hiperglicemica NOS<br />

E11.13 Diabet mellitus tip 2 cu acidoza lactica,<br />

fara coma<br />

Diabet mellitus tip 2 cu acidoza lactica<br />

NOS<br />

E11.14 Diabet mellitus tip 2 cu acidoza lactica,<br />

cu coma<br />

E11.15 Diabet mellitus tip 2 cu ketoacidoza,<br />

cu acidoza lactica, fara coma<br />

Diabet mellitus tip 2 cu ketoacidoza, cu<br />

acidoza lactica NOS<br />

E11.16 Diabet mellitus tip 2 cu ketoacidoza,<br />

cu acidoza lactica, cu coma<br />

E11.2 Diabet mellitus tip 2 cu complicatii<br />

renale<br />

E11.21 Diabet mellitus tip 2 cu nefropatie<br />

diabetica incipienta<br />

Diabet mellitus tip 2 cu:<br />

- glomerular(a):<br />

- membrana bazala ingrosata<br />

- expan<strong>si</strong>une mezangiala<br />

- nefropatie incipienta (timpurie)<br />

(rever<strong>si</strong>bila)<br />

- microalbuminuria:<br />

- constanta<br />

- per<strong>si</strong>stenta<br />

E11.22 Diabet mellitus tip 2 cu nefropatie<br />

diabetica stabilita<br />

Diabet mellitus tip 2 cu:<br />

- glomeruloscleroza:<br />

- difuza<br />

- intracapilara<br />

- nodulara<br />

- Kimmelstiel-Wilson (boala) (leziune)<br />

- macroalbuminuria<br />

- nefropatia (avansata) (NOS)<br />

(progre<strong>si</strong>va)<br />

- proteinuria (fixata) (per<strong>si</strong>stenta)<br />

E11.23 Diabet mellitus tip 2 cu boala renala<br />

stadiu final [ESRD]<br />

Diabet mellitus tip 2 cu insuficienta<br />

renala cronica sau leziune renala cronica<br />

in afectiunile cla<strong>si</strong>ficabile la E11.22<br />

E11.29 Diabet mellitus tip 2 cu alte complicatii<br />

renale specificate<br />

Diabet mellitus tip 2 cu:<br />

- insuficienta renala acuta<br />

- necroza medulara (papilara)<br />

E11.3 Diabet mellitus tip 2 cu complicatii<br />

oculare<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E11.31 Diabet mellitus tip 2 cu retonopatie <strong>de</strong><br />

fond<br />

Diabet mellitus tip 2 cu:<br />

- retinal(a):<br />

- hemoragie (cu puncte <strong>si</strong> pete) (sub<br />

forma <strong>de</strong> flacara)<br />

- exudat<br />

- microanevrism<br />

- dilatare venoasa<br />

- retinopatie NOS<br />

E11.32 Diabet mellitus tip 2 cu retinopatie<br />

preproliferativa<br />

Diabet mellitus tip 2 cu:<br />

- anormalitati microvasculare intraretinale<br />

[IRMA]<br />

- retinal(a):<br />

- pete sub forma vatoasa<br />

- hemoragii (cu pete) (rotun<strong>de</strong>) (mici)<br />

- ischemia<br />

- venos(oasa):<br />

- perlata<br />

- buclata<br />

- dublata<br />

E11.33 Diabet mellitus tip 2 cu retinopatie<br />

proliferativa<br />

Diabet mellitus tip 2 cu:<br />

- hemoragie<br />

- preretinala<br />

- vitroasa<br />

- formare <strong>de</strong> vas nou (neovascularizatie)<br />

- tractiune retinala fara <strong>de</strong>tasare<br />

E11.34 Diabet mellitus tip 2 cu alte retinopatii<br />

Diabet mellitus tip 2 cu:<br />

- macular:<br />

- e<strong>de</strong>m (focal) (generalizat)<br />

(intraretinal)<br />

- sub forma <strong>de</strong> stea<br />

- maculopatie (circinat) (ischemic)<br />

- ingrosare retinala<br />

E11.35 Diabet mellitus tip 2 cu boala oculara<br />

avansata<br />

Diabet mellitus tip 2 cu:<br />

- glaucom neovascular<br />

- rubeoza irisului [rubeo<strong>si</strong>s iridis]<br />

- tractiunea retinei <strong>de</strong>tasate<br />

E11.36 Diabet mellitus tip 2 cu cataracta<br />

diabetica<br />

Exclu<strong>de</strong>: Diabet mellitus tip 2 cu<br />

cataracta cu <strong>de</strong>but la<br />

varsta timpurie (E11.39)<br />

E11.39 Diabet mellitus tip 2 cu alte complicatii<br />

oculare specificate<br />

Diabet mellitus tip 2 cu cataracta cu<br />

<strong>de</strong>but la varsta timpurie<br />

E11.4 Diabet mellitus tip 2 cu complicatii<br />

neurologice<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 77


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E11.40 Diabet mellitus tip 2 cu neuropatie<br />

nespecificata<br />

E11.41 Diabet mellitus tip 2 cu<br />

mononeuropatie diabetica<br />

Diabet mellitus tip 2 cu:<br />

- amiotrofie<br />

- paralizia nervului cranian:<br />

- III (oculomotor)<br />

- VI (abductor)<br />

- neuropatie femurala<br />

- mononeurita multipla<br />

- oftalmoplegia<br />

- radiculopatie:<br />

- toracica<br />

- troncular<br />

E11.42 Diabet mellitus tip 2 cu polineuropatie<br />

diabetica<br />

Diabet mellitus tip 2 cu:<br />

- neurita insulinica<br />

- neuropatie periferica:<br />

- distala <strong>si</strong>metrica<br />

- selectiva 'cu fibre mici'<br />

- senzorimotorie<br />

Exclu<strong>de</strong>: Diabet mellitus tip 2 cu<br />

polineuropatie diabetica<br />

autonoma (E11.43)<br />

E11.43 Diabet mellitus tip 2 cu neuropatie<br />

diabetica autonoma<br />

Diabet mellitus tip 2 cu:<br />

- secretie anormala (gustativa)<br />

- polineuropatie diabetica autonoma<br />

- diareea diabetica<br />

- disfunctie:<br />

- anorectala<br />

- esofagiana<br />

- insuficienta erectila (impotenta)<br />

- gastropareza<br />

- hipotonie, vezica urinara<br />

- e<strong>de</strong>m neuropatic<br />

- hipoten<strong>si</strong>une posturala<br />

E11.49 Diabet mellitus tip 2 cu alte complicatii<br />

neurologice specificate<br />

E11.5 Diabet mellitus tip 2 cu complicatii<br />

circulatorii<br />

E11.51 Diabet mellitus tip 2 cu angiopatie<br />

periferica, fara gangrena<br />

Exclu<strong>de</strong>: Diabet mellitus tip 2 cu<br />

angiopatie periferica, fara<br />

ulceratia piciorului (E11.73)<br />

E11.52 Diabet mellitus tip 2 cu angiopatie<br />

periferica, cu gangrena<br />

Exclu<strong>de</strong>: Diabet mellitus tip 2 cu<br />

angiopatie periferica, cu<br />

gangrena, cu ulceratia<br />

piciorului (E11.73)<br />

E11.53 Diabet mellitus tip 2 cu cardiomiopatie<br />

ischemica diabetica<br />

78<br />

E11.6 Diabet mellitus tip 2 cu alte complicatii<br />

specificate<br />

E11.61 Diabet mellitus tip 2 cu complicatii<br />

diabetice musculoscheletale <strong>si</strong> ale<br />

tesutului conjunctiv specificate<br />

Diabet mellitus tip 2 cu:<br />

- artropatie Charchot<br />

- diabetica/e:<br />

- <strong>si</strong>ndromul mainii (cheiroartropatie)<br />

(contractura Dupuytren) (fibromatoza<br />

fasciala palmara)<br />

- osteopatie<br />

- periartrita umarului<br />

E11.62 Diabet mellitus tip 2 cu complicatii ale<br />

pielii <strong>si</strong> tesutului subcutanat specificate<br />

Diabet mellitus tip 2 cu:<br />

- diabetic(a):<br />

- buloasa [bullo<strong>si</strong>s diabeticorum]<br />

- <strong>de</strong>rmopatie (pete ale pielii)<br />

- eritem<br />

- rubeoza<br />

- sclero<strong>de</strong>rmie<br />

- ingrosarea pielii<br />

- necrobioza lipoidica diabetica [NLD]<br />

- telangiectazie periunghiala<br />

E11.63 Diabet mellitus tip 2 cu complicatii<br />

periodontale specificate<br />

Diabet mellitus tip 2 cu:<br />

- abces periodontal acut<br />

- periodontita<br />

E11.64 Diabet mellitus tip 2 cu hipoglicemie<br />

Diabet mellitus tip 2 cu hipoglicemie(ic):<br />

- coma<br />

- NOS<br />

- atac (convul<strong>si</strong>i) (criza)<br />

E11.65 Diabet mellitus tip 2 cu control slab<br />

Diabet mellitus tip 2:<br />

- pentru stabilizare<br />

- controlat slab<br />

- instabil<br />

E11.69 Diabet mellitus tip 2 cu alte complicatii<br />

specificate<br />

Diabet mellitus tip 2 cu:<br />

- gangrena (<strong>de</strong>rmala acuta) (bacteriana)<br />

(hemolitica):<br />

- Fournier<br />

- Meleney<br />

- fascita necrozanta<br />

- ulcer (extremitati inferioare)<br />

Exclu<strong>de</strong>: ulceratia piciorului la periferie<br />

cu:<br />

- angiopatie (E11.73)<br />

- neuropatie (E11.73)<br />

E11.7 Diabet mellitus tip 2 cu complicatii<br />

multiple<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E11.71 Diabet mellitus tip 2 cu complicatii<br />

microvasculare multiple<br />

Doua sau mai multe dintre afectiunile<br />

cla<strong>si</strong>ficabile la E11.2, E11.3, E11.4,<br />

E11.53 sau E11.62<br />

E11.72 Diabet mellitus tip 2 cu caracteristici<br />

<strong>de</strong> rezistenta la insulina<br />

Diabet mellitus tip 2 cu:<br />

- hiperten<strong>si</strong>une cu:<br />

- orice afectiune <strong>de</strong> mai jos<br />

- obezitate NOS<br />

- <strong>de</strong>pozit <strong>de</strong> gra<strong>si</strong>me viscerala crescut<br />

- rezistenta la insulina NOS<br />

- una sau mai multe din urmatoarele:<br />

- achanto<strong>si</strong>s nigricans<br />

- dislipi<strong>de</strong>mia<br />

- hiperinsulinism<br />

- obezitate (intrunirea criteriilor OMS<br />

sau altele recunoscute)<br />

E11.73 Diabet mellitus tip 2 cu ulceratia<br />

piciorului datorita unor cauze multiple<br />

Diabet mellitus tip 2 cu ulceratia<br />

piciorului <strong>si</strong> la periferie cu:<br />

- angiopatie<br />

- neuropatie<br />

E11.8 Diabet mellitus tip 2 cu complicatii<br />

nespecificate<br />

E11.9 Diabet mellitus tip 2 fara complicatii<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E13 Alte forme specificate <strong>de</strong> diabet<br />

mellitus<br />

Folo<strong>si</strong>ti un cod aditional pentru orice<br />

afectiune <strong>de</strong> baza sau <strong>si</strong>ndrom genetic<br />

Inclu<strong>de</strong>: diabet mellitus (datorita) (in)<br />

(secundar) (cu):<br />

- indus medicamentos sau<br />

indus chimic<br />

- endocrinopatie<br />

- <strong>de</strong>fect genetic <strong>de</strong>:<br />

- functionare celule beta<br />

- actiune a insulinei<br />

- <strong>si</strong>ndrom genetic<br />

- boala imuno-mediata<br />

- infectie<br />

- <strong>de</strong>but matur la tineri<br />

(MODY)<br />

- boala pancreatica exocrina<br />

Exclu<strong>de</strong>: diabet mellitus (in):<br />

- neonatal (P70.2)<br />

- NOS (E14.-)<br />

- sarcina, nastere <strong>si</strong> lauzia<br />

(O24.-)<br />

- Tip 1 (E10.-)<br />

- Tip 2 (E11.-)<br />

glicozuria:<br />

- NOS (R81)<br />

- renala (E74.8)<br />

reglementarea intolerantei la<br />

glucoza (E09.-)<br />

E13.0 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu hiperosmolaritate<br />

E13.01 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu hiperosmolaritate, fara<br />

coma noncetotica hiperglicemicahiperosmolara<br />

[NKHHC]<br />

Diabet mellitus NEC cu<br />

hiperosmolaritate NOS<br />

E13.02 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu hiperosmolaritate, cu coma<br />

E13.1 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu acidoza<br />

E13.11 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu ketoacidoza, fara coma<br />

Diabet mellitus NEC cu ketoacidoza<br />

NOS<br />

E13.12 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu ketoacidoza, cu coma<br />

Diabet mellitus NEC cu coma<br />

hiperglicemica NOS<br />

E13.13 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu acidoza lactica, fara coma<br />

Diabet mellitus NEC cu acidoza lactica<br />

NOS<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 79


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E13.14 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu acidoza lactica, cu coma<br />

E13.15 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu ketoacidoza, cu acidoza<br />

lactica, fara coma<br />

Diabet mellitus NEC cu ketoacidoza cu<br />

acidoza lactica NOS<br />

E13.16 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu ketoacidoza, cu acidoza<br />

lactica, cu coma<br />

E13.2 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu complicatii renale<br />

E13.21 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu nefropatie diabetica<br />

incipienta<br />

Diabet mellitus NEC cu:<br />

- glomerular(a):<br />

- membrana bazala ingrosata<br />

- expan<strong>si</strong>une mezangiala<br />

- nefropatie incipienta (timpurie)<br />

(rever<strong>si</strong>bila)<br />

- microalbuminuria:<br />

- constanta<br />

- per<strong>si</strong>stenta<br />

E13.22 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu nefropatie diabetica<br />

stabilita<br />

Diabet mellitus NEC cu:<br />

- glomeruloscleroza:<br />

- difuza<br />

- intracapilara<br />

- nodulara<br />

- Kimmelstiel-Wilson (boala) (leziune)<br />

- macroalbuminuria<br />

- nefropatia (avansata) (NOS)<br />

(progre<strong>si</strong>va)<br />

- proteinuria (fixata) (per<strong>si</strong>stenta)<br />

E13.23 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu boala renala stadiu final<br />

[ESRD]<br />

Diabet mellitus tip 2 cu insuficienta<br />

renala cronica sau leziune renala cronica<br />

in afectiunile cla<strong>si</strong>ficabile la E13.22<br />

E13.29 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu alte complicatii renale<br />

specificate<br />

Diabet mellitus NEC cu:<br />

- insuficienta renala acuta<br />

- necroza medulara (papilara)<br />

E13.3 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu complicatii oculare<br />

80<br />

E13.31 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu retinopatie <strong>de</strong> fond<br />

Diabet mellitus NEC cu:<br />

- retinal(a):<br />

- hemoragie (cu puncte <strong>si</strong> pete) (sub<br />

forma <strong>de</strong> flacara)<br />

- exudat<br />

- microanevrism<br />

- dilatare venoasa<br />

- retinopatie NOS<br />

E13.32 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu retinopatie preproliferativa<br />

Diabet mellitus NEC cu:<br />

- anormalitati microvasculare intraretinale<br />

[IRMA]<br />

- retinal(a):<br />

- pete sub forma vatoasa<br />

- hemoragii (cu pete) (rotunda) (mica)<br />

- ischemia<br />

- venos(oasa):<br />

- perlata<br />

- buclata<br />

- dublata<br />

E13.33 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu retinopatie proliferativa<br />

Diabet mellitus NEC cu:<br />

- hemoragie<br />

- preretinala<br />

- vitroasa<br />

- formare <strong>de</strong> vas nou (neovascularizatie)<br />

- tractiune retinala fara <strong>de</strong>tasare<br />

E13.34 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu alte retinopatii<br />

Diabet mellitus NEC cu:<br />

- macular:<br />

- e<strong>de</strong>m (focal) (generalizat)<br />

(intraretinal)<br />

- sub forma <strong>de</strong> stea<br />

- maculopatie (circinat) (ischemic)<br />

- ingrosare retinala<br />

E13.35 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu boala oculara avansata<br />

Diabet mellitus NEC cu:<br />

- glaucom neovascular<br />

- rubeoza irisului [rubeo<strong>si</strong>s iridis]<br />

- tractiunea retinei <strong>de</strong>tasate<br />

E13.36 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu cataracta diabetica<br />

Exclu<strong>de</strong>: Diabet mellitus NEC cu<br />

cataracta cu <strong>de</strong>but la<br />

varsta timpurie (E13.39)<br />

E13.39 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu alte complicatii oculare<br />

specificate<br />

Diabet mellitus NEC cu cataracta cu<br />

<strong>de</strong>but la varsta timpurie<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E13.4 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu complicatii neurologice<br />

E13.40 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu neuropatie nespecificata<br />

E13.41 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu mononeuropatie diabetica<br />

Diabet mellitus NEC cu:<br />

- amiotrofie<br />

- paralizia nervului cranian:<br />

- III (oculomotor)<br />

- VI (abductor)<br />

- neuropatie femurala<br />

- mononeurita multipla<br />

- oftalmoplegia<br />

- radiculopatie:<br />

- toracica<br />

- troncular<br />

E13.42 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu polineuropatie diabetica<br />

Diabet mellitus NEC cu:<br />

- neurita insulinica<br />

- neuropatie periferica:<br />

- distala <strong>si</strong>metrica<br />

- selectiva 'cu fibre mici'<br />

- senzorimotorie<br />

Exclu<strong>de</strong>: diabet mellitus NEC cu<br />

polineuropatie diabetica<br />

autonoma (E13.43)<br />

E13.43 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu neuropatie diabetica<br />

autonoma<br />

Diabet mellitus NEC cu:<br />

- transpiratie anormala (gustativa)<br />

- polineuropatie diabetica autonoma<br />

- diareea diabetica<br />

- disfunctie:<br />

- anorectala<br />

- esofagiana<br />

- insuficienta erectila (impotenta)<br />

- gastropareza<br />

- hipotonia, vezica urinara<br />

- e<strong>de</strong>m neuropatic<br />

- hipoten<strong>si</strong>une posturala<br />

E13.49 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu alte complicatii neurologice<br />

specificate<br />

E13.5 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu complicatii circulatorii<br />

E13.51 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu angiopatie periferica, fara<br />

gangrena<br />

Exclu<strong>de</strong>: diabet mellitus NEC cu<br />

angiopatie periferica, cu<br />

ulceratia piciorului (E13.73)<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E13.52 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu angiopatie periferica, cu<br />

gangrena<br />

Exclu<strong>de</strong>: diabet mellitus NEC cu<br />

angiopatie periferica, cu<br />

gangrena, cu ulceratia<br />

piciorului (E13.73)<br />

E13.53 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu cardiomiopatie ischemica<br />

diabetica<br />

E13.6 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu alte complicatii specificate<br />

E13.61 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu complicatii diabetice<br />

musculoscheletale <strong>si</strong> ale tesutului<br />

conjunctiv specificate<br />

Diabet mellitus NEC cu:<br />

- artropatie Charchot<br />

- diabetica/e:<br />

- <strong>si</strong>ndromul mainii (cheiroartropatie)<br />

(contractura Dupuytren) (fibromatoza<br />

fasciala palmara)<br />

- osteopatie<br />

- periartrita umarului<br />

E13.62 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu complicatii ale pielii <strong>si</strong><br />

tesutului subcutanat specificate<br />

Diabet mellitus NEC1 cu:<br />

- diabetic(a):<br />

- buloasa [bullo<strong>si</strong>s diabeticorum]<br />

- <strong>de</strong>rmopatie (pete ale pielii)<br />

- eritem<br />

- rubeoza<br />

- sclero<strong>de</strong>rmie<br />

- ingrosarea pielii<br />

- necrobioza lipoidica diabetica [NLD]<br />

- telangiectazie periunghiala<br />

E13.63 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu complicatii periodontale<br />

specificate<br />

Diabet mellitus NEC cu:<br />

- abces periodontal acut<br />

- periodontita<br />

E13.64 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu hipoglicemie<br />

Diabet mellitus NEC cu hipoglicemie(ic):<br />

- coma<br />

- NOS<br />

- atac (convul<strong>si</strong>i) (criza)<br />

E13.65 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu control slab<br />

Alte forme specificate <strong>de</strong> diabet mellitus:<br />

- pentru stabilizare<br />

- controlat slab<br />

- instabil<br />

- cu esecul tratamentului secundar<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 81


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E13.69 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu alte complicatii specificate<br />

Diabet mellitus NEC cu:<br />

- gangrena (<strong>de</strong>rmala acuta) (bacteriana)<br />

(hemolitica):<br />

- Fournier<br />

- Meleney<br />

- fascita necrozanta<br />

- ulcer (extremitati inferioare)<br />

Exclu<strong>de</strong>: ulceratia piciorului la periferie<br />

cu:<br />

82<br />

- angiopatie (E13.73)<br />

- neuropatie (E13.73)<br />

E13.7 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu complicatii multiple<br />

E13.71 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu complicatii microvasculare<br />

multiple<br />

Doua sau mai multe dintre afectiunile<br />

cla<strong>si</strong>ficabile la E13.2, E13.3, E13.4,<br />

E13.53 sau E13.62<br />

E13.72 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu caracteristici <strong>de</strong> rezistenta<br />

la insulina<br />

Alte forme specificate <strong>de</strong> diabet mellitus<br />

cu:<br />

- hiperten<strong>si</strong>une cu:<br />

- orice afectiune <strong>de</strong> mai jos<br />

- obezitate NOS<br />

- <strong>de</strong>pozit <strong>de</strong> gra<strong>si</strong>me viscerala crescut<br />

- rezistenta la insulina NOS<br />

- una sau mai multe din urmatoarele:<br />

- achanto<strong>si</strong>s nigricans<br />

- dislipi<strong>de</strong>mia<br />

- hiperinsulinism<br />

- obezitate (intrunirea criteriilor OMS<br />

sau altele recunoscute)<br />

E13.73 Alte forme specificate <strong>de</strong> diabet<br />

mellitus ulceratia piciorului datorita<br />

unor cauza multiple<br />

Diabet mellitus NEC cu ulceratia<br />

piciorului <strong>si</strong> la periferie:<br />

- angiopatie<br />

- neuropatie<br />

E13.8 Alte forme specificate <strong>de</strong> diabet<br />

mellitus cu complicatii nespecificate<br />

E13.9 Alte forme specificate <strong>de</strong> diabet<br />

mellitus fara complicatii<br />

E14 Diabet mellitus nespecificat<br />

Diabet mellitus NOS<br />

Exclu<strong>de</strong>: diabet mellitus (in):<br />

- neonatal (P70.2)<br />

- non-insulino <strong>de</strong>pen<strong>de</strong>nt<br />

(E11.-)<br />

- sarcina, nastere <strong>si</strong> lauzie<br />

(O24.-)<br />

- Tip 1 (E10.-)<br />

- Tip 2 (E11.-)<br />

glicozuria:<br />

- NOS (R81)<br />

- renala (E74.8)<br />

reglementarea intolerantei la<br />

glucoza (E09.-)<br />

hipoinsulinemia<br />

postprocedurala (E89.1)<br />

E14.0 Diabet mellitus nespecificat cu<br />

hiperosmolaritate<br />

E14.01 Diabet mellitus nespecificat cu<br />

hiperosmolaritate, fara coma<br />

noncetotica hiperglicemicahiperosmolara<br />

[NKHHC]<br />

Diabet mellitus NOS cu<br />

hiperosmolaritate NOS<br />

E14.02 Diabet mellitus nespecificat cu<br />

hiperosmolaritate, cu coma<br />

E14.1 Diabet mellitus nespecificat cu acidoza<br />

E14.11 Diabet mellitus nespecificat cu<br />

ketoacidoza, fara coma<br />

Diabet mellitus NOS cu ketoacidoza<br />

NOS<br />

E14.12 Diabet mellitus nespecificat cu<br />

ketoacidoza, cu coma<br />

Diabet mellitus NOS cu coma<br />

hiperglicemica NOS<br />

E14.13 Diabet mellitus nespecificat cu acidoza<br />

lactica, fara coma<br />

Diabet mellitus NOS cu acidoza lactica<br />

NOS<br />

E14.14 Diabet mellitus nespecificat cu acidoza<br />

lactica, cu coma<br />

E14.15 Diabet mellitus nespecificat cu<br />

ketoacidoza, cu acidoza lactica, fara<br />

coma<br />

Diabet mellitus NOS cu ketoacidoza cu<br />

acidoza lactica NOS<br />

E14.16 Diabet mellitus nespecificat cu<br />

ketoacidoza, cu acidoza lactica, cu<br />

coma<br />

E14.2 Diabet mellitus nespecificat cu<br />

complicatii renale<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E14.21 Diabet mellitus nespecificat cu<br />

nefropatie diabetica incipienta<br />

Diabet mellitus NOS cu:<br />

- glomerular(a):<br />

- membrana bazala ingrosata<br />

- expan<strong>si</strong>une mezangiala<br />

- nefropatie incipienta (timpurie)<br />

(rever<strong>si</strong>bila)<br />

- microalbuminuria:<br />

- constanta<br />

- per<strong>si</strong>stenta<br />

E14.22 Diabet mellitus nespecificat cu<br />

nefropatie diabetica stabilita<br />

Diabet mellitus NOS cu:<br />

- glomeruloscleroza:<br />

- difuza<br />

- intracapilara<br />

- nodulara<br />

- Kimmelstiel-Wilson (boala) (leziune)<br />

- macroalbuminuria<br />

- nefropatia (avansata) (NOS) (progre<strong>si</strong>va)<br />

- proteinuria (fixata) (per<strong>si</strong>stenta)<br />

E14.23 Diabet mellitus nespecificat cu boala<br />

renala stadiu final [ESRD]<br />

Diabet mellitus NOS cu insuficienta<br />

renala cronica sau leziune renala cronica<br />

in afectiunile cla<strong>si</strong>ficabile la E14.22<br />

E14.29 Diabet mellitus nespecificat cu alte<br />

complicatii renale specificate<br />

Diabet mellitus NOS cu:<br />

- insuficienta renala acuta<br />

- necroza medulara (papilara)<br />

E14.3 Diabet mellitus nespecificat cu<br />

complicatii oculare<br />

E14.31 Diabet mellitus nespecificat cu<br />

retinopatie <strong>de</strong> fond<br />

Diabet mellitus NOS cu:<br />

- retinal(a):<br />

- hemoragie (cu puncte <strong>si</strong> pete) (sub<br />

forma <strong>de</strong> flacara)<br />

- exudat<br />

- microanevrism<br />

- dilatare venoasa<br />

- retinopatie NOS<br />

E14.32 Diabet mellitus nespecificat cu<br />

retinopatie preproliferativa<br />

Diabet mellitus NOS cu:<br />

- anormalitati microvasculare intraretinale<br />

[IRMA]<br />

- retinal(a):<br />

- pete sub forma vatoasa<br />

- hemoragii (cu pete) (rotunda) (mica)<br />

- ischemia<br />

- venos(oasa):<br />

- perlata<br />

- buclata<br />

- dublata<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E14.33 Diabet mellitus nespecificat cu<br />

retinopatie proliferativa<br />

Diabet mellitus NOS cu:<br />

- hemoragie<br />

- preretinala<br />

- vitroasa<br />

- formare <strong>de</strong> vas nou (neovascularizatie)<br />

- tractiune retinala fara <strong>de</strong>tasare<br />

E14.34 Diabet mellitus nespecificat cu alte<br />

retinopatii<br />

Diabet mellitus NOS cu:<br />

- macular:<br />

- e<strong>de</strong>m (focal) (generalizat)<br />

(intraretinal)<br />

- sub forma <strong>de</strong> stea<br />

- maculopatie (circinat) (ischemic)<br />

- ingrosare retinala<br />

E14.35 Diabet mellitus nespecificat cu boala<br />

oculara avansata<br />

Diabet mellitus NOS cu:<br />

- glaucom neovascular<br />

- rubeoza irisului [rubeo<strong>si</strong>s iridis]<br />

- tractiunea retinei <strong>de</strong>tasate<br />

E14.36 Diabet mellitus nespecificat cu<br />

cataracta diabetica<br />

Exclu<strong>de</strong>: Diabet mellitus NOS cu<br />

cataracta cu <strong>de</strong>but la<br />

varsta timpurie (E14.39)<br />

E14.39 Diabet mellitus nespecificat cu alte<br />

complicatii oculare specificate<br />

Diabet mellitus NOS cu cataracta cu<br />

<strong>de</strong>but la varsta timpurie<br />

E14.4 Diabet mellitus nespecificat cu<br />

complicatii neurologice<br />

E14.40 Diabet mellitus nespecificat cu<br />

neuropatie nespecificata<br />

E14.41 Diabet mellitus nespecificat cu<br />

mononeuropatie diabetica<br />

Diabet mellitus NOS cu:<br />

- amiotrofie<br />

- paralizia nervului cranian:<br />

- III (oculomotor)<br />

- VI (abductor)<br />

- neuropatie femurala<br />

- mononeurita multipla<br />

- oftalmoplegia<br />

- radiculopatie:<br />

- toracica<br />

- troncular<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 83


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E14.42 Diabet mellitus nespecificat cu<br />

polineuropatie diabetica<br />

Diabet mellitus NOS cu:<br />

- neurita insulinica<br />

- neuropatie periferica:<br />

- distala <strong>si</strong>metrica<br />

- selectiva 'cu fibre mici'<br />

- senzorimotorie<br />

Exclu<strong>de</strong>: diabet mellitus NOS cu<br />

polineuropatie diabetica<br />

autonoma (E14.43)<br />

E14.43 Diabet mellitus nespecificat cu<br />

neuropatie diabetica autonoma<br />

Diabet mellitus NOS cu:<br />

- transpiratie anormala (gustativa)<br />

- polineuropatie diabetica autonoma<br />

- diareea diabetica<br />

- disfunctie:<br />

- anorectala<br />

- esofagiana<br />

- insuficienta erectila (impotenta)<br />

- gastropareza<br />

- hipotonia, vezica urinara<br />

- e<strong>de</strong>m neuropatic<br />

- hipoten<strong>si</strong>une posturala<br />

E14.49 Diabet mellitus nespecificat cu alte<br />

complicatii neurologice specificate<br />

E14.5 Diabet mellitus nespecificat cu<br />

complicatii circulatorii<br />

E14.51 Diabet mellitus nespecificat cu<br />

agiopatie periferica, fara gangrena<br />

Exclu<strong>de</strong>: diabet mellitus NOS cu<br />

angiopatie periferica, cu<br />

ulceratia piciorului (E14.73)<br />

E14.52 Diabet mellitus nespecificat cu<br />

agiopatie periferica, cu gangrena<br />

Exclu<strong>de</strong>: diabet mellitus NOS cu<br />

angiopatie periferica, cu<br />

gangrena, cu ulceratia<br />

piciorului (E14.73)<br />

E14.53 Diabet mellitus nespecificat cu<br />

cardiomiopatie ischemica diabetica<br />

E14.6 Diabet mellitus nespecificat cu alte<br />

complicatii specificate<br />

E14.61 Diabet mellitus nespecificat cu<br />

complicatii diabetice musculoscheletale<br />

<strong>si</strong> ale tesutului conjunctiv specificate<br />

Diabet mellitus NOS cu:<br />

- artropatie Charchot<br />

- diabetica/e:<br />

- <strong>si</strong>ndromul mainii (cheiroartropatie)<br />

(contractura Dupuytren) (fibromatoza<br />

fasciala palmara)<br />

- osteopatie<br />

- periartrita umarului<br />

84<br />

E14.62 Diabet mellitus nespecificat cu<br />

complicatii ale pielii <strong>si</strong> tesutului<br />

subcutanat specificate<br />

Diabet mellitus NOS cu:<br />

- diabetic(a):<br />

- buloasa [bullo<strong>si</strong>s diabeticorum]<br />

- <strong>de</strong>rmopatie (pete ale pielii)<br />

- eritem<br />

- rubeoza<br />

- sclero<strong>de</strong>rmie<br />

- ingrosarea pielii<br />

- necrobioza lipoidica diabetica [NLD]<br />

- telangiectazie periungveala<br />

E14.63 Diabet mellitus nespecificat cu<br />

complicatii periodontale specificate<br />

Diabet mellitus NOS cu:<br />

- abces periodontal acut<br />

- periodontita<br />

E14.64 Diabet mellitus nespecificat cu<br />

hipoglicemie<br />

Diabet mellitus NOS cu hipoglicemie(ic):<br />

- coma<br />

- NOS<br />

- atac (convul<strong>si</strong>i) (criza)<br />

E14.65 Diabet mellitus nespecificat cu control<br />

slab<br />

Diabet mellitus nespecificat:<br />

- pentru stabilizare<br />

- controlat slab<br />

- instabil<br />

- cu esecul tratamentului secundar<br />

E14.69 Diabet mellitus nespecificat cu alte<br />

complicatii specifice<br />

Diabet mellitus NOS cu:<br />

- gangrena (<strong>de</strong>rmala acuta) (bacteriana)<br />

(hemolitica):<br />

- Fournier<br />

- Meleney<br />

- fascita necrozanta<br />

- ulcer (extremitati inferioare)<br />

Exclu<strong>de</strong>: ulceratia piciorului la periferie<br />

cu:<br />

- angiopatie (E14.73)<br />

- neuropatie (E14.73)<br />

E14.7 Diabet mellitus nespecificat cu<br />

complicatii multiple<br />

E14.71 Diabet mellitus nespecificat cu<br />

complicatii microvasculare multiple<br />

Doua sau mai multe dintre afectiunile<br />

cla<strong>si</strong>ficabile la E14.2, E14.3, E14.4,<br />

E14.53 sau E14.62<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E14.72 Diabet mellitus nespecificat cu<br />

caracteristici <strong>de</strong> rezistenta la insulina<br />

Diabet mellitus nespecificat cu:<br />

- hiperten<strong>si</strong>une cu:<br />

- orice afectiune <strong>de</strong> mai jos<br />

- obezitate NOS<br />

- <strong>de</strong>pozit <strong>de</strong> gra<strong>si</strong>me viscerala crescut<br />

- rezistenta la insulina NOS<br />

- una sau mai multe din urmatoarele:<br />

- achanto<strong>si</strong>s nigricans<br />

- dislipi<strong>de</strong>mia<br />

- hiperinsulinism<br />

- obezitate (intrunirea criteriilor OMS<br />

sau altele recunoscute)<br />

E14.73 Diabet mellitus nespecificat cu<br />

ulceratia piciorului datorita unor cauze<br />

multiple<br />

Diabet mellitus NOS cu ulceratia<br />

piciorului <strong>si</strong>la periferie:<br />

- angiopatie<br />

- neuropatie<br />

E14.8 Diabet mellitus nespecificat cu<br />

complicatii nespecificate<br />

E14.9 Diabet mellitus nespecificat fara<br />

complicatii<br />

Alte tulburari ale <strong>metabolism</strong>ului<br />

glucozei <strong>si</strong> ale secretiei pancreatice<br />

interne (E15-E16)<br />

E15<br />

Coma hipoglicemica nondiabetica<br />

Coma insulinica indusa medicamentos la<br />

nondiabetici<br />

Hiperinsulinism cu coma hipoglicemica<br />

Coma hipoglicemica NOS<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul, daca este indusa<br />

medicamentos.<br />

E16 Alte tulburari ale secretiei interne<br />

pancreatice<br />

E16.0 Hipoglicemia indusa medicamentos, fara<br />

coma<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul.<br />

E16.1 Alte hipoglicemii<br />

Hipoglicemia nonhiperinsulinemica<br />

functionala<br />

Hiperinsulinism:<br />

- functional<br />

- NOS<br />

Hiperplazia celulelor beta ale insulelor<br />

pancreatice NOS<br />

Encefalopatie datorita comei<br />

posthipoglicemice<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E16.2 Hipoglicemie nespecificata<br />

E16.3 Hipersecretia <strong>de</strong> glucagon<br />

Hiperplazia celulelor <strong>endocrine</strong> pancreatice<br />

cu exces <strong>de</strong> glucagon<br />

E16.4 Secretie anormala <strong>de</strong> gastrina<br />

Hipergastrinemia<br />

Sindromul Zollinger-Ellison<br />

E16.8 Alte tulburari specificate ale secretiei<br />

interne pancreatice<br />

Hipersecretia endocrina a pancreasului <strong>de</strong>:<br />

- reali<strong>si</strong>ng factor al hormonului <strong>de</strong> crestere<br />

(GHRH)<br />

- polipepti<strong>de</strong> pancreatice<br />

- somatostatin<br />

- polipepti<strong>de</strong> vasoactive intestinal<br />

E16.9 Tulburari ale secretiei interne<br />

pancreatice, nespecificate<br />

Hiperplazia celulelor insulelor lui<br />

Langerhans NOS<br />

Hiperplazia celulelor insulelor pancreatice<br />

NOS<br />

<strong>Boli</strong>le altor glan<strong>de</strong> <strong>endocrine</strong><br />

(E20-E35)<br />

Exclu<strong>de</strong>: galactoreea (N64.3)<br />

ginecomastia (N62)<br />

E20 Hipoparatiroidism<br />

Exclu<strong>de</strong>: <strong>si</strong>ndromul Di George (D82.1)<br />

hipoparatiroidism<br />

postprocedural (E89.2)<br />

tetania NOS (R29.0)<br />

hipoparatiroidism neonatal<br />

tranzitoriu (P71.4)<br />

E20.0 Hipoparatiroidism idiopatic<br />

E20.1 Pseudohipoparatiroidism<br />

E20.8 Alte hipoparatiroidisme<br />

E20.9 Hipoparatiroidism, nespecificat<br />

Tetania paratiroida<br />

E21 Hiperparatiroidism <strong>si</strong> alte tulburari<br />

ale glan<strong>de</strong>i paratiroi<strong>de</strong><br />

Exclu<strong>de</strong>: osteomalacia:<br />

- adultului (M83.-)<br />

infantila <strong>si</strong> juvenila (E55.0)<br />

E21.0 Hiperparatiroidism primar<br />

Hiperplazia paratiroi<strong>de</strong>i<br />

Osteita fibro-chistica generalizata [boala<br />

osoasa von Recklinghausen]<br />

E21.1 Hiperparatiroidism secundar, necla<strong>si</strong>ficat<br />

altun<strong>de</strong>va<br />

Exclu<strong>de</strong>: Hiperparatiroidism secundar <strong>de</strong><br />

origine renala (N25.8)<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 85


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E21.2 Alte hiperparatiroidisme<br />

Exclu<strong>de</strong>: hipercalcemia hipocalciurica<br />

familiala (E83.5)<br />

E21.3 Hiperparatiroidism, nespecificat<br />

E21.4 Alte tulburari specificate ale glan<strong>de</strong>i<br />

paratiroi<strong>de</strong><br />

E21.5 Tulburare a glan<strong>de</strong>i paratiroi<strong>de</strong>,<br />

nespecificata<br />

E22 Hipersecretia glan<strong>de</strong>i pituitare<br />

Exclu<strong>de</strong>: Sindromul Cushing (E24.-)<br />

86<br />

Sindromul Nelson (E24.1)<br />

Hipersecretia <strong>de</strong>:<br />

- ACTH neasociata cu boala<br />

Cushing (E27.0)<br />

- ACTH pituitara (E24.0)<br />

- hormon <strong>de</strong> stimulare<br />

tiroidiana (E05.8)<br />

E22.0 Acromegalia <strong>si</strong> gigantismul pituitar<br />

Artropatia asociata cu acromegalia<br />

† (M14.5*)<br />

Hipersecretia hormonului <strong>de</strong> crestere<br />

Exclu<strong>de</strong>: constitutional(a):<br />

- gigantism (E34.4)<br />

- statura inalta (E34.4)<br />

reali<strong>si</strong>ng factor al hormonului<br />

<strong>de</strong> crestere (GHRH) (E16.8)<br />

E22.1 Hiperprolactinemia<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul, daca este indusa<br />

medicamentos.<br />

E22.2 Sindromul secretiei anormale a<br />

hormonului antidiuretic<br />

E22.8 Alte hipersecretii ale glan<strong>de</strong>i pituitare<br />

Pubertate precoce centrala<br />

E22.9 Hipersecretia glan<strong>de</strong>i pituitare,<br />

nespecificata<br />

E23 Hiposecretia <strong>si</strong> alte tulburari ale<br />

glan<strong>de</strong>i pituitare<br />

Inclu<strong>de</strong>: afectiunile listate indiferent<br />

daca tulburarea se produce<br />

in glanda pituitara sau in<br />

hipotalamus<br />

Exclu<strong>de</strong>: hipopituitarism postprocedural<br />

(E89.3)<br />

E23.0 Hipopituitarism<br />

Sindromul eunucoidismului fertil<br />

Hipogonadism hipogonadotrofic<br />

Insuficienta idiopatica a hormonului <strong>de</strong><br />

crestere<br />

Insuficienta izolata <strong>de</strong>:<br />

- gonadotrofina<br />

- hormonul <strong>de</strong> crestere<br />

- hormonul pituitar<br />

Sindromul Kallmann<br />

Sindromul Lorain-Levi<br />

Necroza glan<strong>de</strong>i pituitare (postpartum)<br />

Panhipopituitarism<br />

Pituitar(a):<br />

- casexia<br />

- insuficienta NOS<br />

- insuficienta staturala<br />

Sindromul Sheehan<br />

Boala Simmonds<br />

E23.1 Hipopituitarismul indus medicamentos<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul.<br />

E23.2 Diabetul in<strong>si</strong>pid<br />

Exclu<strong>de</strong>: diabet in<strong>si</strong>pid nefrogen (N25.1)<br />

E23.3 Tulburari hipotalamice, necla<strong>si</strong>ficate<br />

altun<strong>de</strong>va<br />

Exclu<strong>de</strong>: Sindromul Pra<strong>de</strong>r-Willi<br />

(Q87.14)<br />

Sindromul Russell-Silver<br />

(Q87.15)<br />

E23.6 Alte tulburari ale glan<strong>de</strong>i pituitare<br />

Abcesul glan<strong>de</strong>i pituitare<br />

Distrofia adiposo-genitala<br />

E23.7 Tulburari ale glan<strong>de</strong>i pituitare,<br />

nespecificate<br />

E24 Sindromul Cushing<br />

E24.0 Boala Cushing pituitaro-<strong>de</strong>pen<strong>de</strong>nta<br />

Hipersecretia <strong>de</strong> ACTH pituitar<br />

Hiperadrenocorticismul pituitaro<strong>de</strong>pen<strong>de</strong>nt<br />

E24.1 Sindromul Nelson<br />

E24.2 Sindromul Cushing indus medicamentos<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul.<br />

E24.3 Sindromul <strong>de</strong> secretie ectopica <strong>de</strong> ACTH<br />

E24.4 Pseudo-<strong>si</strong>ndromul Cushing indus <strong>de</strong><br />

alcool<br />

E24.8 Alte <strong>si</strong>ndroame Cushing<br />

E24.9 Sindromul Cushing, nespecificat<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E25 Tulburari adrenogenitale<br />

Inclu<strong>de</strong>: <strong>si</strong>ndrom adrenogenital,<br />

masculinizant sau feminizant,<br />

fie dobandit, fie datorit<br />

hiperplaziei suprarenale<br />

consecinta anomaliilor<br />

congenitale a <strong>si</strong>ntezei<br />

hormonilor<br />

la femeie:<br />

- pseudohermafroditism<br />

suprarenal<br />

- pseudopubertate<br />

heterosexuala precoce<br />

la barbat:<br />

- pseudopubertate precoce<br />

isosexuala<br />

- macrogenitosomia precoce<br />

- precocitate sexuala cu<br />

hiperplazia suprarenala<br />

virilizare (la femeie)<br />

E25.0 Tulburari adrenogenitale congenitale<br />

legate <strong>de</strong> un <strong>de</strong>ficit enzimatic<br />

Deficit <strong>de</strong> 21-Hidroxilaza<br />

Hiperplazia suprarenala congenitala<br />

Hiperplazia suprarenala congenitala cu<br />

pier<strong>de</strong>re <strong>de</strong> sare<br />

E25.8 Alte tulburari adrenogenitale<br />

Tulburare adrenogenitala idiopatica<br />

Folo<strong>si</strong>ti un cod <strong>de</strong> cauza externa (Capitolul<br />

XX) pentru a i<strong>de</strong>ntifica medicamentul, daca<br />

este indusa medicamentos.<br />

E25.9 Tulburare adrenogenitala, nespecificata<br />

Sindrom adrenogenital NOS<br />

E26 Hiperaldosteronism<br />

E26.0 Hiperaldosteronism primar<br />

Sindromul Conn<br />

Aldosteronism primar datorit hiperplaziei<br />

suprarenale (bilateral)<br />

E26.1 Hiperaldosteronism secundar<br />

E26.8 Alte hiperaldosteronisme<br />

Sindromul Bartter<br />

E26.9 Hiperaldosteronism, nespecificat<br />

E27 Alte tulburari a<strong>de</strong>nocorticale<br />

E27.0 Alte hiperfunctiuni a<strong>de</strong>nocorticale<br />

Hipersecretia <strong>de</strong> ACTH, nelegata <strong>de</strong> boala<br />

Cushing<br />

Pubertate a<strong>de</strong>nocorticala precoce<br />

Exclu<strong>de</strong>: Sindromul Cushing (E24.-)<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E27.1 Insuficienta a<strong>de</strong>nocorticala primara<br />

Boala Addison<br />

Adrenalita autoimuna<br />

Exclu<strong>de</strong>: amiloidoza (E85.-)<br />

boala Addison tuberculoasa<br />

(A18.7)<br />

<strong>si</strong>ndromul Waterhouse-<br />

Fri<strong>de</strong>richsen (A39.1)<br />

E27.2 Criza addisoniana<br />

Criza adrenala<br />

Criza a<strong>de</strong>nocorticala<br />

E27.3 Insuficienta a<strong>de</strong>nocorticala primara<br />

indusa medicamentos<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul.<br />

E27.4 Insuficienta a<strong>de</strong>nocorticala, alta <strong>si</strong><br />

nespecificata<br />

Adrenal(a):<br />

- hemoragie<br />

- infarct<br />

Insuficienta a<strong>de</strong>nocorticala NOS<br />

Hipoaldosteronism<br />

Exclu<strong>de</strong>: leucodistrofia adrenala<br />

[Addison-Schil<strong>de</strong>r] (E71.3)<br />

<strong>si</strong>ndromul Waterhouse-<br />

Fri<strong>de</strong>richsen (A39.1)<br />

E27.5 Hiperfunctia adreno-medulara<br />

Hiperplazia adreno-medulara<br />

Hipersecretia catecolaminei<br />

E27.8 Alte tulburari specificate ale glan<strong>de</strong>i<br />

adrenale<br />

Anomalia cortizonului legand globulina<br />

E27.9 Tulburari ale glan<strong>de</strong>i adrenale,<br />

nespecificate<br />

E28 Disfunctia ovariana<br />

Exclu<strong>de</strong>: <strong>de</strong>ficienta izolatului in<br />

gonadotrofica (E23.0)<br />

insuficienta ovariana<br />

postprocedurala (E89.4)<br />

E28.0 Hiperestrogenia<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul, daca este indusa<br />

medicamentos.<br />

E28.1 Hiperandrogenia<br />

Hipersecretia <strong>de</strong> androgeni ovarieni<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul, daca este indusa<br />

medicamentos.<br />

E28.2 Sindrom ovarian polichistic<br />

Sindromul ovarian sclerochistic<br />

Sindromul Stein-Leventhal<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 87


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E28.3 Insuficienta ovariana primara<br />

Diminuarea estrogenilor<br />

Menopauza prematura NOS<br />

Sindromul ovarului rezistent<br />

Exclu<strong>de</strong>: tulburari <strong>de</strong> menopauza <strong>si</strong><br />

climacterium feminin (N95.1)<br />

88<br />

disgenezia gonadica pura<br />

(Q99.1)<br />

Sindromul Turner (Q96.-)<br />

E28.8 Alte disfunctii ovariene<br />

Hiperfunctia ovariana NOS<br />

E28.9 Disfunctia ovariana, nespecificata<br />

E29 Disfunctia testiculara<br />

Exclu<strong>de</strong>: <strong>si</strong>ndromul rezistentei la<br />

androgeni (E34.5)<br />

azoospermia sau oligospermia<br />

NOS (N46)<br />

insuficienta izolata <strong>de</strong><br />

gonadotropina (E23.0)<br />

<strong>si</strong>ndromul Klinefelter (Q98.0-<br />

Q98.2, Q98.4)<br />

hipofunctia testiculara<br />

postprocedurala (E89.5)<br />

<strong>si</strong>ndromul testicol feminizat<br />

(E34.5)<br />

E29.0 Hiperfunctia testiculara<br />

Hipersecretia <strong>de</strong> hormoni testiculari<br />

E29.1 Hipofunctia testiculara<br />

Deficit in 5-alfa-reductaza (cu<br />

pseudohermafrodism masculin)<br />

Bio<strong>si</strong>nteza <strong>de</strong>fectuoasa a hormonului<br />

androgen testicular NOS<br />

Hipogonadism testicular NOS<br />

Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />

(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul, daca este indusa<br />

medicamentos.<br />

E29.8 Alte disfunctii testiculare<br />

E29.9 Disfunctia testiculara, nespecificata<br />

E30 Tulburarile pubertatii, necla<strong>si</strong>ficate<br />

altun<strong>de</strong>va<br />

E30.0 Pubertate intarziata<br />

Intarzierea <strong>de</strong>zvoltarii constitutionale<br />

Dezvoltare sexuala intarziata<br />

E30.1 Pubertate precoce<br />

Menstruatie precoce<br />

Exclu<strong>de</strong>: <strong>si</strong>ndromul Albright(McCune)(-<br />

Sternberg) (Q78.1)<br />

pubertate precoce centrala<br />

(E22.8)<br />

hiperplazia adrenala<br />

congenitala (E25.0)<br />

pseudopubertatea<br />

heterosexuala la femeie<br />

(E25.-)<br />

pseudopubertatea isosexuala<br />

precoce la barbat (E25.-)<br />

E30.8 Alte tulburari ale pubertatii<br />

Menarha prematura<br />

E30.9 Tulburare <strong>de</strong> pubertate, nespecificata<br />

E31 Disfunctiuni pluriglandulare<br />

Exclu<strong>de</strong>: ataxia teleangiectazica [Louis-<br />

Bar] (G11.3)<br />

distrofia miotonica [Steinert]<br />

(G71.1)<br />

pseudohipoparatiroidism<br />

(E20.1)<br />

E31.0 Insuficienta poliglandulara autoimuna<br />

Sindromul Schmidt<br />

E31.1 Hiperfunctia poliglandulara<br />

Exclu<strong>de</strong>: a<strong>de</strong>nomatoza multipla<br />

endocrina (D44.8)<br />

E31.8 Alte disfunctii poliglandulare<br />

E31.9 Disfunctii poliglandulare, nespecificate<br />

E32 <strong>Boli</strong>le timusului<br />

Exclu<strong>de</strong>: aplazia sau hipoplazia cu<br />

imuno<strong>de</strong>ficienta (D82.1)<br />

miastenia gravis (G70.0)<br />

E32.0 Hiperplazia per<strong>si</strong>stenta a timusului<br />

Hipertrofia timusului<br />

E32.1 Abcesul timusului<br />

E32.8 Alte boli ale timusului<br />

E32.9 Boala timusului, nespecificata<br />

E34 Alte tulburari <strong>endocrine</strong><br />

Exclu<strong>de</strong>: pseudohipoparatiroidism<br />

(E20.1)<br />

E34.0 Sindrom carcinoid<br />

Nota: Poate fi folo<strong>si</strong>t ca un cod aditional,<br />

daca se doreste a se i<strong>de</strong>ntifica<br />

activitatea functionala asociata<br />

cu o tumora carcinoida<br />

E34.1 Alte hipersecretii <strong>de</strong> hormoni intestinali<br />

E34.2 Secretia hormonala ectopica,<br />

necla<strong>si</strong>ficata altun<strong>de</strong>va<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E34.3 Insuficienta staturala, necla<strong>si</strong>ficata<br />

altun<strong>de</strong>va<br />

Insuficienta staturala:<br />

- constitutionala<br />

- tip Laron<br />

- NOS<br />

- p<strong>si</strong>hosociala<br />

Exclu<strong>de</strong>: progeria (E34.8)<br />

<strong>si</strong>ndromul Russell-Silver<br />

(Q87.15)<br />

insuficienta staturala:<br />

- achondroplazica (Q77.4)<br />

- hipochondroplazica (Q77.4)<br />

- in <strong>si</strong>ndromul <strong>de</strong> malformatie<br />

congenitala (Q78.1)<br />

- in <strong>si</strong>ndromul dismorfic<br />

specific - codificati <strong>si</strong>ndromul<br />

(vezi In<strong>de</strong>xul alfabetic)<br />

- nutritionala (E45)<br />

- pituitara (E23.0)<br />

- renala (N25.0)<br />

- imuno<strong>de</strong>ficienta cu<br />

micromelie (D82.2)<br />

E34.4 Statura inalta constitutionala<br />

Gigantism constitutional<br />

E34.5 Sindromul <strong>de</strong> rezistenta la androgeni<br />

Pseudohermafroditism masculin cu<br />

rezistenta la androgeni<br />

Tulburarea receptorilor hormonali<br />

periferici<br />

Sindromul Reifenstein<br />

Feminizare testiculara (<strong>si</strong>ndrom)<br />

E34.8 Alte tulburari hormonale specificate<br />

Disfunctia glan<strong>de</strong>i pineale<br />

Progeria<br />

E34.9 Tulburare endocrina, nespecificata<br />

Tulburare:<br />

- endocrina NOS<br />

- hormonala NOS<br />

E35* Tulburari ale glan<strong>de</strong>lor <strong>endocrine</strong> in<br />

boli cla<strong>si</strong>ficate altun<strong>de</strong>va<br />

E35.0* Tulburarile glan<strong>de</strong>i tiroi<strong>de</strong> in boli<br />

cla<strong>si</strong>ficate altun<strong>de</strong>va<br />

Tuberculoza glan<strong>de</strong>i tiroi<strong>de</strong> (A18.8†)<br />

E35.1* Tulburarile glan<strong>de</strong>i adrenale in boli<br />

cla<strong>si</strong>ficate altun<strong>de</strong>va<br />

Siondromul Waterhouse-Fri<strong>de</strong>richsen<br />

(meningococic) (A39.1†)<br />

E35.8* Tulburarile altor glan<strong>de</strong> <strong>endocrine</strong> in boli<br />

cla<strong>si</strong>ficate altun<strong>de</strong>va<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

Malnutritia (E40-E46)<br />

Nota: Gradul <strong>de</strong> mal<strong>nutritie</strong> se masoara <strong>de</strong><br />

obicei in termenii greutatii, exprimat<br />

in <strong>de</strong>viatii standard <strong>de</strong> la media<br />

populatiei <strong>de</strong> referinta relevante.<br />

Indicatorul <strong>de</strong> mal<strong>nutritie</strong> apare <strong>de</strong><br />

obicei atunci cand una sau mai multe<br />

din masuratorile anterioare sunt<br />

disponibile, lipsa castigului greutatii la<br />

copii sau evi<strong>de</strong>nta pier<strong>de</strong>rii greutatii la<br />

copii sau adulti. Cand numai o<br />

masuratoare este disponibila,<br />

diagnosticul se bazeaza pe<br />

probabilitati <strong>si</strong> nu este <strong>de</strong>finitiv fara<br />

alte teste clinice sau <strong>de</strong> laborator. In<br />

circumstante exceptionale in care nu<br />

este disponibila nici o masuratoare a<br />

greutatii, diagnosticul se va baza pe<br />

investigatiile clinice.<br />

Daca o greutate observata este sub<br />

valoarea medie a populatiei <strong>de</strong><br />

referinta, exista o probabilitate mare<br />

<strong>de</strong> mal<strong>nutritie</strong> severa atunci cand<br />

valoarea observata este <strong>si</strong>tuata cu 3<br />

sau mai multe <strong>de</strong>viatii standard sub<br />

valoarea medie a populatiei <strong>de</strong><br />

referinta; o mare probabilitate <strong>de</strong><br />

mal<strong>nutritie</strong> mo<strong>de</strong>rata pentru o valoare<br />

observata se <strong>si</strong>tueaza intre 2 <strong>si</strong> mai<br />

putin <strong>de</strong> 3 <strong>de</strong>viatii standard sub<br />

aceasta medie; <strong>si</strong> o probabilitate<br />

mare <strong>de</strong> mal<strong>nutritie</strong> usoara pentru o<br />

valoare observata, se localizeaza intre<br />

1 <strong>si</strong> mai putin <strong>de</strong> 2 <strong>de</strong>viatii standard<br />

sub aceasta medie.<br />

Exclu<strong>de</strong>: malabsorbtia intestinala (K90.-)<br />

anemii nutritionale (D50-D53)<br />

sechele ale mal<strong>nutritie</strong>i proteinoenergetice<br />

(E64.0)<br />

infometare (T73.0)<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 89<br />

E40<br />

E41<br />

E42<br />

Kwashiorkor<br />

Malnutritia severa cu e<strong>de</strong>m nutritional cu<br />

<strong>de</strong>pigmentarea pielii <strong>si</strong> a parului<br />

Exclu<strong>de</strong>: kwashiorkor <strong>de</strong> marasm (E42)<br />

Marasm nutritional<br />

Mal<strong>nutritie</strong> grava cu marasm<br />

Exclu<strong>de</strong>: kwashiorkor <strong>de</strong> marasm (E42)<br />

Kwashiorkor <strong>de</strong> marasm<br />

Mal<strong>nutritie</strong> proteino-energetica grava [ca la<br />

E43]:<br />

- forma intermediara<br />

- cu semne atat <strong>de</strong> kwashiorkor, cat <strong>si</strong> <strong>de</strong><br />

marasm


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E43<br />

90<br />

Malnutritia proteino-energetica<br />

grava, nespecificata<br />

Pier<strong>de</strong>rea severa in greutate [emaciere] la<br />

copii sau adulti, sau lipsa <strong>de</strong> castig pon<strong>de</strong>ral<br />

la copil, ajungand la o greutate observata<br />

care este cu cel putin 3 <strong>de</strong>viatii standard sub<br />

valoarea medie pentru populatia <strong>de</strong> referinta<br />

(sau la o pier<strong>de</strong>re <strong>si</strong>milara exprimata dupa<br />

alte meto<strong>de</strong> statistice). Cand nu dispunem<br />

<strong>de</strong>cat <strong>de</strong> o <strong>si</strong>ngura masuratoare, exista o<br />

probabilitate puternica <strong>de</strong> emaciere grava<br />

atunci cand greutatea este cu 3 sau mai<br />

multe <strong>de</strong>viatii standard sub media populatiei<br />

<strong>de</strong> referinta.<br />

E<strong>de</strong>m <strong>de</strong> infometare<br />

E44 Malnutritia proteino-energetica<br />

usoara sau mo<strong>de</strong>rata<br />

E44.0 Malnutritia proteino-energetica mo<strong>de</strong>rata<br />

Pier<strong>de</strong>rea greutatii la copii sau adulti sau<br />

lipsa castigului in greutate la copii ducand la<br />

o greutate observata care este <strong>de</strong> 2 sau mai<br />

mult dar ne<strong>de</strong>pa<strong>si</strong>nd 3 <strong>de</strong>viatii standard sub<br />

valoarea medie pentru populatia <strong>de</strong> referinta<br />

(sau o pier<strong>de</strong>re <strong>si</strong>milara exprimata prin alte<br />

abordari statistice). Atunci cand numai o<br />

masuratoare este disponibila, exista o<br />

probabilitate mare <strong>de</strong> mal<strong>nutritie</strong> proteinoenergetica<br />

mo<strong>de</strong>rata cand greutatea<br />

observata este <strong>de</strong> 2 sau mai mult, dar<br />

ne<strong>de</strong>pa<strong>si</strong>nd 3 <strong>de</strong>viatii standard sub media<br />

populatiei <strong>de</strong> referinta.<br />

E44.1 Malnutritia proteino-energetica usoara<br />

Pier<strong>de</strong>rea greutatii la copii sau adulti sau<br />

lipsa castigului in greutate la copii ducand la<br />

o greutate observata care este <strong>de</strong> 1sau mai<br />

mult dar ne<strong>de</strong>pa<strong>si</strong>nd 2 <strong>de</strong>viatii standard sub<br />

valoarea medie pentru populatia <strong>de</strong> referinta<br />

(sau o pier<strong>de</strong>re <strong>si</strong>milara exprimata prin alte<br />

abordari statistice). Atunci cand numai o<br />

masuratoare este disponibila, exista o<br />

probabilitate mare <strong>de</strong> mal<strong>nutritie</strong> proteinoenergetica<br />

mo<strong>de</strong>rata cand greutatea<br />

observata este <strong>de</strong> 1 sau mai mult, dar<br />

ne<strong>de</strong>pa<strong>si</strong>nd 2 <strong>de</strong>viatii standard sub media<br />

populatiei <strong>de</strong> referinta.<br />

E45<br />

E46<br />

Intarzierea <strong>de</strong> <strong>de</strong>zvoltare datorita<br />

mal<strong>nutritie</strong>i proteino-energetice<br />

Nutritionala:<br />

- insuficienta staturala<br />

- intreruperea cresterii<br />

Retardare p<strong>si</strong>hica datorita mal<strong>nutritie</strong>i<br />

Malnutritia proteino-energetica<br />

nespecificata<br />

Malnutritia NOS<br />

Dezechilibru proteino-energetic NOS<br />

Alte carente nutritionale (E50-E64)<br />

Exclu<strong>de</strong>: anemia nutritionala (D50-D53)<br />

E50 Avitaminoza A<br />

Exclu<strong>de</strong>: sechele ale avitaminozei A<br />

(E64.1)<br />

E50.0 Avitaminoza A cu xeroza conjunctivei<br />

E50.1 Avitaminoza A cu pete Bitot <strong>si</strong> xeroza<br />

conjunctivei<br />

Pete Bitot la copilul mic<br />

E50.2 Avitaminoza A cu xeroza corneei<br />

E50.3 Avitaminoza A cu ulceratia corneei <strong>si</strong><br />

xeroza<br />

E50.4 Avitaminoza A cu cheratomalacie<br />

E50.5 Avitaminoza A cu hemeralopie vesperala<br />

E50.6 Avitaminoza A cu cicatrice xeroftalmica a<br />

corneei<br />

E50.7 Alte manifestari oculare ale avitaminozei<br />

A<br />

Xeroftalmia NOS<br />

E50.8 Alte manifestari ale avitaminozei A<br />

Keratoza foliculara datorita avitaminozei A<br />

† (L86*)<br />

Xero<strong>de</strong>rmia datorita avitaminozei A† (L86*)<br />

E50.9 Avitaminoza A, nespecificata<br />

Hipovitaminoza A NOS<br />

E51 Carenta in tiamina<br />

Exclu<strong>de</strong>: sechele ale carentei <strong>de</strong> tiamina<br />

(E64.8)<br />

E51.1 Beriberi<br />

Beriberi:<br />

- uscat<br />

- umed† (I98.8*)<br />

E51.2 Encefalopatia Wernicke<br />

E51.8 Alte manifestari ale carentei in tiamina<br />

E51.9 Carenta in tiamina, nespecificata<br />

E52<br />

Carenta in acid nicotinic (pelagra)<br />

Carenta in:<br />

- acid nicotinic (-triptofan)<br />

- nicotinami<strong>de</strong><br />

Pelagra (alcoolica)<br />

Exclu<strong>de</strong>: sechele ale carentei in acid<br />

nicotinic (E64.8)<br />

E53 Alte avitaminoze din grupa B<br />

Exclu<strong>de</strong>: sechele ale avitaminozei B<br />

(E64.8)<br />

E53.0 Carenta in riboflavine<br />

Ariboflavinoza<br />

anemia prin carenta <strong>de</strong> vitamina<br />

B12 (D51.-)<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E53.1 Carenta in piridoxina<br />

Avitaminoza B6<br />

Exclu<strong>de</strong>: anemia <strong>si</strong><strong>de</strong>roblastica<br />

reactionand la piridoxina<br />

(D64.3)<br />

E53.8 Carenta <strong>de</strong> alte vitamine din grupa B<br />

Carenta <strong>de</strong>:<br />

- biotina<br />

- cianocobalmina<br />

- folat<br />

- acid folic<br />

- acid pantotenic<br />

- vitamina B12<br />

E53.9 Avitaminoze din grupa B, nespecificate<br />

E54<br />

Carenta <strong>de</strong> acid ascorbic<br />

Carenta <strong>de</strong> vitamina C<br />

Scorbut<br />

Exclu<strong>de</strong>: anemia in scorbut (D53.2)<br />

sechele ale avitaminozei C<br />

(E64.2)<br />

E55 Carenta <strong>de</strong> vitamina D<br />

Exclu<strong>de</strong>: osteomalacia adultului (M83.-)<br />

E55.0 Rahitism evolutiv<br />

Osteomalacia:<br />

- infantila<br />

- juvenila<br />

Exclu<strong>de</strong>: rahitism:<br />

osteoporoza (M80-M81)<br />

sechele ale rahitismului (E64.3)<br />

- celiac (K90.0)<br />

- Crohn (K50.-)<br />

- inactiv (E64.3)<br />

- renal (N25.0)<br />

- rezistent la vitamina D<br />

(E83.3)<br />

E55.9 Carenta <strong>de</strong> vitamina D, nespecificata<br />

Avitaminoza D<br />

E56 Alte avitaminoze<br />

Exclu<strong>de</strong>: sechele ale altor avitaminoze<br />

(E64.8)<br />

E56.0 Carenta <strong>de</strong> vitamina E<br />

E56.1 Carenta <strong>de</strong> vitamina K<br />

Exclu<strong>de</strong>: <strong>de</strong>ficienta factorului <strong>de</strong><br />

coagulare datorita carentei <strong>de</strong><br />

vitamina K (D68.4)<br />

<strong>de</strong>ficienta <strong>de</strong> vitamina K a nounascutului<br />

(P53)<br />

E56.8 Carenta <strong>de</strong> alte vitamine<br />

E56.9 Avitaminoza, nespecificata<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 91<br />

E58<br />

E59<br />

E60<br />

Carenta alimentara <strong>de</strong> calciu<br />

Exclu<strong>de</strong>: tulburari in <strong>metabolism</strong>ul<br />

calciului (E83.5)<br />

sechelele carentei <strong>de</strong> calciu<br />

(E64.8)<br />

Carenta alimentara <strong>de</strong> seleniu<br />

Boala Keshan<br />

Exclu<strong>de</strong>: sechele ale carentei <strong>de</strong> seleniu<br />

(E64.8)<br />

Carenta <strong>de</strong> zinc<br />

E61 Carenta <strong>de</strong> alte elemente<br />

nutritionale<br />

Folo<strong>si</strong>ti un cod aditional pentru cauza<br />

externa (Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul, daca este indusa<br />

medicamentos.<br />

Exclu<strong>de</strong>: tulburari ale <strong>metabolism</strong>ului<br />

sarurilor minerale (E83.-)<br />

tulburari tiroidiene legate <strong>de</strong><br />

carenta <strong>de</strong> iod (E00-E02)<br />

sechele ale mal<strong>nutritie</strong>i <strong>si</strong> altor<br />

carente nutritionale (E64.-)<br />

E61.0 Carenta <strong>de</strong> cupru<br />

E61.1 Carenta <strong>de</strong> fier<br />

Exclu<strong>de</strong>: anemia prin carenta <strong>de</strong> fier<br />

(D50.-)<br />

E61.2 Carenta <strong>de</strong> magneziu<br />

E61.3 Carenta <strong>de</strong> mangan<br />

E61.4 Carenta <strong>de</strong> crom<br />

E61.5 Carenta <strong>de</strong> molib<strong>de</strong>n<br />

E61.6 Carenta <strong>de</strong> vanadiu<br />

E61.7 Carenta mai multor elemente nutritionale<br />

E61.8 Carenta <strong>de</strong> alte elemente nutritionale<br />

specificate<br />

E61.9 Carenta <strong>de</strong> element nutritional,<br />

nespecificata<br />

E63 Alte carente nutritionale<br />

Exclu<strong>de</strong>: <strong>de</strong>shidratare (E86)<br />

insuficienta <strong>de</strong> <strong>de</strong>zvoltare<br />

(R62.8)<br />

tulburari nutritionale la nounascuta<br />

(P92.-)<br />

sechele ale mal<strong>nutritie</strong>i <strong>si</strong> alte<br />

carente nutritionale (E64.-)<br />

E63.0 Carenta <strong>de</strong> acizi gra<strong>si</strong> esentiali [EFA]<br />

E63.1 Dezechilibru constituentilor alimentari<br />

ingerati<br />

E63.8 Alte carente nutritionale specificate<br />

E63.9 Carenta nutritionala, nespecificata<br />

Cardiomiopatie nutritionala NOS† (I43.2*)


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E64<br />

<br />

0008<br />

92<br />

Sechele ale mal<strong>nutritie</strong>i <strong>si</strong> alte<br />

carente nutritionale<br />

E64.0 Sechele ale mal<strong>nutritie</strong>i proteinoenergetica<br />

Exclu<strong>de</strong>: intarziere <strong>de</strong> <strong>de</strong>zvoltare ca<br />

urmare a unei malnutritii<br />

proteino-energetice (E45)<br />

E64.1 Sechele ale avitaminozei A<br />

E64.2 Sechele ale avitaminozei C<br />

E64.3 Sechele <strong>de</strong> rahitism<br />

E64.8 Sechele ale altor carente nutritionale<br />

E64.9 Sechele <strong>de</strong> carente nutritionale<br />

nespecificate<br />

Obezitatea <strong>si</strong> alte tulburari prin<br />

exces <strong>de</strong> aport (E65-E68)<br />

E65<br />

Adipozitate localizata<br />

Sort abdominal sau proeminent<br />

Burelet adipos<br />

E66 Obezitate<br />

Exclu<strong>de</strong>: distrofia adiposogenitala (E23.6)<br />

lipomatoza:<br />

- dureroasa [Dercum] (E88.2)<br />

- NOS (E88.2)<br />

<strong>si</strong>ndromul Pra<strong>de</strong>r-Willi (Q87.14)<br />

E66.0 Obezitate datorita unui exces caloric<br />

E66.1 Obezitate indusa medicamentos<br />

Folo<strong>si</strong>ti un cod aditional pentru cauza<br />

externa (Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul<br />

E66.2 Obezitate extrema cu hipoventilatie<br />

alveolara<br />

Sindromul Pickwickian<br />

E66.8 Alte obezitati<br />

Obezitate morbida<br />

E66.9 Obezitate, nespecificata<br />

Obezitate <strong>si</strong>mpla NOS<br />

E67 Alte excese <strong>de</strong> aport<br />

Exclu<strong>de</strong>: hiperalimentatia NOS (N63.2)<br />

sechelele hiperalimentatiei (E68)<br />

E67.0 Hipervitaminoza A<br />

E67.1 Hipercarotenemia<br />

E67.2 Sindrom <strong>de</strong> hipervitaminoza B6<br />

E67.3 Hipervitaminoza D<br />

E67.8 Alte excese <strong>de</strong> aport specificate<br />

E68<br />

<br />

0008<br />

Sechele ale excesului <strong>de</strong> aport<br />

Tulburari <strong>de</strong> <strong>metabolism</strong> (E70-E89)<br />

Exclu<strong>de</strong>: <strong>de</strong>ficit <strong>de</strong> 5-alfa-reductaza (E29.1)<br />

<strong>si</strong>ndromul rezistentei la androgeni<br />

(E34.5)<br />

hiperplazia suprarenala congenitala<br />

(E25.0)<br />

<strong>si</strong>ndromul Ehlers-Danlos (Q79.6)<br />

anemia hemolitica datorita unor<br />

tulburari enzimatice (D55.-)<br />

<strong>si</strong>ndromul Marfan (Q87.4)<br />

E70 Tulburari <strong>de</strong> <strong>metabolism</strong> ale<br />

aminoacizilor aromatici<br />

E70.0 Fenilcetonuria cla<strong>si</strong>ca<br />

E70.1 Alte hiperfenilalanilemii<br />

E70.2 Tulburari in <strong>metabolism</strong>ul tirozinei<br />

Alcaptonuria<br />

Hipertiro<strong>si</strong>nemia<br />

Ocronoza<br />

Tiro<strong>si</strong>nemia<br />

Tiro<strong>si</strong>noza<br />

E70.3 Albinism<br />

Albinism:<br />

- ocular<br />

- cutaneo-ocular<br />

Sindromul:<br />

- Chediak(-Steinbrinck)-Higashi<br />

- Cross<br />

- Hermansky-Pudlak<br />

E70.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

aminoacizilor aromatici<br />

Tulburari <strong>de</strong>:<br />

- <strong>metabolism</strong>ul histidinei<br />

- <strong>metabolism</strong>ul triptofanului<br />

E70.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al aminoacizilori<br />

aromatici, nespecificate<br />

E71 Tulburari <strong>de</strong> <strong>metabolism</strong> ale<br />

aminoacizilor cu lant ramificat <strong>si</strong> ale<br />

<strong>metabolism</strong>ului acizilor gra<strong>si</strong><br />

E71.0 Boala urinei cu miros <strong>de</strong> <strong>si</strong>rop <strong>de</strong> artar<br />

E71.1 Alte tulburari <strong>de</strong> <strong>metabolism</strong> ale<br />

aminoacizilor cu lant ramificat<br />

Hiperleucine-izoleucinemia<br />

Hipervalinemia<br />

Aci<strong>de</strong>mia izovalerica<br />

Aci<strong>de</strong>mia metilmalonica<br />

Aci<strong>de</strong>mia propionica<br />

E71.2 Tulburari <strong>de</strong> <strong>metabolism</strong> al aminoacizilor<br />

cu lant ramificat, nespecificate<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E71.3 Tulburari <strong>de</strong> <strong>metabolism</strong> al acizilor gra<strong>si</strong><br />

A<strong>de</strong>noleucodistrofia [Addison-Schil<strong>de</strong>r]<br />

Insuficienta <strong>de</strong> carnitine palmitiltransferaza<br />

musculara<br />

Exclu<strong>de</strong>: boala Refsum (G60.1)<br />

boala Schil<strong>de</strong>r (G37.0)<br />

<strong>si</strong>ndromul Zellweger (Q87.83)<br />

E72 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

aminoacizilor<br />

Exclu<strong>de</strong>: rezultate anormale fara boala<br />

evi<strong>de</strong>nta (R70-R89)<br />

tulburari <strong>de</strong>:<br />

- <strong>metabolism</strong>ul acizilor<br />

aromatici (E70.-)<br />

- <strong>metabolism</strong>ul aminoacizilor<br />

cu lant ramificat ((E71.0-<br />

E71.1)<br />

- <strong>metabolism</strong>ul acizilor gra<strong>si</strong><br />

(E71.3)<br />

- <strong>metabolism</strong>ul purinelor <strong>si</strong><br />

pirimidinelor (E79.-)<br />

guta (M10.-)<br />

E72.0 Tulburari in transportul aminoacizilor<br />

Cistinoza<br />

Cistinuria<br />

Sindromul Fanconi(-<strong>de</strong> Toni)(-Debré)<br />

Boala Hartnup<br />

Sindromul Lowe<br />

Exclu<strong>de</strong>: tulburari ale <strong>metabolism</strong>ului<br />

triptofanului (E70.8)<br />

E72.1 Tulburari <strong>de</strong> <strong>metabolism</strong> al aminoacizilor<br />

sulfurati<br />

Cistationinuria<br />

Homocistinuria<br />

Metioninemia<br />

Deficit in sulfit oxidaza<br />

Exclu<strong>de</strong>: carenta <strong>de</strong> transcobalamin II<br />

(D51.2)<br />

E72.2 Tulburari <strong>de</strong> <strong>metabolism</strong> al ciclului ureei<br />

Arginemia<br />

Aciduria arginosuccinica<br />

Citrulinemia<br />

Hiperamonemia<br />

Exclu<strong>de</strong>: tulburari ale <strong>metabolism</strong>ului<br />

ornitinei (E72.4)<br />

E72.3 Tulburari <strong>de</strong> <strong>metabolism</strong> al lizinei <strong>si</strong><br />

hidroxilizinei<br />

Aciduria glutarica<br />

Hidroxilizinemia<br />

Hiperlizinemia<br />

E72.4 Tulburari <strong>de</strong> <strong>metabolism</strong> al ornitinei<br />

Ornitinemia (tip I, II)<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E72.5 Tulburari <strong>de</strong> <strong>metabolism</strong> al glicinei<br />

Hiperhidroxiprolinemia<br />

Hiperprolinemia (tip I, II)<br />

Hiperglicinemia noncetozica<br />

Sarco<strong>si</strong>nemia<br />

E72.8 Alte tulburari specificate <strong>de</strong> <strong>metabolism</strong><br />

al aminoacizilor<br />

Tulburari <strong>de</strong>:<br />

- <strong>metabolism</strong>ul aminoacidului ß<br />

- ciclului gammaglutamil<br />

E72.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

aminoacizilori, nespecificate<br />

E73 Intoleranta la lactoza<br />

E73.0 Deficit congenital in lactaza<br />

E73.1 Deficit secundar in lactaza<br />

E73.8 Alte intolerante la lactoza<br />

E73.9 Intoleranta la lactoza, nespecificata<br />

E74 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

carbohidratilor<br />

Exclu<strong>de</strong>: diabet mellitus (E10.E14)<br />

hipoglicemia NOS (E16.2)<br />

hipersecretia <strong>de</strong> glucagon<br />

(E16.3)<br />

mucopolizaharidoza (E76.0-<br />

E76.3)<br />

E74.0 Boala <strong>de</strong>pozitarii glicogenului<br />

Glicogenoza cardiaca<br />

Boala:<br />

- An<strong>de</strong>rsen<br />

- Cori<br />

- Forbes<br />

- Hers<br />

- McArdle<br />

- Pompe<br />

- Tauri<br />

- von Gierke<br />

Deficit in fosforilaza hepatica<br />

E74.1 Tulburari <strong>de</strong> <strong>metabolism</strong> al fructozei<br />

Fructozuria esentiala<br />

Deficit in fructoza-1,6-disfosfataza<br />

Intoleranta ereditara la fructoza<br />

E74.2 Tulburari <strong>de</strong> <strong>metabolism</strong> al galactozei<br />

Deficit <strong>de</strong> galactochinaza<br />

Galactosemia<br />

E74.3 Alte tulburari <strong>de</strong> absorbtie intestinala a<br />

carbohidratilor<br />

Malabsorbtia glucozo-galactoza<br />

Deficit <strong>de</strong> sucraza<br />

Exclu<strong>de</strong>: intoleranta la lactoza (E73.-)<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 93


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E74.4 Tulburari <strong>de</strong> <strong>metabolism</strong> al piruvatului <strong>si</strong><br />

al gluconeogenezei<br />

Deficit <strong>de</strong>:<br />

- carboxikinaza fosfoenolpiruvat<br />

- piruvat:<br />

- carboxilaza<br />

- <strong>de</strong>hidrogenaza<br />

Exclu<strong>de</strong>: cu anemie (D55.-)<br />

E74.8 Alte tulburari specificate <strong>de</strong> <strong>metabolism</strong><br />

al carbohidratilor<br />

Pentosuria esentiala<br />

Oxaloza<br />

Oxaluria<br />

Glicozuria renala<br />

E74.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

carbohidratilor, nespecificate<br />

E75 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

sfingolipi<strong>de</strong>lor <strong>si</strong> al altor lipi<strong>de</strong> <strong>de</strong><br />

rezerva<br />

Exclu<strong>de</strong>: mucolipidoza, tipuri I-III<br />

(E77.0-E77.1)<br />

94<br />

boala Refsum (G60.1)<br />

E75.0 Ganglio<strong>si</strong>doza GM2<br />

Boala:<br />

- Sandhoff<br />

- Tay-Sachs<br />

Ganglio<strong>si</strong>doza GM2:<br />

- la adult<br />

- juvenila<br />

- NOS<br />

E75.1 Alte ganglio<strong>si</strong>doze<br />

Ganglio<strong>si</strong>doze:<br />

- GM1<br />

- GM3<br />

- NOS<br />

Mucolipidoza IV<br />

E75.2 Alte sfingolipidoze<br />

Boala:<br />

- Fabry(-An<strong>de</strong>rson)<br />

- Gaucher<br />

- Krabbe<br />

- Niemann-Pick<br />

Sindromul Farber<br />

Leucodistrofia metacromatica<br />

Deficit <strong>de</strong> sulfataza<br />

Exclu<strong>de</strong>: adrenoleucodistrofia [Addison-<br />

Schil<strong>de</strong>r] (E71.3)<br />

E75.3 Sfincolipidoza, nespecificata<br />

E75.4 Lipofuscinoza cu ceroi<strong>de</strong> neuronale<br />

Boala:<br />

- Batten<br />

- Bielschowsky-Jansky<br />

- Kufs<br />

- Spielmeyer-Vogt<br />

E75.5 Alte tulburari ale lipi<strong>de</strong>lor <strong>de</strong> rezerva<br />

Colesteroza cerebrotendinoasa [van<br />

Bogaert-Scherer-Epstein]<br />

Boala Wolman<br />

E75.6 Tulburari ale lipi<strong>de</strong>lor <strong>de</strong> rezerva,<br />

nespecificate<br />

E76 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

glicosaminoglicani<br />

E76.0 Mucopolizaharidoze, tip I<br />

Sindrom:<br />

- Hurler<br />

- Hurler-Scheie<br />

- Scheie<br />

E76.1 Mucopolizaharidoza, tip II<br />

Sindromul Hunter<br />

E76.2 Alte mucopolizaharidoze<br />

Mucopolizaharidoza, tip III, IV, VI, VII<br />

Carenta <strong>de</strong> ß-glucoronidasa<br />

Sindrom:<br />

- Maroteaux-Lamy (usor)(sever)<br />

- Morquio(-asemanator)(cla<strong>si</strong>c)<br />

- Sanfilippo (tip B)(tip C)(tipD)<br />

E76.3 Mucopolizaharidoza, nespecificata<br />

E76.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

glicosaminoglicani<br />

E76.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

glicosaminoglicani, nespecificate<br />

E77 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

glicoproteinelor<br />

E77.0 Deficit <strong>de</strong> transformare posttraductionala<br />

a enzimelor lisosomale<br />

Mucolipidoza II [boala celulelor I]<br />

Mucolipidoza III [polidistrofia pseudo-<br />

Hurler]<br />

E77.1 Deficit <strong>de</strong> <strong>de</strong>gradare a glicoproteinelor<br />

Aspartilglucozaminurie<br />

Fucozidoza<br />

Manozidoza<br />

Sialidoza [mucolipidoza I]<br />

E77.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

glicoproteinelor<br />

E77.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

glicoproteinelor, nespecificate<br />

E78 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

lipoproteinelor <strong>si</strong> alte lipi<strong>de</strong>mii<br />

Exclu<strong>de</strong>: sfingolipidoza (E75.0-E75.3)<br />

E78.0 Hipercolesterolemie esentiala<br />

Hipercolesterolemie familiala<br />

Hiperlipoproteinemia Fredrickson, tip IIa<br />

Hiperbetalipoproteinemia<br />

Hiperlipi<strong>de</strong>mia, grupa A<br />

Hiperlipoproteinemia cu lipoproteine <strong>de</strong><br />

<strong>de</strong>n<strong>si</strong>tate joasa [LDL]<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E78.1 Hipergliceri<strong>de</strong>mia esentiala<br />

Hipergliceri<strong>de</strong>mia endogena<br />

Hiperlipoproteinemia Fredrickson, tip IV<br />

Hiperlipi<strong>de</strong>mia, grupa B<br />

Hiperbetalipoproteinemia<br />

Hiperlipoproteinemia cu lipoproteine <strong>de</strong><br />

<strong>de</strong>n<strong>si</strong>tate foarte joasa [VLDL]<br />

E78.2 Hiperlipi<strong>de</strong>mie mixta<br />

Betalipoproteinemia larga sau flotanta<br />

Hiperlipoproteinemia Fredrickson, tip IIb<br />

sau III<br />

Hiperbetalipoproteinemia cu<br />

prebetalipoproteinemie<br />

Hipercolesterolemia cu hipergliceri<strong>de</strong>mie<br />

endogena<br />

Hiperlipi<strong>de</strong>mia, grupa C<br />

Xantom tubero-eruptiv<br />

Xantom tuberos<br />

Exclu<strong>de</strong>: colesteroza cerebrotendinoasa<br />

[van Bogaert-Scherer-<br />

Epstein] (E75.5)<br />

E78.3 Hiperchilomicroanemie<br />

Hiperlipoproteinemia Fredrickson, tip I sau<br />

V<br />

Hiperlipi<strong>de</strong>mia, grupa D<br />

Hipergliceri<strong>de</strong>mia mixta<br />

E78.4 Alte hiperlipi<strong>de</strong>mii<br />

Hiperlipi<strong>de</strong>mia familiala combinata<br />

E78.5 Hiperlipi<strong>de</strong>mia, nespecificata<br />

E78.6 Deficit in lipoproteine<br />

Abetalipoproteinemia<br />

Deficienta <strong>de</strong> lipoproteine <strong>de</strong> <strong>de</strong>n<strong>si</strong>tate<br />

inalta<br />

Hipoalfalipoproteinemia<br />

Hipobetalipoproteinemia (familiala)<br />

Deficienta <strong>de</strong> lecitin colesterol<br />

aciltransferaza<br />

Boala Tangier<br />

E78.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

lipoproteinelor<br />

E78.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

lipoproteinelor, nespecificate<br />

E79 Tulburari <strong>de</strong> <strong>metabolism</strong> ale<br />

purinelor <strong>si</strong> pirimidinei<br />

Exclu<strong>de</strong>: litiaza renala (N20.0)<br />

tulburari imunitare combinate<br />

(D81.-)<br />

guta (M10.-)<br />

anemia cu orotacidurie (D53.0)<br />

xero<strong>de</strong>rma pigmentosum<br />

(Q82.1)<br />

E79.0 Hiperuricemia fara semne <strong>de</strong> artrita<br />

inflamatorie sau <strong>de</strong> boala tofacee<br />

Hiperuricemia a<strong>si</strong>mptomatica<br />

E79.1 Sindromul Lesch-Nyhan<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E79.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al purinelor<br />

<strong>si</strong> pirimidinei<br />

Xantinuria ereditara<br />

E79.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al purinelor <strong>si</strong><br />

pirimidinei, nespecificate<br />

E80 Tulburari <strong>de</strong> <strong>metabolism</strong> al porfirinei<br />

<strong>si</strong> bilirubinei<br />

Inclu<strong>de</strong>: <strong>de</strong>ficit in cantalaza <strong>si</strong> peroxidaza<br />

E80.0 Porfirie eritropoietica ereditara<br />

Porfirie eritropoietica congenitala<br />

Protoporfiria eritropoietica<br />

E80.1 Porfirie cutanata tardiva<br />

E80.2 Alte porfirii<br />

Coproporfiria ereditara<br />

Porfiria:<br />

- acuta periodica (hepatica)<br />

- NOS<br />

Folo<strong>si</strong>ti un cod aditional pentru cauza<br />

externa (Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

cauza<br />

E80.3 Deficit in catalaza <strong>si</strong> peroxidaza<br />

Acatalazia [Takahara]<br />

E80.4 Sindromul Gilbert<br />

E80.5 Sindromul Crigler-Najjar<br />

E80.6 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al bilirubinei<br />

Sindromul Dubin-Johnson<br />

Sindromul Rotor<br />

E80.7 Tulburari <strong>de</strong> <strong>metabolism</strong> al bilirubinei,<br />

nespecificate<br />

E83 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

mineralelor<br />

Exclu<strong>de</strong>: carenta alimentara <strong>de</strong> minerale<br />

(E58-E61)<br />

tulburari ale glan<strong>de</strong>i paratiroi<strong>de</strong><br />

(E20-E21)<br />

carenta <strong>de</strong> vitamina D (E55.-)<br />

E83.0 Tulburari <strong>de</strong> <strong>metabolism</strong> al cuprului<br />

Boala Menkes (par cret)(par otelit)<br />

Boala Wilson<br />

E83.1 Tulburari <strong>de</strong> <strong>metabolism</strong> al fierului<br />

Hemocromatoza<br />

Exclu<strong>de</strong>: anemia:<br />

- carenta <strong>de</strong> fier (D50.-)<br />

- <strong>si</strong><strong>de</strong>roblastica (D64.0-D64.3)<br />

E83.2 Tulburari <strong>de</strong> <strong>metabolism</strong> al zincului<br />

Acro<strong>de</strong>rmatita enteropatica<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 95


<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E83.3 Tulburari <strong>de</strong> <strong>metabolism</strong> al fosforului<br />

Deficit in fosfataza acida<br />

Hipopotasemia familiala<br />

Hipofosfatazia<br />

Rezistent la vitamina D:<br />

- osteomalacia<br />

- rahitism<br />

Exclu<strong>de</strong>: osteomalacia adultului (M83.-)<br />

96<br />

osteoporoza (M80-M81)<br />

E83.4 Tulburari <strong>de</strong> <strong>metabolism</strong> al magneziului<br />

Hipermagnezemia<br />

Hipomagnezemia<br />

E83.5 Tulburari <strong>de</strong> <strong>metabolism</strong> al calciului<br />

Hipocalcemia hipocalciurica familiala<br />

Hipercalciuria idiopatica<br />

Exclu<strong>de</strong>: chondrocalcinoza (M11.1-<br />

M11.2)<br />

hiperparatiroidism (E21.0-<br />

E21.3)<br />

E83.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

mineralelor<br />

E83.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al mineralelor,<br />

nespecificate<br />

E84<br />

<br />

0402<br />

Fibroza chistica<br />

Inclu<strong>de</strong>: mucoviscidoza<br />

E84.0 Fibroza chistica cu manifestari<br />

pulmonare<br />

E84.1 Fibroza chistica cu manifestari intestinale<br />

Ileus meconial† (P75*)<br />

Exclu<strong>de</strong>: obstructia meconiana in cazurile<br />

un<strong>de</strong> se stie ca fibroza<br />

chistica nu este prezenta<br />

(P76.0)<br />

E84.8 Fibroza chistica cu alte manifestari<br />

Fibroza chistica cu manifestari combinate<br />

E84.9 Fibroza chistica, nespecificata<br />

E85 Amiloidoza<br />

Exclu<strong>de</strong>: boala Alzheimer (G30.-)<br />

amiloidoza primara (D47.7)<br />

E85.0 Amiloidoza heredofamiliala<br />

nonneuropatica<br />

Febra familiala mediteraneana<br />

Nefropatia amiloida ereditara<br />

E85.1 Amiloidoza heredofamiliala neuropatica<br />

Polineuropatia amiloida (portugheza)<br />

E85.2 Amiloidoza heredofamiliara, nespecificata<br />

E85.3<br />

<br />

1426<br />

Amiloidoza <strong>si</strong>stemica secundara<br />

Amiloidoza asociata cu hemodializa<br />

E85.4 Amiloidoza la unul sau mai multe organe<br />

Amiloidoza localizata<br />

E85.8 Alte amiloidoze<br />

E85.9 Amiloidoza, nespecificata<br />

E86<br />

Hipovolemia, <strong>de</strong>shidratarea<br />

Deshidratare<br />

Depletia volumului <strong>de</strong> plasma sau a<br />

lichidului extracelular<br />

Hipovolemia<br />

Exclu<strong>de</strong>: <strong>de</strong>shidratarea nou-nascutului<br />

(P74.1)<br />

soc hipovolemic:<br />

- NOS (R57.1)<br />

- postprocedural (T81.1)<br />

- traumatic (T79.4)<br />

E87 Alte tulburari <strong>de</strong> echilibru acidobazic,<br />

hidric <strong>si</strong> electrolitic<br />

E87.0 Hiperosmolaritate <strong>si</strong> hipernatremie<br />

Exces <strong>de</strong> sodiu [Na]<br />

Supraincarcare cu sodiu [Na]<br />

Exclu<strong>de</strong>: cu diabet mellitus (E1 - E14 <strong>de</strong><br />

obicei cu al patrulea caracter .0)<br />

E87.1 Hipoosmolaritate <strong>si</strong> hiponatremie<br />

Carenta <strong>de</strong> sodiu [Na]<br />

Exclu<strong>de</strong>: <strong>si</strong>ndromul <strong>de</strong> secretie anormala<br />

a hormonului antidiuretic<br />

(E22.2)<br />

E87.2 Acidoza<br />

Acidoza:<br />

- lactica<br />

- metabolica<br />

- NOS<br />

- respiratorie<br />

Exclu<strong>de</strong>: acidoza diabetica (E10 - E14 <strong>de</strong><br />

obicei cu al patrulea caracter .1)<br />

E87.3 Alcaloza<br />

Alcaloza:<br />

- metabolica<br />

- NOS<br />

- respiratorie<br />

E87.4 Tulburari mixte ale echilibrului acidobazic<br />

E87.5 Hiperpotasemie<br />

Exces <strong>de</strong> pota<strong>si</strong>u [K]<br />

Supraincarcare cu pota<strong>si</strong>u [K]<br />

E87.6 Hipopotasemie<br />

Carenta <strong>de</strong> pota<strong>si</strong>u [K]<br />

E87.7 Supraincarcare cu lichi<strong>de</strong><br />

Exclu<strong>de</strong>: e<strong>de</strong>m (R60.-)<br />

E87.8 Alte tulburari hidrice <strong>si</strong> electrolitice,<br />

necla<strong>si</strong>ficate altun<strong>de</strong>va<br />

Dezechilibru electrolitic NOS<br />

Hipercloremia<br />

Hipocloremia<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002


E88 Alte tulburari <strong>de</strong> <strong>metabolism</strong><br />

Folo<strong>si</strong>ti un cod aditional pentru cauza<br />

externa (Capitolul XX) pentru a i<strong>de</strong>ntifica<br />

medicamentul, daca sunt induse<br />

medicamentos.<br />

Exclu<strong>de</strong>: histiocitoza X (cronica) (D76.0)<br />

E88.0 Tulburari <strong>de</strong> <strong>metabolism</strong> al alfaproteinelor,<br />

necla<strong>si</strong>ficate altun<strong>de</strong>va<br />

Deficit <strong>de</strong> alfa-1-antitrip<strong>si</strong>na<br />

Bisalbuminemia<br />

Exclu<strong>de</strong>: tulburari <strong>de</strong> <strong>metabolism</strong> al<br />

lipoproteinelor (E78.-)<br />

gammapatia monoclonala<br />

(D47.2)<br />

hipergammaglobulinemia<br />

policlonala (D89.0)<br />

macroglobulinemia<br />

Wal<strong>de</strong>nström (C88.0)<br />

E88.1 Lipodistrofia, necla<strong>si</strong>ficata altun<strong>de</strong>va<br />

Lipodistrofia NOS<br />

Exclu<strong>de</strong>: Boala Whipple (K90.8)<br />

E88.2 Lipomatoza, necla<strong>si</strong>ficata altun<strong>de</strong>va<br />

Lipomatoza:<br />

- dureroasa [Dercum]<br />

- NOS<br />

E88.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> specificate<br />

Defecte ale canalului respirator<br />

mitocondrial:<br />

- stergerea DNA mitocondrial<br />

- <strong>de</strong>ficienta <strong>de</strong> NADH-coenzima Q<br />

reductaza<br />

- NOS<br />

- <strong>de</strong>ficienta <strong>de</strong> coenzima Q-citocroma<br />

reductaza<br />

- <strong>de</strong>ficienta <strong>de</strong> succinat coenzima Q<br />

reductaza<br />

Boala Hoffa-Kastert<br />

A<strong>de</strong>nolipomatoza Launois-Bensau<strong>de</strong><br />

Mitocondrial(a):<br />

- citopatia NOS<br />

- <strong>de</strong>fect NOS<br />

- boala NOS<br />

- tulburare NOS<br />

- <strong>si</strong>ndrom NOS<br />

Trimetillaminuria<br />

Codificati mai intai manifestarea(arile), daca<br />

este cunoscuta.<br />

E88.9 Tulburari metabolice, nespecificate<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

E89 Tulburari postprocedurale <strong>endocrine</strong><br />

<strong>si</strong> metabolice, necla<strong>si</strong>ficate<br />

altun<strong>de</strong>va<br />

E89.0 Hipotiroidism postprocedural<br />

Hipotiroidism dupa iradiere<br />

E89.1<br />

<br />

0401<br />

Hipoinsulinemia postprocedurala<br />

Hiperglicemia dupa pancreatectomie<br />

E89.2 Hipoparatiroidism postprocedural<br />

Tetania paratireopriva<br />

E89.3 Hipopituitarism postprocedural<br />

Hipopituitarism dupa iradiere<br />

E89.4 Insuficienta ovariana postprocedurala<br />

E89.5 Hipofunctiunea testiculara<br />

postprocedurala<br />

E89.6 Hipofunctiunea adrenocorticala<br />

(medulara) postprocedurala<br />

E89.8 Alte tulburari metabolice <strong>si</strong> endrocrine<br />

postprocedurale<br />

E89.9 Tulburari metabolice <strong>si</strong> endrocrine<br />

postprocedurale, nespecificate<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 97

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