Boli endocrine, de nutritie si metabolism
Boli endocrine, de nutritie si metabolism
Boli endocrine, de nutritie si metabolism
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Capitolul IV<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong><br />
<strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
(E00-E89)<br />
Acest capitol contine urmatoarele<br />
blocuri:<br />
E00 - E07 Afectiunile glan<strong>de</strong>i tiroi<strong>de</strong><br />
E09 - E14 Reglementarea intolerantei la<br />
glucoza <strong>si</strong> diabetul mellitus<br />
E15 - E16 Alte tulburari ale<br />
<strong>metabolism</strong>ului glucozei <strong>si</strong> ale<br />
secretiei pancreatice interne<br />
E20 - E35 <strong>Boli</strong>le altor glan<strong>de</strong> <strong>endocrine</strong><br />
E40 - E46 Malnutritia<br />
E50 - E64 Alte carente nutritionale<br />
E65 - E68 Obezitatea <strong>si</strong> alte tulburari prin<br />
exces <strong>de</strong> aport<br />
E70 – E89 Tulburari <strong>de</strong> <strong>metabolism</strong><br />
Categoriile cu asterisc <strong>de</strong> la acest<br />
capitol sunt urmatoarele:<br />
E35* Tulburari ale glan<strong>de</strong>lor<br />
<strong>endocrine</strong> in boli cla<strong>si</strong>ficate<br />
altun<strong>de</strong>va<br />
Nota: Toate tumorile, indiferent daca sunt<br />
active sau nu in mod functional, sunt<br />
cla<strong>si</strong>ficate la Capitolul II. Codurile<br />
a<strong>de</strong>cvate din acest capitol (adica<br />
E05.8, E07.0, E16-E31, E34.-) pot fi<br />
folo<strong>si</strong>te, daca se doreste, drept coduri<br />
aditionale pentru a indica fie<br />
activitatea functionala a unei tumori<br />
maligne <strong>si</strong> tesut endocrin ectopic, fie<br />
hiperfunctia <strong>si</strong> hipofunctia glan<strong>de</strong>lor<br />
<strong>endocrine</strong> asociate cu tumorile<br />
maligne <strong>si</strong> alte afectiuni cla<strong>si</strong>ficate<br />
altun<strong>de</strong>va.<br />
Exclu<strong>de</strong>: complicatii ale sarcinii, nasterii <strong>si</strong> lauziei<br />
(O00-O99)<br />
<strong>si</strong>mptome, semne <strong>si</strong> rezultate clinice <strong>si</strong><br />
<strong>de</strong> laborator anormale, necla<strong>si</strong>ficate<br />
altun<strong>de</strong>va (R00-R99)<br />
tulburari tranzitorii <strong>endocrine</strong> <strong>si</strong><br />
metabolice specifice fatului <strong>si</strong> nounascutului<br />
(P70-P74)<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
Afectiunile glan<strong>de</strong>i tiroi<strong>de</strong><br />
(E00-E07)<br />
E00 Sindromul <strong>de</strong>ficientei congenitale <strong>de</strong><br />
iod<br />
Folo<strong>si</strong>ti codul aditional (F70-F79) pentru a<br />
i<strong>de</strong>ntifica orice intarziere mentala asociata.<br />
Inclu<strong>de</strong>: afectiuni en<strong>de</strong>mice asociate cu<br />
<strong>de</strong>ficienta <strong>de</strong> iod a mediului,<br />
fie direct, fie ca o consecinta<br />
a <strong>de</strong>ficientei <strong>de</strong> iod materne.<br />
Unele dintre afectiuni nu au o<br />
hipotiroidie curenta, dar sunt<br />
consecinta secretiei anormale<br />
a hormonului tiroidian in<br />
<strong>de</strong>zvoltarea fatului. Gusa<br />
datorita mediului poate fi<br />
asociata.<br />
Exclu<strong>de</strong>: hipotiroidie prin carenta<br />
subclinica in iod (E02)<br />
E00.0 Sindromul <strong>de</strong>ficientei congenitale <strong>de</strong> iod<br />
<strong>de</strong> tip neurologic<br />
Cretinism e<strong>de</strong>mic <strong>de</strong> tip neurologic<br />
E00.1 Sindromul <strong>de</strong>ficientei congenitale <strong>de</strong> iod<br />
<strong>de</strong> tip mixe<strong>de</strong>matos<br />
Cretinism en<strong>de</strong>mic:<br />
- hipotiroidian<br />
- tip mixe<strong>de</strong>matos<br />
E00.2 Sindromul <strong>de</strong>ficientei congenitale <strong>de</strong> iod<br />
<strong>de</strong> tip mixt<br />
Cretinism en<strong>de</strong>mic <strong>de</strong> tip mixt<br />
E00.9 Sindromul <strong>de</strong>ficientei congenitale <strong>de</strong> iod,<br />
nespecificat<br />
Hipotiroidia prin <strong>de</strong>ficienta congenitala <strong>de</strong><br />
iod NOS<br />
Cretinism en<strong>de</strong>mic NOS<br />
E01 Tulburari tiroidiene <strong>si</strong> afectiuni<br />
inrudite legate <strong>de</strong> <strong>de</strong>ficienta <strong>de</strong> iod<br />
Exclu<strong>de</strong>: <strong>si</strong>ndromul <strong>de</strong>ficientei congenitale<br />
<strong>de</strong> iod (E00.-)<br />
hipotiroidia prin carenta<br />
subclinica <strong>de</strong> iod (E02)<br />
E01.0 Gusa difuza (en<strong>de</strong>mica) legata <strong>de</strong><br />
carenta <strong>de</strong> iod<br />
E01.1 Gusa multinodulara (en<strong>de</strong>mica) legata <strong>de</strong><br />
o carenta <strong>de</strong> iod<br />
Gusa nodulara legata <strong>de</strong> carenta <strong>de</strong> iod<br />
E01.2 Gusa (en<strong>de</strong>mica) legata <strong>de</strong> carenta <strong>de</strong><br />
iod, nespecificata<br />
Gusa en<strong>de</strong>mica NOS<br />
E01.8 Alte afectiuni tiroidiene <strong>si</strong> inrudite legate<br />
<strong>de</strong> carenta <strong>de</strong> iod<br />
Hipotiroidia prin carenta <strong>de</strong> iod dobandita<br />
NOS<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 71
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E02<br />
72<br />
Hipotiroidia prin carenta subclinica<br />
<strong>de</strong> iod<br />
E03 Alte hipotiroidii<br />
Exclu<strong>de</strong>: hipotiroidia legata <strong>de</strong> o carenta<br />
<strong>de</strong> iod (E00-E02)<br />
hipotiroidia postprocedurala<br />
(E89.0)<br />
E03.0 Hipotiroidia congenitala, cu gusa difuza<br />
Gusa (nontoxica) congenitala:<br />
- NOS<br />
- parenchimatoasa<br />
Exclu<strong>de</strong>: gusa congenitala tranzitorie cu<br />
functiune normala (P72.0)<br />
E03.1 Hipotiroidia congenitala fara gusa<br />
Aplazia tiroi<strong>de</strong>i (cu mixe<strong>de</strong>m)<br />
Congenitala:<br />
- atrofia tiroi<strong>de</strong>i<br />
- hipotiroidia NOS<br />
E03.2 Hipotiroidia datorita unor medicamente <strong>si</strong><br />
altor substante exogene<br />
Folo<strong>si</strong>ti un cod <strong>de</strong> cauza externa (Capitolul<br />
XX) pentru a i<strong>de</strong>ntifica cauza.<br />
E03.3 Hipotiroidia postinfectioasa<br />
E03.4 Atrofia tiroi<strong>de</strong>i (dobandita)<br />
Exclu<strong>de</strong>: atrofia congenitala a tiroi<strong>de</strong>i<br />
(E03.1)<br />
E03.5 Coma mixe<strong>de</strong>matoasa<br />
E03.8 Alte hipotiroidii specificate<br />
E03.9 Hipotiroidia, nespecificata<br />
Mixe<strong>de</strong>m NOS<br />
E04 Alte guse netoxice<br />
Exclu<strong>de</strong>: gusa congenitala:<br />
- difuza (E03.0)<br />
- NOS (E03.0)<br />
- parenchimatoasa (E03.0)<br />
gusa legata <strong>de</strong> o carenta <strong>de</strong> iod<br />
(E00-E02)<br />
E04.0 Gusa difuza netoxica<br />
Gusa, netoxica:<br />
- difuza (coloida)<br />
- <strong>si</strong>mpla<br />
E04.1 Nodul tiroidian unic, netoxic<br />
Nodul coloid (chistic) (tiroidian)<br />
Gusa uninodulara netoxica<br />
Nodul tiroidian (chistic) NOS<br />
E04.2 Gusa multinodulara netoxica<br />
Gusa chistica NOS<br />
Gusa multinodulara (chistica) NOS<br />
E04.8 Alte guse netoxice, specificate<br />
E04.9 Gusa netoxica, nespecificata<br />
Gusa NOS<br />
Gusa nodulara (nontoxica) NOS<br />
E05 Tireotoxicoza [hipertiroidia]<br />
Exclu<strong>de</strong>: tiroidita cronica cu tireotoxicoza<br />
tranzitorie (E06.2)<br />
tireotoxicoza neonatala (P72.1)<br />
E05.0 Tireotoxicoza cu gusa difuza<br />
Gusa exoftalmica sau toxica NOS<br />
Boala Graves<br />
Gusa toxica difuza<br />
E05.1 Tireotoxicoza cu nodul unic tiroidian<br />
Tireotoxicoza cu gusa uninodulara toxica<br />
E05.2 Tireotoxicoza cu gusa multinodulara<br />
toxica<br />
Gusa nodulara toxica NOS<br />
E05.3 Tireotoxicoza datorita tesutului ectopic<br />
tiroidian<br />
E05.4 Tireotoxicoza factica<br />
E05.5 Criza acuta tireotoxica<br />
Folo<strong>si</strong>ti un cod aditional pentru a indica<br />
tipul tereotoxicozei (E05.0-E05.4, E05.8-<br />
E05.9)<br />
E05.8 Alte tireotoxicoze<br />
Supraproductia <strong>de</strong> hormon tiroido-stimulant<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica cauza.<br />
E05.9 Tireotoxicoza, nespecificata<br />
Hipertiroidism NOS<br />
Afectiunea cardiaca tireotoxica† (I43.8*)<br />
E06 Tiroidita<br />
Exclu<strong>de</strong>: tiroidita postpartum (O90.5)<br />
E06.0 Tiroidita acuta<br />
Abces al tiroi<strong>de</strong>i<br />
Tiroidita:<br />
- piogena<br />
- supurata<br />
Folo<strong>si</strong>ti un cod aditional (B95-B97) pentru a<br />
i<strong>de</strong>ntifica agentul infectios.<br />
E06.1 Tiroidita subacuta<br />
Tiroidita:<br />
- <strong>de</strong> Quervain<br />
- celule gigantice<br />
- granulomatoasa<br />
- nonsupurativa<br />
Exclu<strong>de</strong>: tiroidita autoimuna (E06.3)<br />
E06.2 Tiroidita cronica cu tireotoxicoza<br />
tranzitorie<br />
Exclu<strong>de</strong>: tiroidita autoimuna (E06.3)<br />
E06.3 Tiroidita autoimuna<br />
Tiroidita Hashimoto<br />
Hashitoxicoza (tranzitorie)<br />
Gusa limfa<strong>de</strong>noida<br />
Tiroidita limfocitica<br />
Strumita limfomatoasa<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E06.4 Tiroidita provocata <strong>de</strong> medicamente<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul.<br />
E06.5 Alte tiroidite cronice<br />
Tiroidita:<br />
- cronica:<br />
- fibroasa<br />
- NOS<br />
- lemnoasa<br />
- Rie<strong>de</strong>l<br />
E06.9 Tiroidita, nespecificata<br />
E07 Alte afectiuni ale tiroi<strong>de</strong>i<br />
E07.0 Hipersecretia <strong>de</strong> calcitonina<br />
Hiperplazia <strong>de</strong> celule C a tiroi<strong>de</strong>i<br />
Hipersecretia <strong>de</strong> tirocalcitonina<br />
E07.1 Gusa datorita unei tulburari a <strong>si</strong>ntezei<br />
hormonale<br />
Gusa familiala datorita unei tulburari a<br />
<strong>si</strong>ntezei hormonale<br />
Sindromul Pendred<br />
Exclu<strong>de</strong>: gusa congenitala tranzitorie cu<br />
functie normala (P72.0)<br />
E07.8 Alte afectiuni specificate ale tiroi<strong>de</strong>i<br />
Anomalia tiroglobulinei<br />
Hemoragia tiroi<strong>de</strong>i<br />
Infarctul tiroi<strong>de</strong>i<br />
Sindromul disfunctiei eutiroidiene<br />
E07.9 Afectiunea tiroi<strong>de</strong>i, nespecificata<br />
Reglementarea intolerantei la<br />
glucoza <strong>si</strong> diabetul mellitus<br />
(E09-E14)<br />
0401<br />
Nota: Criterii <strong>de</strong> diagnostic:<br />
Criteriile OMS pentru<br />
reglementarea intolerantei la<br />
glucoza (revizuite in 1999):<br />
Testul <strong>de</strong> toleranta bazat pe<br />
administrarea corecta a glucozei pe<br />
cale orala (glucoza plasmatica<br />
recoltata venos pe nemancate 6.1-6.9<br />
mmol/l, sau<br />
glucoza plasmatica venoasa la 2 ore<br />
dupa administarea glucozei orale 7.8-<br />
11.0 mmol/l), sau<br />
nivelul glucozei plasmatice venoase<br />
pe nemancate 6.1-6.9 mmol/l<br />
Criteriile OMS pentru diabet<br />
mellitus (revizuite in 1999):<br />
Testul <strong>de</strong> toleranta bazat pe<br />
administrarea corecta a glucozei pe<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
cale orala (glucoza plasmatica<br />
recoltata venos pe nemancate ≥ 7.0<br />
mmol/l sau glucoza plasmatica<br />
venoasa la 2 ore dupa administrarea<br />
glucozei orale, glucoza plasmatica<br />
venoasa la 2 ore dupa administrarea<br />
glucozei orale ≥ 11.1 mmol/L), sau<br />
Asociatia Americana <strong>de</strong> Diabet<br />
(ADA) - criterii:<br />
Nivelul glucozei plasmatice venoase<br />
pe nemancate ≥ 7.0 mmol/L, sau<br />
Simptomele cla<strong>si</strong>ce <strong>de</strong> sete, poliurie <strong>si</strong><br />
glucoza plasmatica venoasa<br />
randomizata ≥ 11.1 mmol/L.<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica daca este indus<br />
medicamentos sau chimic.<br />
E09<br />
<br />
0401<br />
E09.0<br />
<br />
Reglementarea intolerantei la<br />
glucoza<br />
Folo<strong>si</strong>ti un cod aditional pentru orice<br />
afectiune <strong>de</strong> baza sau <strong>si</strong>ndrom genetic<br />
asociat.<br />
Inclu<strong>de</strong>: Glucoza anormala<br />
(carbohidrati):<br />
- reglementare<br />
- toleranta<br />
Diabet, chimic<br />
Diabet, latent<br />
Intoleranta:<br />
- scazuta a glicemiei pe<br />
nemancate (IFG)<br />
- scazuta la glucoza<br />
(carbohidrati) (IGT)<br />
Prediabet<br />
Exclu<strong>de</strong>: diabet mellitus (E10-E14)<br />
nivel ridicat al glucozei in<br />
sange (R73)<br />
Reglementarea intolerantei la glucoza<br />
cu angiopatie periferica<br />
E09.01 Reglementarea intolerantei la glucoza<br />
cu angiopatie periferica fara gangrena<br />
E09.02 Reglementarea intolerantei la glucoza<br />
cu angiopatie periferica cu gangrena<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 73
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E09.1 Reglementarea intolerantei la glucoza<br />
cu caracteristici <strong>de</strong> rezistenta la<br />
insulina<br />
Reglementarea intolerantei la glucoza cu:<br />
- hiperten<strong>si</strong>une cu:<br />
- orice afectiune <strong>de</strong> mai jos<br />
- obezitate NOS<br />
- <strong>de</strong>pozit <strong>de</strong> gra<strong>si</strong>me viscerala crescut<br />
- rezistenta la insulina NOS<br />
- una sau mai multe din urmatoarele:<br />
- achanto<strong>si</strong>s nigricans<br />
- dislipi<strong>de</strong>mia<br />
- hiperinsulinism<br />
- obezitate (intrunirea criteriilor OMS<br />
sau altele recunoscute)<br />
E09.8 Reglementarea intolerantei la glucoza<br />
cu complicatii nespecificate<br />
E09.9 Reglementarea intolerantei la glucoza<br />
fara complicatii<br />
E10 Diabet mellitus tip 1<br />
Inclu<strong>de</strong>: diabet (mellitus):<br />
74<br />
- autoimun<br />
- fragil<br />
- idiopatic<br />
- insulino-<strong>de</strong>pen<strong>de</strong>nt [IDDM]<br />
- cu <strong>de</strong>but la tineri<br />
- predispus la cetoza<br />
Exclu<strong>de</strong>: diabet mellitus (datorit) (in):<br />
- neonatal (P70.2)<br />
- NOS (E14.-)<br />
- alte forme specificate<br />
(E13.-)<br />
- sarcina, nastere <strong>si</strong> lauzie<br />
(O24.-)<br />
- tip 2 (E11.-)<br />
glicozuria:<br />
- NOS (R81)<br />
- renala (E74.8)<br />
reglementarea intolerantei la<br />
glucoza (E09.-)<br />
hipoinsulinemie<br />
postprocedurala (E89.1)<br />
E10.1 Diabet mellitus tip 1 cu acidoza<br />
E10.11 Diabet mellitus tip 1 cu ketoacidoza,<br />
fara coma<br />
Diabet mellitus tip 1 cu ketoacidoza NOS<br />
E10.12 Diabet mellitus tip 1 cu ketoacidoza,<br />
cu coma<br />
Diabet mellitus tip 1cu coma<br />
hiperglicemica NOS<br />
E10.13 Diabet mellitus tip 1 cu acidoza lactica,<br />
fara coma<br />
Diabet mellitus tip 1 cu acidoza lactica<br />
NOS<br />
E10.14 Diabet mellitus tip 1 cu acidoza lactica,<br />
cu coma<br />
E10.15 Diabet mellitus tip 1 cu ketoacidoza,<br />
cu acidoza lactica, fara coma<br />
Diabet mellitus tip 1 cu ketoacidoza, cu<br />
acidoza lactica NOS<br />
E10.16 Diabet mellitus tip 1 cu ketoacidoza,<br />
cu acidoza lactica, cu coma<br />
E10.2 Diabet mellitus tip 1 cu complicatii<br />
renale<br />
E10.21 Diabet mellitus tip 1 cu nefropatie<br />
diabetica incipienta<br />
Diabet mellitus tip 1 cu:<br />
- glomerular(a):<br />
- membrana bazala ingrosata<br />
- expan<strong>si</strong>une mezangiala<br />
- nefropatie incipienta (timpurie)<br />
(rever<strong>si</strong>bila)<br />
- microalbuminuria:<br />
- constanta<br />
- per<strong>si</strong>stenta<br />
E10.22 Diabet mellitus tip 1 cu nefropatie<br />
diabetica stabilita<br />
Diabet mellitus tip 1 cu:<br />
- glomeruloscleroza:<br />
- difuza<br />
- intracapilara<br />
- nodulara<br />
- Kimmelstiel-Wilson (boala) (leziune)<br />
- macroalbuminuria<br />
- nefropatia (avansata) (NOS)<br />
(progre<strong>si</strong>va)<br />
- proteinuria (fixata) (per<strong>si</strong>stenta)<br />
E10.23 Diabet mellitus tip 1 cu boala renala<br />
stadiu final [ESRD]<br />
Diabet mellitus tip 1 cu insuficienta<br />
renala cronica sau leziune renala cronica<br />
in afectiunile cla<strong>si</strong>ficabile la E10.22<br />
E10.29 Diabet mellitus tip 1 cu alte complicatii<br />
renale specificate<br />
Diabet mellitus tip 1 cu:<br />
- insuficienta renala acuta<br />
- necroza medulara (papilara)<br />
E10.3 Diabet mellitus tip 1 cu complicatii<br />
oculare<br />
E10.31 Diabet mellitus tip 1 cu retinopatie <strong>de</strong><br />
fond<br />
Diabet mellitus tip 1 cu:<br />
- retinal(a):<br />
- hemoragie (cu puncte <strong>si</strong> pete) (sub<br />
forma <strong>de</strong> flacara)<br />
- exudat<br />
- microanevrism<br />
- dilatare venoasa<br />
- retinopatie NOS<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E10.32 Diabet mellitus tip 1 cu retinopatie<br />
preproliferativa<br />
Diabet mellitus tip 1 cu:<br />
- anormalitati microvasculare intraretinale<br />
[IRMA]<br />
- retinal(a):<br />
- pete sub forma vatoasa<br />
- hemoragii (cu pete) (rotun<strong>de</strong>) (mici)<br />
- ischemia<br />
- venos(oasa):<br />
- perlata<br />
- buclata<br />
- dublata<br />
E10.33 Diabet mellitus tip 1 cu retinopatie<br />
proliferativa<br />
Diabet mellitus tip 1 cu:<br />
- hemoragie<br />
- preretinala<br />
- sticloasa<br />
- formare <strong>de</strong> vas nou (neovascularizatie)<br />
- tractiune retinala fara <strong>de</strong>tasare<br />
E10.34 Diabet mellitus tip 1 cu alte retinopatii<br />
Diabet mellitus tip 1 cu:<br />
- macular:<br />
- e<strong>de</strong>m (focal) (generalizat)<br />
(intraretinal)<br />
- sub forma <strong>de</strong> stea<br />
- maculopatie (circinat) (ischemic)<br />
- ingrosare retinala<br />
E10.35 Diabet mellitus tip 1 cu boala oculara<br />
avansata<br />
Diabet mellitus tip 1 cu:<br />
- glaucom neovascular<br />
- rubeoza irisului [rubeo<strong>si</strong>s iridis]<br />
- tractiunea retinei <strong>de</strong>tasate<br />
E10.36 Diabet mellitus tip 1 cu cataracta<br />
diabetica<br />
Exclu<strong>de</strong>: Diabet mellitus tip 1 cu<br />
cataracta cu <strong>de</strong>but la<br />
varsta timpurie (E10.39)<br />
E10.39 Diabet mellitus tip 1 cu alte complicatii<br />
oculare specificate<br />
Diabet mellitus tip 1 cu cataracta cu<br />
<strong>de</strong>but la varsta timpurie<br />
E10.4 Diabet mellitus tip 1 cu cataracta cu<br />
complicatii neurologice<br />
E10.40 Diabet mellitus tip 1 cu neuropatie<br />
nespecificata<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E10.41 Diabet mellitus tip 1 cu<br />
mononeuropatie diabetica<br />
Diabet mellitus tip 1 cu:<br />
- amiotrofie<br />
- paralizia nervului cranian:<br />
- III (oculomotor)<br />
- VI (abductor)<br />
- neuropatie femurala<br />
- mononeurita multipla<br />
- oftalmoplegia<br />
- radiculopatie:<br />
- toracica<br />
- tronculara<br />
E10.42 Diabet mellitus tip 1 cu polineuropatie<br />
diabetica<br />
Diabet mellitus tip 1 cu:<br />
- neurita insulinica<br />
- neuropatie periferica:<br />
- distala <strong>si</strong>metrica<br />
- selectiva 'cu fibre mici'<br />
- senzo-motorie<br />
Exclu<strong>de</strong>: Diabet mellitus tip 1 cu<br />
polineuropatie diabetica<br />
autonoma (E10.43)<br />
E10.43 Diabet mellitus tip 1 cu neuropatie<br />
diabetica autonoma<br />
Diabet mellitus tip 1 cu:<br />
- secretie anormala (gustativa)<br />
- polineuropatie diabetica autonoma<br />
- diareea diabetica<br />
- disfunctie:<br />
- anorectala<br />
- esofagiana<br />
- insuficienta erectila (impotenta)<br />
- gastropareza<br />
- hipotonia, vezica urinara<br />
- e<strong>de</strong>m neuropatic<br />
- hipoten<strong>si</strong>une posturala<br />
E10.49 Diabet mellitus tip 1 cu alte complicatii<br />
neurologice specificate<br />
E10.5 Diabet mellitus tip 1 cu complicatii<br />
circulatorii<br />
E10.51 Diabet mellitus tip 1 cu angiopatie<br />
periferica, fara gangrena<br />
Exclu<strong>de</strong>: Diabet mellitus tip 1 cu<br />
angiopatie periferica, fara<br />
ulceratia piciorului (E10.73)<br />
E10.52 Diabet mellitus tip 1 cu angiopatie<br />
periferica, cu gangrena<br />
Exclu<strong>de</strong>: Diabet mellitus tip 1 cu<br />
angiopatie periferica, cu<br />
gangrena, cu ulceratia<br />
piciorului (E10.73)<br />
E10.53 Diabet mellitus tip 1 cu cardiomiopatie<br />
ischemica diabetica<br />
E10.6 Diabet mellitus tip 1 cu alte complicatii<br />
specificate<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 75
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E10.61 Diabet mellitus tip 1 cu complicatii<br />
diabetice musculoscheletale <strong>si</strong> ale<br />
tesutului conjunctiv specificate<br />
Diabet mellitus tip 1 cu:<br />
- artropatie Charchot<br />
- diabetica/e:<br />
- <strong>si</strong>ndromul mainii (cheiroartropatie)<br />
(contractura Dupuytren) (fibromatoza<br />
fasciala palmara)<br />
- osteopatie<br />
- periartrita umarului<br />
E10.62 Diabet mellitus tip 1 cu complicatii ale<br />
pielii <strong>si</strong> tesutului subcutanat specificate<br />
Diabet mellitus tip 1 cu:<br />
- diabetic(a):<br />
- buloasa [bullo<strong>si</strong>s diabeticorum]<br />
- <strong>de</strong>rmopatie (pete ale pielii)<br />
- eritem<br />
- rubeoza<br />
- sclero<strong>de</strong>rmie<br />
- ingrosarea pielii<br />
- necrobioza lipoidica diabetica [NLD]<br />
- telangiectazie periunghiala<br />
E10.63 Diabet mellitus tip 1 cu complicatii<br />
periodontale specificate<br />
Diabet mellitus tip 1 cu:<br />
- abces periodontal acut<br />
- periodontita<br />
E10.64 Diabet mellitus tip 1 cu hipoglicemie<br />
Diabet mellitus tip 1 cu hipoglicemie(ic):<br />
- coma<br />
- NOS<br />
- atac (convul<strong>si</strong>i) (criza)<br />
E10.65 Diabet mellitus tip 1 cu control slab<br />
Diabet mellitus tip 1:<br />
- pentru stabilizare<br />
- controlat slab<br />
- instabil<br />
E10.69 Diabet mellitus tip 1 cu alte complicatii<br />
specificate<br />
Diabet mellitus tip 1 cu:<br />
- gangrena (<strong>de</strong>rmala acuta) (bacteriana)<br />
(hemolitica):<br />
- Fournier<br />
- Meleney<br />
- fascita necrozanta<br />
- ulcer (extremitati inferioare)<br />
Exclu<strong>de</strong>: ulceratia piciorului la periferie<br />
cu:<br />
76<br />
- angiopatie (E10.73)<br />
- neuropatie (E10.73)<br />
E10.7 Diabet mellitus tip 1 cu complicatii<br />
multiple<br />
E10.71 Diabet mellitus tip 1 cu complicatii<br />
microvasculare multiple<br />
Doua sau mai multe dintre afectiunile<br />
cla<strong>si</strong>ficabile la E10.2, E10.3, E10.4,<br />
E10.53 sau E10.62<br />
E10.73 Diabet mellitus tip 1 cu ulceratia<br />
piciorului datorita unor cauze multiple<br />
Diabet mellitus tip 1 cu ulceratia<br />
piciorului la periferie cu:<br />
- angiopatie<br />
- neuropatie<br />
E10.8 Diabet mellitus tip 1 cu complicatii<br />
nespecificate<br />
E10.9 Diabet mellitus tip 1 fara complicatii<br />
E11 Diabet mellitus tip 2<br />
Inclu<strong>de</strong>: diabet (mellitus) (fara<br />
obezitate) (obezitate)<br />
- <strong>de</strong>but la adulti<br />
- datorit unui <strong>de</strong>fect al<br />
secretiei <strong>de</strong> insulina<br />
- rezistent la insulina<br />
- <strong>de</strong>but matur<br />
- noncetonic<br />
Exclu<strong>de</strong>: diabet mellitus (in):<br />
glicozuria:<br />
- NOS (R81)<br />
- renala (E74.8)<br />
- <strong>de</strong>but matur (la<br />
tineri)(MODY) (E13.-)<br />
- neonatal (E70.2)<br />
- NOS (E14.-)<br />
- alte forme specificate<br />
(E13.-)<br />
- sarcina, nastere <strong>si</strong> lauzie<br />
(O24.-)<br />
- Tip 1 (E10.-)<br />
reglementarea intolerantei la<br />
glucoza (E09.-)<br />
hipoinsulinemia<br />
postpreocedurala (E89.1)<br />
E11.0 Diabet mellitus tip 2 cu<br />
hiperosmolaritate<br />
E11.01 Diabet mellitus tip 2 cu<br />
hiperosmolaritate fara coma<br />
noncetotica hiperglicemicahiperosmolara<br />
[NKHHC]<br />
Diabet mellitus tip 2 cu hiperosmolaritate<br />
NOS<br />
E11.02 Diabet mellitus tip 2 cu<br />
hiperosmolaritate cu coma<br />
E11.1 Diabet mellitus tip 2 cu acidoza<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E11.11 Diabet mellitus tip 2 cu ketoacidoza,<br />
fara coma<br />
Diabet mellitus tip 2 cu ketoacidoza NOS<br />
E11.12 Diabet mellitus tip 2 cu ketoacidoza,<br />
cu coma<br />
Diabet mellitus tip 2 cu coma<br />
hiperglicemica NOS<br />
E11.13 Diabet mellitus tip 2 cu acidoza lactica,<br />
fara coma<br />
Diabet mellitus tip 2 cu acidoza lactica<br />
NOS<br />
E11.14 Diabet mellitus tip 2 cu acidoza lactica,<br />
cu coma<br />
E11.15 Diabet mellitus tip 2 cu ketoacidoza,<br />
cu acidoza lactica, fara coma<br />
Diabet mellitus tip 2 cu ketoacidoza, cu<br />
acidoza lactica NOS<br />
E11.16 Diabet mellitus tip 2 cu ketoacidoza,<br />
cu acidoza lactica, cu coma<br />
E11.2 Diabet mellitus tip 2 cu complicatii<br />
renale<br />
E11.21 Diabet mellitus tip 2 cu nefropatie<br />
diabetica incipienta<br />
Diabet mellitus tip 2 cu:<br />
- glomerular(a):<br />
- membrana bazala ingrosata<br />
- expan<strong>si</strong>une mezangiala<br />
- nefropatie incipienta (timpurie)<br />
(rever<strong>si</strong>bila)<br />
- microalbuminuria:<br />
- constanta<br />
- per<strong>si</strong>stenta<br />
E11.22 Diabet mellitus tip 2 cu nefropatie<br />
diabetica stabilita<br />
Diabet mellitus tip 2 cu:<br />
- glomeruloscleroza:<br />
- difuza<br />
- intracapilara<br />
- nodulara<br />
- Kimmelstiel-Wilson (boala) (leziune)<br />
- macroalbuminuria<br />
- nefropatia (avansata) (NOS)<br />
(progre<strong>si</strong>va)<br />
- proteinuria (fixata) (per<strong>si</strong>stenta)<br />
E11.23 Diabet mellitus tip 2 cu boala renala<br />
stadiu final [ESRD]<br />
Diabet mellitus tip 2 cu insuficienta<br />
renala cronica sau leziune renala cronica<br />
in afectiunile cla<strong>si</strong>ficabile la E11.22<br />
E11.29 Diabet mellitus tip 2 cu alte complicatii<br />
renale specificate<br />
Diabet mellitus tip 2 cu:<br />
- insuficienta renala acuta<br />
- necroza medulara (papilara)<br />
E11.3 Diabet mellitus tip 2 cu complicatii<br />
oculare<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E11.31 Diabet mellitus tip 2 cu retonopatie <strong>de</strong><br />
fond<br />
Diabet mellitus tip 2 cu:<br />
- retinal(a):<br />
- hemoragie (cu puncte <strong>si</strong> pete) (sub<br />
forma <strong>de</strong> flacara)<br />
- exudat<br />
- microanevrism<br />
- dilatare venoasa<br />
- retinopatie NOS<br />
E11.32 Diabet mellitus tip 2 cu retinopatie<br />
preproliferativa<br />
Diabet mellitus tip 2 cu:<br />
- anormalitati microvasculare intraretinale<br />
[IRMA]<br />
- retinal(a):<br />
- pete sub forma vatoasa<br />
- hemoragii (cu pete) (rotun<strong>de</strong>) (mici)<br />
- ischemia<br />
- venos(oasa):<br />
- perlata<br />
- buclata<br />
- dublata<br />
E11.33 Diabet mellitus tip 2 cu retinopatie<br />
proliferativa<br />
Diabet mellitus tip 2 cu:<br />
- hemoragie<br />
- preretinala<br />
- vitroasa<br />
- formare <strong>de</strong> vas nou (neovascularizatie)<br />
- tractiune retinala fara <strong>de</strong>tasare<br />
E11.34 Diabet mellitus tip 2 cu alte retinopatii<br />
Diabet mellitus tip 2 cu:<br />
- macular:<br />
- e<strong>de</strong>m (focal) (generalizat)<br />
(intraretinal)<br />
- sub forma <strong>de</strong> stea<br />
- maculopatie (circinat) (ischemic)<br />
- ingrosare retinala<br />
E11.35 Diabet mellitus tip 2 cu boala oculara<br />
avansata<br />
Diabet mellitus tip 2 cu:<br />
- glaucom neovascular<br />
- rubeoza irisului [rubeo<strong>si</strong>s iridis]<br />
- tractiunea retinei <strong>de</strong>tasate<br />
E11.36 Diabet mellitus tip 2 cu cataracta<br />
diabetica<br />
Exclu<strong>de</strong>: Diabet mellitus tip 2 cu<br />
cataracta cu <strong>de</strong>but la<br />
varsta timpurie (E11.39)<br />
E11.39 Diabet mellitus tip 2 cu alte complicatii<br />
oculare specificate<br />
Diabet mellitus tip 2 cu cataracta cu<br />
<strong>de</strong>but la varsta timpurie<br />
E11.4 Diabet mellitus tip 2 cu complicatii<br />
neurologice<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 77
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E11.40 Diabet mellitus tip 2 cu neuropatie<br />
nespecificata<br />
E11.41 Diabet mellitus tip 2 cu<br />
mononeuropatie diabetica<br />
Diabet mellitus tip 2 cu:<br />
- amiotrofie<br />
- paralizia nervului cranian:<br />
- III (oculomotor)<br />
- VI (abductor)<br />
- neuropatie femurala<br />
- mononeurita multipla<br />
- oftalmoplegia<br />
- radiculopatie:<br />
- toracica<br />
- troncular<br />
E11.42 Diabet mellitus tip 2 cu polineuropatie<br />
diabetica<br />
Diabet mellitus tip 2 cu:<br />
- neurita insulinica<br />
- neuropatie periferica:<br />
- distala <strong>si</strong>metrica<br />
- selectiva 'cu fibre mici'<br />
- senzorimotorie<br />
Exclu<strong>de</strong>: Diabet mellitus tip 2 cu<br />
polineuropatie diabetica<br />
autonoma (E11.43)<br />
E11.43 Diabet mellitus tip 2 cu neuropatie<br />
diabetica autonoma<br />
Diabet mellitus tip 2 cu:<br />
- secretie anormala (gustativa)<br />
- polineuropatie diabetica autonoma<br />
- diareea diabetica<br />
- disfunctie:<br />
- anorectala<br />
- esofagiana<br />
- insuficienta erectila (impotenta)<br />
- gastropareza<br />
- hipotonie, vezica urinara<br />
- e<strong>de</strong>m neuropatic<br />
- hipoten<strong>si</strong>une posturala<br />
E11.49 Diabet mellitus tip 2 cu alte complicatii<br />
neurologice specificate<br />
E11.5 Diabet mellitus tip 2 cu complicatii<br />
circulatorii<br />
E11.51 Diabet mellitus tip 2 cu angiopatie<br />
periferica, fara gangrena<br />
Exclu<strong>de</strong>: Diabet mellitus tip 2 cu<br />
angiopatie periferica, fara<br />
ulceratia piciorului (E11.73)<br />
E11.52 Diabet mellitus tip 2 cu angiopatie<br />
periferica, cu gangrena<br />
Exclu<strong>de</strong>: Diabet mellitus tip 2 cu<br />
angiopatie periferica, cu<br />
gangrena, cu ulceratia<br />
piciorului (E11.73)<br />
E11.53 Diabet mellitus tip 2 cu cardiomiopatie<br />
ischemica diabetica<br />
78<br />
E11.6 Diabet mellitus tip 2 cu alte complicatii<br />
specificate<br />
E11.61 Diabet mellitus tip 2 cu complicatii<br />
diabetice musculoscheletale <strong>si</strong> ale<br />
tesutului conjunctiv specificate<br />
Diabet mellitus tip 2 cu:<br />
- artropatie Charchot<br />
- diabetica/e:<br />
- <strong>si</strong>ndromul mainii (cheiroartropatie)<br />
(contractura Dupuytren) (fibromatoza<br />
fasciala palmara)<br />
- osteopatie<br />
- periartrita umarului<br />
E11.62 Diabet mellitus tip 2 cu complicatii ale<br />
pielii <strong>si</strong> tesutului subcutanat specificate<br />
Diabet mellitus tip 2 cu:<br />
- diabetic(a):<br />
- buloasa [bullo<strong>si</strong>s diabeticorum]<br />
- <strong>de</strong>rmopatie (pete ale pielii)<br />
- eritem<br />
- rubeoza<br />
- sclero<strong>de</strong>rmie<br />
- ingrosarea pielii<br />
- necrobioza lipoidica diabetica [NLD]<br />
- telangiectazie periunghiala<br />
E11.63 Diabet mellitus tip 2 cu complicatii<br />
periodontale specificate<br />
Diabet mellitus tip 2 cu:<br />
- abces periodontal acut<br />
- periodontita<br />
E11.64 Diabet mellitus tip 2 cu hipoglicemie<br />
Diabet mellitus tip 2 cu hipoglicemie(ic):<br />
- coma<br />
- NOS<br />
- atac (convul<strong>si</strong>i) (criza)<br />
E11.65 Diabet mellitus tip 2 cu control slab<br />
Diabet mellitus tip 2:<br />
- pentru stabilizare<br />
- controlat slab<br />
- instabil<br />
E11.69 Diabet mellitus tip 2 cu alte complicatii<br />
specificate<br />
Diabet mellitus tip 2 cu:<br />
- gangrena (<strong>de</strong>rmala acuta) (bacteriana)<br />
(hemolitica):<br />
- Fournier<br />
- Meleney<br />
- fascita necrozanta<br />
- ulcer (extremitati inferioare)<br />
Exclu<strong>de</strong>: ulceratia piciorului la periferie<br />
cu:<br />
- angiopatie (E11.73)<br />
- neuropatie (E11.73)<br />
E11.7 Diabet mellitus tip 2 cu complicatii<br />
multiple<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E11.71 Diabet mellitus tip 2 cu complicatii<br />
microvasculare multiple<br />
Doua sau mai multe dintre afectiunile<br />
cla<strong>si</strong>ficabile la E11.2, E11.3, E11.4,<br />
E11.53 sau E11.62<br />
E11.72 Diabet mellitus tip 2 cu caracteristici<br />
<strong>de</strong> rezistenta la insulina<br />
Diabet mellitus tip 2 cu:<br />
- hiperten<strong>si</strong>une cu:<br />
- orice afectiune <strong>de</strong> mai jos<br />
- obezitate NOS<br />
- <strong>de</strong>pozit <strong>de</strong> gra<strong>si</strong>me viscerala crescut<br />
- rezistenta la insulina NOS<br />
- una sau mai multe din urmatoarele:<br />
- achanto<strong>si</strong>s nigricans<br />
- dislipi<strong>de</strong>mia<br />
- hiperinsulinism<br />
- obezitate (intrunirea criteriilor OMS<br />
sau altele recunoscute)<br />
E11.73 Diabet mellitus tip 2 cu ulceratia<br />
piciorului datorita unor cauze multiple<br />
Diabet mellitus tip 2 cu ulceratia<br />
piciorului <strong>si</strong> la periferie cu:<br />
- angiopatie<br />
- neuropatie<br />
E11.8 Diabet mellitus tip 2 cu complicatii<br />
nespecificate<br />
E11.9 Diabet mellitus tip 2 fara complicatii<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E13 Alte forme specificate <strong>de</strong> diabet<br />
mellitus<br />
Folo<strong>si</strong>ti un cod aditional pentru orice<br />
afectiune <strong>de</strong> baza sau <strong>si</strong>ndrom genetic<br />
Inclu<strong>de</strong>: diabet mellitus (datorita) (in)<br />
(secundar) (cu):<br />
- indus medicamentos sau<br />
indus chimic<br />
- endocrinopatie<br />
- <strong>de</strong>fect genetic <strong>de</strong>:<br />
- functionare celule beta<br />
- actiune a insulinei<br />
- <strong>si</strong>ndrom genetic<br />
- boala imuno-mediata<br />
- infectie<br />
- <strong>de</strong>but matur la tineri<br />
(MODY)<br />
- boala pancreatica exocrina<br />
Exclu<strong>de</strong>: diabet mellitus (in):<br />
- neonatal (P70.2)<br />
- NOS (E14.-)<br />
- sarcina, nastere <strong>si</strong> lauzia<br />
(O24.-)<br />
- Tip 1 (E10.-)<br />
- Tip 2 (E11.-)<br />
glicozuria:<br />
- NOS (R81)<br />
- renala (E74.8)<br />
reglementarea intolerantei la<br />
glucoza (E09.-)<br />
E13.0 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu hiperosmolaritate<br />
E13.01 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu hiperosmolaritate, fara<br />
coma noncetotica hiperglicemicahiperosmolara<br />
[NKHHC]<br />
Diabet mellitus NEC cu<br />
hiperosmolaritate NOS<br />
E13.02 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu hiperosmolaritate, cu coma<br />
E13.1 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu acidoza<br />
E13.11 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu ketoacidoza, fara coma<br />
Diabet mellitus NEC cu ketoacidoza<br />
NOS<br />
E13.12 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu ketoacidoza, cu coma<br />
Diabet mellitus NEC cu coma<br />
hiperglicemica NOS<br />
E13.13 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu acidoza lactica, fara coma<br />
Diabet mellitus NEC cu acidoza lactica<br />
NOS<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 79
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E13.14 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu acidoza lactica, cu coma<br />
E13.15 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu ketoacidoza, cu acidoza<br />
lactica, fara coma<br />
Diabet mellitus NEC cu ketoacidoza cu<br />
acidoza lactica NOS<br />
E13.16 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu ketoacidoza, cu acidoza<br />
lactica, cu coma<br />
E13.2 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu complicatii renale<br />
E13.21 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu nefropatie diabetica<br />
incipienta<br />
Diabet mellitus NEC cu:<br />
- glomerular(a):<br />
- membrana bazala ingrosata<br />
- expan<strong>si</strong>une mezangiala<br />
- nefropatie incipienta (timpurie)<br />
(rever<strong>si</strong>bila)<br />
- microalbuminuria:<br />
- constanta<br />
- per<strong>si</strong>stenta<br />
E13.22 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu nefropatie diabetica<br />
stabilita<br />
Diabet mellitus NEC cu:<br />
- glomeruloscleroza:<br />
- difuza<br />
- intracapilara<br />
- nodulara<br />
- Kimmelstiel-Wilson (boala) (leziune)<br />
- macroalbuminuria<br />
- nefropatia (avansata) (NOS)<br />
(progre<strong>si</strong>va)<br />
- proteinuria (fixata) (per<strong>si</strong>stenta)<br />
E13.23 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu boala renala stadiu final<br />
[ESRD]<br />
Diabet mellitus tip 2 cu insuficienta<br />
renala cronica sau leziune renala cronica<br />
in afectiunile cla<strong>si</strong>ficabile la E13.22<br />
E13.29 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu alte complicatii renale<br />
specificate<br />
Diabet mellitus NEC cu:<br />
- insuficienta renala acuta<br />
- necroza medulara (papilara)<br />
E13.3 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu complicatii oculare<br />
80<br />
E13.31 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu retinopatie <strong>de</strong> fond<br />
Diabet mellitus NEC cu:<br />
- retinal(a):<br />
- hemoragie (cu puncte <strong>si</strong> pete) (sub<br />
forma <strong>de</strong> flacara)<br />
- exudat<br />
- microanevrism<br />
- dilatare venoasa<br />
- retinopatie NOS<br />
E13.32 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu retinopatie preproliferativa<br />
Diabet mellitus NEC cu:<br />
- anormalitati microvasculare intraretinale<br />
[IRMA]<br />
- retinal(a):<br />
- pete sub forma vatoasa<br />
- hemoragii (cu pete) (rotunda) (mica)<br />
- ischemia<br />
- venos(oasa):<br />
- perlata<br />
- buclata<br />
- dublata<br />
E13.33 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu retinopatie proliferativa<br />
Diabet mellitus NEC cu:<br />
- hemoragie<br />
- preretinala<br />
- vitroasa<br />
- formare <strong>de</strong> vas nou (neovascularizatie)<br />
- tractiune retinala fara <strong>de</strong>tasare<br />
E13.34 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu alte retinopatii<br />
Diabet mellitus NEC cu:<br />
- macular:<br />
- e<strong>de</strong>m (focal) (generalizat)<br />
(intraretinal)<br />
- sub forma <strong>de</strong> stea<br />
- maculopatie (circinat) (ischemic)<br />
- ingrosare retinala<br />
E13.35 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu boala oculara avansata<br />
Diabet mellitus NEC cu:<br />
- glaucom neovascular<br />
- rubeoza irisului [rubeo<strong>si</strong>s iridis]<br />
- tractiunea retinei <strong>de</strong>tasate<br />
E13.36 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu cataracta diabetica<br />
Exclu<strong>de</strong>: Diabet mellitus NEC cu<br />
cataracta cu <strong>de</strong>but la<br />
varsta timpurie (E13.39)<br />
E13.39 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu alte complicatii oculare<br />
specificate<br />
Diabet mellitus NEC cu cataracta cu<br />
<strong>de</strong>but la varsta timpurie<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E13.4 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu complicatii neurologice<br />
E13.40 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu neuropatie nespecificata<br />
E13.41 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu mononeuropatie diabetica<br />
Diabet mellitus NEC cu:<br />
- amiotrofie<br />
- paralizia nervului cranian:<br />
- III (oculomotor)<br />
- VI (abductor)<br />
- neuropatie femurala<br />
- mononeurita multipla<br />
- oftalmoplegia<br />
- radiculopatie:<br />
- toracica<br />
- troncular<br />
E13.42 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu polineuropatie diabetica<br />
Diabet mellitus NEC cu:<br />
- neurita insulinica<br />
- neuropatie periferica:<br />
- distala <strong>si</strong>metrica<br />
- selectiva 'cu fibre mici'<br />
- senzorimotorie<br />
Exclu<strong>de</strong>: diabet mellitus NEC cu<br />
polineuropatie diabetica<br />
autonoma (E13.43)<br />
E13.43 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu neuropatie diabetica<br />
autonoma<br />
Diabet mellitus NEC cu:<br />
- transpiratie anormala (gustativa)<br />
- polineuropatie diabetica autonoma<br />
- diareea diabetica<br />
- disfunctie:<br />
- anorectala<br />
- esofagiana<br />
- insuficienta erectila (impotenta)<br />
- gastropareza<br />
- hipotonia, vezica urinara<br />
- e<strong>de</strong>m neuropatic<br />
- hipoten<strong>si</strong>une posturala<br />
E13.49 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu alte complicatii neurologice<br />
specificate<br />
E13.5 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu complicatii circulatorii<br />
E13.51 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu angiopatie periferica, fara<br />
gangrena<br />
Exclu<strong>de</strong>: diabet mellitus NEC cu<br />
angiopatie periferica, cu<br />
ulceratia piciorului (E13.73)<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E13.52 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu angiopatie periferica, cu<br />
gangrena<br />
Exclu<strong>de</strong>: diabet mellitus NEC cu<br />
angiopatie periferica, cu<br />
gangrena, cu ulceratia<br />
piciorului (E13.73)<br />
E13.53 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu cardiomiopatie ischemica<br />
diabetica<br />
E13.6 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu alte complicatii specificate<br />
E13.61 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu complicatii diabetice<br />
musculoscheletale <strong>si</strong> ale tesutului<br />
conjunctiv specificate<br />
Diabet mellitus NEC cu:<br />
- artropatie Charchot<br />
- diabetica/e:<br />
- <strong>si</strong>ndromul mainii (cheiroartropatie)<br />
(contractura Dupuytren) (fibromatoza<br />
fasciala palmara)<br />
- osteopatie<br />
- periartrita umarului<br />
E13.62 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu complicatii ale pielii <strong>si</strong><br />
tesutului subcutanat specificate<br />
Diabet mellitus NEC1 cu:<br />
- diabetic(a):<br />
- buloasa [bullo<strong>si</strong>s diabeticorum]<br />
- <strong>de</strong>rmopatie (pete ale pielii)<br />
- eritem<br />
- rubeoza<br />
- sclero<strong>de</strong>rmie<br />
- ingrosarea pielii<br />
- necrobioza lipoidica diabetica [NLD]<br />
- telangiectazie periunghiala<br />
E13.63 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu complicatii periodontale<br />
specificate<br />
Diabet mellitus NEC cu:<br />
- abces periodontal acut<br />
- periodontita<br />
E13.64 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu hipoglicemie<br />
Diabet mellitus NEC cu hipoglicemie(ic):<br />
- coma<br />
- NOS<br />
- atac (convul<strong>si</strong>i) (criza)<br />
E13.65 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu control slab<br />
Alte forme specificate <strong>de</strong> diabet mellitus:<br />
- pentru stabilizare<br />
- controlat slab<br />
- instabil<br />
- cu esecul tratamentului secundar<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 81
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E13.69 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu alte complicatii specificate<br />
Diabet mellitus NEC cu:<br />
- gangrena (<strong>de</strong>rmala acuta) (bacteriana)<br />
(hemolitica):<br />
- Fournier<br />
- Meleney<br />
- fascita necrozanta<br />
- ulcer (extremitati inferioare)<br />
Exclu<strong>de</strong>: ulceratia piciorului la periferie<br />
cu:<br />
82<br />
- angiopatie (E13.73)<br />
- neuropatie (E13.73)<br />
E13.7 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu complicatii multiple<br />
E13.71 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu complicatii microvasculare<br />
multiple<br />
Doua sau mai multe dintre afectiunile<br />
cla<strong>si</strong>ficabile la E13.2, E13.3, E13.4,<br />
E13.53 sau E13.62<br />
E13.72 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu caracteristici <strong>de</strong> rezistenta<br />
la insulina<br />
Alte forme specificate <strong>de</strong> diabet mellitus<br />
cu:<br />
- hiperten<strong>si</strong>une cu:<br />
- orice afectiune <strong>de</strong> mai jos<br />
- obezitate NOS<br />
- <strong>de</strong>pozit <strong>de</strong> gra<strong>si</strong>me viscerala crescut<br />
- rezistenta la insulina NOS<br />
- una sau mai multe din urmatoarele:<br />
- achanto<strong>si</strong>s nigricans<br />
- dislipi<strong>de</strong>mia<br />
- hiperinsulinism<br />
- obezitate (intrunirea criteriilor OMS<br />
sau altele recunoscute)<br />
E13.73 Alte forme specificate <strong>de</strong> diabet<br />
mellitus ulceratia piciorului datorita<br />
unor cauza multiple<br />
Diabet mellitus NEC cu ulceratia<br />
piciorului <strong>si</strong> la periferie:<br />
- angiopatie<br />
- neuropatie<br />
E13.8 Alte forme specificate <strong>de</strong> diabet<br />
mellitus cu complicatii nespecificate<br />
E13.9 Alte forme specificate <strong>de</strong> diabet<br />
mellitus fara complicatii<br />
E14 Diabet mellitus nespecificat<br />
Diabet mellitus NOS<br />
Exclu<strong>de</strong>: diabet mellitus (in):<br />
- neonatal (P70.2)<br />
- non-insulino <strong>de</strong>pen<strong>de</strong>nt<br />
(E11.-)<br />
- sarcina, nastere <strong>si</strong> lauzie<br />
(O24.-)<br />
- Tip 1 (E10.-)<br />
- Tip 2 (E11.-)<br />
glicozuria:<br />
- NOS (R81)<br />
- renala (E74.8)<br />
reglementarea intolerantei la<br />
glucoza (E09.-)<br />
hipoinsulinemia<br />
postprocedurala (E89.1)<br />
E14.0 Diabet mellitus nespecificat cu<br />
hiperosmolaritate<br />
E14.01 Diabet mellitus nespecificat cu<br />
hiperosmolaritate, fara coma<br />
noncetotica hiperglicemicahiperosmolara<br />
[NKHHC]<br />
Diabet mellitus NOS cu<br />
hiperosmolaritate NOS<br />
E14.02 Diabet mellitus nespecificat cu<br />
hiperosmolaritate, cu coma<br />
E14.1 Diabet mellitus nespecificat cu acidoza<br />
E14.11 Diabet mellitus nespecificat cu<br />
ketoacidoza, fara coma<br />
Diabet mellitus NOS cu ketoacidoza<br />
NOS<br />
E14.12 Diabet mellitus nespecificat cu<br />
ketoacidoza, cu coma<br />
Diabet mellitus NOS cu coma<br />
hiperglicemica NOS<br />
E14.13 Diabet mellitus nespecificat cu acidoza<br />
lactica, fara coma<br />
Diabet mellitus NOS cu acidoza lactica<br />
NOS<br />
E14.14 Diabet mellitus nespecificat cu acidoza<br />
lactica, cu coma<br />
E14.15 Diabet mellitus nespecificat cu<br />
ketoacidoza, cu acidoza lactica, fara<br />
coma<br />
Diabet mellitus NOS cu ketoacidoza cu<br />
acidoza lactica NOS<br />
E14.16 Diabet mellitus nespecificat cu<br />
ketoacidoza, cu acidoza lactica, cu<br />
coma<br />
E14.2 Diabet mellitus nespecificat cu<br />
complicatii renale<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E14.21 Diabet mellitus nespecificat cu<br />
nefropatie diabetica incipienta<br />
Diabet mellitus NOS cu:<br />
- glomerular(a):<br />
- membrana bazala ingrosata<br />
- expan<strong>si</strong>une mezangiala<br />
- nefropatie incipienta (timpurie)<br />
(rever<strong>si</strong>bila)<br />
- microalbuminuria:<br />
- constanta<br />
- per<strong>si</strong>stenta<br />
E14.22 Diabet mellitus nespecificat cu<br />
nefropatie diabetica stabilita<br />
Diabet mellitus NOS cu:<br />
- glomeruloscleroza:<br />
- difuza<br />
- intracapilara<br />
- nodulara<br />
- Kimmelstiel-Wilson (boala) (leziune)<br />
- macroalbuminuria<br />
- nefropatia (avansata) (NOS) (progre<strong>si</strong>va)<br />
- proteinuria (fixata) (per<strong>si</strong>stenta)<br />
E14.23 Diabet mellitus nespecificat cu boala<br />
renala stadiu final [ESRD]<br />
Diabet mellitus NOS cu insuficienta<br />
renala cronica sau leziune renala cronica<br />
in afectiunile cla<strong>si</strong>ficabile la E14.22<br />
E14.29 Diabet mellitus nespecificat cu alte<br />
complicatii renale specificate<br />
Diabet mellitus NOS cu:<br />
- insuficienta renala acuta<br />
- necroza medulara (papilara)<br />
E14.3 Diabet mellitus nespecificat cu<br />
complicatii oculare<br />
E14.31 Diabet mellitus nespecificat cu<br />
retinopatie <strong>de</strong> fond<br />
Diabet mellitus NOS cu:<br />
- retinal(a):<br />
- hemoragie (cu puncte <strong>si</strong> pete) (sub<br />
forma <strong>de</strong> flacara)<br />
- exudat<br />
- microanevrism<br />
- dilatare venoasa<br />
- retinopatie NOS<br />
E14.32 Diabet mellitus nespecificat cu<br />
retinopatie preproliferativa<br />
Diabet mellitus NOS cu:<br />
- anormalitati microvasculare intraretinale<br />
[IRMA]<br />
- retinal(a):<br />
- pete sub forma vatoasa<br />
- hemoragii (cu pete) (rotunda) (mica)<br />
- ischemia<br />
- venos(oasa):<br />
- perlata<br />
- buclata<br />
- dublata<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E14.33 Diabet mellitus nespecificat cu<br />
retinopatie proliferativa<br />
Diabet mellitus NOS cu:<br />
- hemoragie<br />
- preretinala<br />
- vitroasa<br />
- formare <strong>de</strong> vas nou (neovascularizatie)<br />
- tractiune retinala fara <strong>de</strong>tasare<br />
E14.34 Diabet mellitus nespecificat cu alte<br />
retinopatii<br />
Diabet mellitus NOS cu:<br />
- macular:<br />
- e<strong>de</strong>m (focal) (generalizat)<br />
(intraretinal)<br />
- sub forma <strong>de</strong> stea<br />
- maculopatie (circinat) (ischemic)<br />
- ingrosare retinala<br />
E14.35 Diabet mellitus nespecificat cu boala<br />
oculara avansata<br />
Diabet mellitus NOS cu:<br />
- glaucom neovascular<br />
- rubeoza irisului [rubeo<strong>si</strong>s iridis]<br />
- tractiunea retinei <strong>de</strong>tasate<br />
E14.36 Diabet mellitus nespecificat cu<br />
cataracta diabetica<br />
Exclu<strong>de</strong>: Diabet mellitus NOS cu<br />
cataracta cu <strong>de</strong>but la<br />
varsta timpurie (E14.39)<br />
E14.39 Diabet mellitus nespecificat cu alte<br />
complicatii oculare specificate<br />
Diabet mellitus NOS cu cataracta cu<br />
<strong>de</strong>but la varsta timpurie<br />
E14.4 Diabet mellitus nespecificat cu<br />
complicatii neurologice<br />
E14.40 Diabet mellitus nespecificat cu<br />
neuropatie nespecificata<br />
E14.41 Diabet mellitus nespecificat cu<br />
mononeuropatie diabetica<br />
Diabet mellitus NOS cu:<br />
- amiotrofie<br />
- paralizia nervului cranian:<br />
- III (oculomotor)<br />
- VI (abductor)<br />
- neuropatie femurala<br />
- mononeurita multipla<br />
- oftalmoplegia<br />
- radiculopatie:<br />
- toracica<br />
- troncular<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 83
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E14.42 Diabet mellitus nespecificat cu<br />
polineuropatie diabetica<br />
Diabet mellitus NOS cu:<br />
- neurita insulinica<br />
- neuropatie periferica:<br />
- distala <strong>si</strong>metrica<br />
- selectiva 'cu fibre mici'<br />
- senzorimotorie<br />
Exclu<strong>de</strong>: diabet mellitus NOS cu<br />
polineuropatie diabetica<br />
autonoma (E14.43)<br />
E14.43 Diabet mellitus nespecificat cu<br />
neuropatie diabetica autonoma<br />
Diabet mellitus NOS cu:<br />
- transpiratie anormala (gustativa)<br />
- polineuropatie diabetica autonoma<br />
- diareea diabetica<br />
- disfunctie:<br />
- anorectala<br />
- esofagiana<br />
- insuficienta erectila (impotenta)<br />
- gastropareza<br />
- hipotonia, vezica urinara<br />
- e<strong>de</strong>m neuropatic<br />
- hipoten<strong>si</strong>une posturala<br />
E14.49 Diabet mellitus nespecificat cu alte<br />
complicatii neurologice specificate<br />
E14.5 Diabet mellitus nespecificat cu<br />
complicatii circulatorii<br />
E14.51 Diabet mellitus nespecificat cu<br />
agiopatie periferica, fara gangrena<br />
Exclu<strong>de</strong>: diabet mellitus NOS cu<br />
angiopatie periferica, cu<br />
ulceratia piciorului (E14.73)<br />
E14.52 Diabet mellitus nespecificat cu<br />
agiopatie periferica, cu gangrena<br />
Exclu<strong>de</strong>: diabet mellitus NOS cu<br />
angiopatie periferica, cu<br />
gangrena, cu ulceratia<br />
piciorului (E14.73)<br />
E14.53 Diabet mellitus nespecificat cu<br />
cardiomiopatie ischemica diabetica<br />
E14.6 Diabet mellitus nespecificat cu alte<br />
complicatii specificate<br />
E14.61 Diabet mellitus nespecificat cu<br />
complicatii diabetice musculoscheletale<br />
<strong>si</strong> ale tesutului conjunctiv specificate<br />
Diabet mellitus NOS cu:<br />
- artropatie Charchot<br />
- diabetica/e:<br />
- <strong>si</strong>ndromul mainii (cheiroartropatie)<br />
(contractura Dupuytren) (fibromatoza<br />
fasciala palmara)<br />
- osteopatie<br />
- periartrita umarului<br />
84<br />
E14.62 Diabet mellitus nespecificat cu<br />
complicatii ale pielii <strong>si</strong> tesutului<br />
subcutanat specificate<br />
Diabet mellitus NOS cu:<br />
- diabetic(a):<br />
- buloasa [bullo<strong>si</strong>s diabeticorum]<br />
- <strong>de</strong>rmopatie (pete ale pielii)<br />
- eritem<br />
- rubeoza<br />
- sclero<strong>de</strong>rmie<br />
- ingrosarea pielii<br />
- necrobioza lipoidica diabetica [NLD]<br />
- telangiectazie periungveala<br />
E14.63 Diabet mellitus nespecificat cu<br />
complicatii periodontale specificate<br />
Diabet mellitus NOS cu:<br />
- abces periodontal acut<br />
- periodontita<br />
E14.64 Diabet mellitus nespecificat cu<br />
hipoglicemie<br />
Diabet mellitus NOS cu hipoglicemie(ic):<br />
- coma<br />
- NOS<br />
- atac (convul<strong>si</strong>i) (criza)<br />
E14.65 Diabet mellitus nespecificat cu control<br />
slab<br />
Diabet mellitus nespecificat:<br />
- pentru stabilizare<br />
- controlat slab<br />
- instabil<br />
- cu esecul tratamentului secundar<br />
E14.69 Diabet mellitus nespecificat cu alte<br />
complicatii specifice<br />
Diabet mellitus NOS cu:<br />
- gangrena (<strong>de</strong>rmala acuta) (bacteriana)<br />
(hemolitica):<br />
- Fournier<br />
- Meleney<br />
- fascita necrozanta<br />
- ulcer (extremitati inferioare)<br />
Exclu<strong>de</strong>: ulceratia piciorului la periferie<br />
cu:<br />
- angiopatie (E14.73)<br />
- neuropatie (E14.73)<br />
E14.7 Diabet mellitus nespecificat cu<br />
complicatii multiple<br />
E14.71 Diabet mellitus nespecificat cu<br />
complicatii microvasculare multiple<br />
Doua sau mai multe dintre afectiunile<br />
cla<strong>si</strong>ficabile la E14.2, E14.3, E14.4,<br />
E14.53 sau E14.62<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E14.72 Diabet mellitus nespecificat cu<br />
caracteristici <strong>de</strong> rezistenta la insulina<br />
Diabet mellitus nespecificat cu:<br />
- hiperten<strong>si</strong>une cu:<br />
- orice afectiune <strong>de</strong> mai jos<br />
- obezitate NOS<br />
- <strong>de</strong>pozit <strong>de</strong> gra<strong>si</strong>me viscerala crescut<br />
- rezistenta la insulina NOS<br />
- una sau mai multe din urmatoarele:<br />
- achanto<strong>si</strong>s nigricans<br />
- dislipi<strong>de</strong>mia<br />
- hiperinsulinism<br />
- obezitate (intrunirea criteriilor OMS<br />
sau altele recunoscute)<br />
E14.73 Diabet mellitus nespecificat cu<br />
ulceratia piciorului datorita unor cauze<br />
multiple<br />
Diabet mellitus NOS cu ulceratia<br />
piciorului <strong>si</strong>la periferie:<br />
- angiopatie<br />
- neuropatie<br />
E14.8 Diabet mellitus nespecificat cu<br />
complicatii nespecificate<br />
E14.9 Diabet mellitus nespecificat fara<br />
complicatii<br />
Alte tulburari ale <strong>metabolism</strong>ului<br />
glucozei <strong>si</strong> ale secretiei pancreatice<br />
interne (E15-E16)<br />
E15<br />
Coma hipoglicemica nondiabetica<br />
Coma insulinica indusa medicamentos la<br />
nondiabetici<br />
Hiperinsulinism cu coma hipoglicemica<br />
Coma hipoglicemica NOS<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul, daca este indusa<br />
medicamentos.<br />
E16 Alte tulburari ale secretiei interne<br />
pancreatice<br />
E16.0 Hipoglicemia indusa medicamentos, fara<br />
coma<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul.<br />
E16.1 Alte hipoglicemii<br />
Hipoglicemia nonhiperinsulinemica<br />
functionala<br />
Hiperinsulinism:<br />
- functional<br />
- NOS<br />
Hiperplazia celulelor beta ale insulelor<br />
pancreatice NOS<br />
Encefalopatie datorita comei<br />
posthipoglicemice<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E16.2 Hipoglicemie nespecificata<br />
E16.3 Hipersecretia <strong>de</strong> glucagon<br />
Hiperplazia celulelor <strong>endocrine</strong> pancreatice<br />
cu exces <strong>de</strong> glucagon<br />
E16.4 Secretie anormala <strong>de</strong> gastrina<br />
Hipergastrinemia<br />
Sindromul Zollinger-Ellison<br />
E16.8 Alte tulburari specificate ale secretiei<br />
interne pancreatice<br />
Hipersecretia endocrina a pancreasului <strong>de</strong>:<br />
- reali<strong>si</strong>ng factor al hormonului <strong>de</strong> crestere<br />
(GHRH)<br />
- polipepti<strong>de</strong> pancreatice<br />
- somatostatin<br />
- polipepti<strong>de</strong> vasoactive intestinal<br />
E16.9 Tulburari ale secretiei interne<br />
pancreatice, nespecificate<br />
Hiperplazia celulelor insulelor lui<br />
Langerhans NOS<br />
Hiperplazia celulelor insulelor pancreatice<br />
NOS<br />
<strong>Boli</strong>le altor glan<strong>de</strong> <strong>endocrine</strong><br />
(E20-E35)<br />
Exclu<strong>de</strong>: galactoreea (N64.3)<br />
ginecomastia (N62)<br />
E20 Hipoparatiroidism<br />
Exclu<strong>de</strong>: <strong>si</strong>ndromul Di George (D82.1)<br />
hipoparatiroidism<br />
postprocedural (E89.2)<br />
tetania NOS (R29.0)<br />
hipoparatiroidism neonatal<br />
tranzitoriu (P71.4)<br />
E20.0 Hipoparatiroidism idiopatic<br />
E20.1 Pseudohipoparatiroidism<br />
E20.8 Alte hipoparatiroidisme<br />
E20.9 Hipoparatiroidism, nespecificat<br />
Tetania paratiroida<br />
E21 Hiperparatiroidism <strong>si</strong> alte tulburari<br />
ale glan<strong>de</strong>i paratiroi<strong>de</strong><br />
Exclu<strong>de</strong>: osteomalacia:<br />
- adultului (M83.-)<br />
infantila <strong>si</strong> juvenila (E55.0)<br />
E21.0 Hiperparatiroidism primar<br />
Hiperplazia paratiroi<strong>de</strong>i<br />
Osteita fibro-chistica generalizata [boala<br />
osoasa von Recklinghausen]<br />
E21.1 Hiperparatiroidism secundar, necla<strong>si</strong>ficat<br />
altun<strong>de</strong>va<br />
Exclu<strong>de</strong>: Hiperparatiroidism secundar <strong>de</strong><br />
origine renala (N25.8)<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 85
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E21.2 Alte hiperparatiroidisme<br />
Exclu<strong>de</strong>: hipercalcemia hipocalciurica<br />
familiala (E83.5)<br />
E21.3 Hiperparatiroidism, nespecificat<br />
E21.4 Alte tulburari specificate ale glan<strong>de</strong>i<br />
paratiroi<strong>de</strong><br />
E21.5 Tulburare a glan<strong>de</strong>i paratiroi<strong>de</strong>,<br />
nespecificata<br />
E22 Hipersecretia glan<strong>de</strong>i pituitare<br />
Exclu<strong>de</strong>: Sindromul Cushing (E24.-)<br />
86<br />
Sindromul Nelson (E24.1)<br />
Hipersecretia <strong>de</strong>:<br />
- ACTH neasociata cu boala<br />
Cushing (E27.0)<br />
- ACTH pituitara (E24.0)<br />
- hormon <strong>de</strong> stimulare<br />
tiroidiana (E05.8)<br />
E22.0 Acromegalia <strong>si</strong> gigantismul pituitar<br />
Artropatia asociata cu acromegalia<br />
† (M14.5*)<br />
Hipersecretia hormonului <strong>de</strong> crestere<br />
Exclu<strong>de</strong>: constitutional(a):<br />
- gigantism (E34.4)<br />
- statura inalta (E34.4)<br />
reali<strong>si</strong>ng factor al hormonului<br />
<strong>de</strong> crestere (GHRH) (E16.8)<br />
E22.1 Hiperprolactinemia<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul, daca este indusa<br />
medicamentos.<br />
E22.2 Sindromul secretiei anormale a<br />
hormonului antidiuretic<br />
E22.8 Alte hipersecretii ale glan<strong>de</strong>i pituitare<br />
Pubertate precoce centrala<br />
E22.9 Hipersecretia glan<strong>de</strong>i pituitare,<br />
nespecificata<br />
E23 Hiposecretia <strong>si</strong> alte tulburari ale<br />
glan<strong>de</strong>i pituitare<br />
Inclu<strong>de</strong>: afectiunile listate indiferent<br />
daca tulburarea se produce<br />
in glanda pituitara sau in<br />
hipotalamus<br />
Exclu<strong>de</strong>: hipopituitarism postprocedural<br />
(E89.3)<br />
E23.0 Hipopituitarism<br />
Sindromul eunucoidismului fertil<br />
Hipogonadism hipogonadotrofic<br />
Insuficienta idiopatica a hormonului <strong>de</strong><br />
crestere<br />
Insuficienta izolata <strong>de</strong>:<br />
- gonadotrofina<br />
- hormonul <strong>de</strong> crestere<br />
- hormonul pituitar<br />
Sindromul Kallmann<br />
Sindromul Lorain-Levi<br />
Necroza glan<strong>de</strong>i pituitare (postpartum)<br />
Panhipopituitarism<br />
Pituitar(a):<br />
- casexia<br />
- insuficienta NOS<br />
- insuficienta staturala<br />
Sindromul Sheehan<br />
Boala Simmonds<br />
E23.1 Hipopituitarismul indus medicamentos<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul.<br />
E23.2 Diabetul in<strong>si</strong>pid<br />
Exclu<strong>de</strong>: diabet in<strong>si</strong>pid nefrogen (N25.1)<br />
E23.3 Tulburari hipotalamice, necla<strong>si</strong>ficate<br />
altun<strong>de</strong>va<br />
Exclu<strong>de</strong>: Sindromul Pra<strong>de</strong>r-Willi<br />
(Q87.14)<br />
Sindromul Russell-Silver<br />
(Q87.15)<br />
E23.6 Alte tulburari ale glan<strong>de</strong>i pituitare<br />
Abcesul glan<strong>de</strong>i pituitare<br />
Distrofia adiposo-genitala<br />
E23.7 Tulburari ale glan<strong>de</strong>i pituitare,<br />
nespecificate<br />
E24 Sindromul Cushing<br />
E24.0 Boala Cushing pituitaro-<strong>de</strong>pen<strong>de</strong>nta<br />
Hipersecretia <strong>de</strong> ACTH pituitar<br />
Hiperadrenocorticismul pituitaro<strong>de</strong>pen<strong>de</strong>nt<br />
E24.1 Sindromul Nelson<br />
E24.2 Sindromul Cushing indus medicamentos<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul.<br />
E24.3 Sindromul <strong>de</strong> secretie ectopica <strong>de</strong> ACTH<br />
E24.4 Pseudo-<strong>si</strong>ndromul Cushing indus <strong>de</strong><br />
alcool<br />
E24.8 Alte <strong>si</strong>ndroame Cushing<br />
E24.9 Sindromul Cushing, nespecificat<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E25 Tulburari adrenogenitale<br />
Inclu<strong>de</strong>: <strong>si</strong>ndrom adrenogenital,<br />
masculinizant sau feminizant,<br />
fie dobandit, fie datorit<br />
hiperplaziei suprarenale<br />
consecinta anomaliilor<br />
congenitale a <strong>si</strong>ntezei<br />
hormonilor<br />
la femeie:<br />
- pseudohermafroditism<br />
suprarenal<br />
- pseudopubertate<br />
heterosexuala precoce<br />
la barbat:<br />
- pseudopubertate precoce<br />
isosexuala<br />
- macrogenitosomia precoce<br />
- precocitate sexuala cu<br />
hiperplazia suprarenala<br />
virilizare (la femeie)<br />
E25.0 Tulburari adrenogenitale congenitale<br />
legate <strong>de</strong> un <strong>de</strong>ficit enzimatic<br />
Deficit <strong>de</strong> 21-Hidroxilaza<br />
Hiperplazia suprarenala congenitala<br />
Hiperplazia suprarenala congenitala cu<br />
pier<strong>de</strong>re <strong>de</strong> sare<br />
E25.8 Alte tulburari adrenogenitale<br />
Tulburare adrenogenitala idiopatica<br />
Folo<strong>si</strong>ti un cod <strong>de</strong> cauza externa (Capitolul<br />
XX) pentru a i<strong>de</strong>ntifica medicamentul, daca<br />
este indusa medicamentos.<br />
E25.9 Tulburare adrenogenitala, nespecificata<br />
Sindrom adrenogenital NOS<br />
E26 Hiperaldosteronism<br />
E26.0 Hiperaldosteronism primar<br />
Sindromul Conn<br />
Aldosteronism primar datorit hiperplaziei<br />
suprarenale (bilateral)<br />
E26.1 Hiperaldosteronism secundar<br />
E26.8 Alte hiperaldosteronisme<br />
Sindromul Bartter<br />
E26.9 Hiperaldosteronism, nespecificat<br />
E27 Alte tulburari a<strong>de</strong>nocorticale<br />
E27.0 Alte hiperfunctiuni a<strong>de</strong>nocorticale<br />
Hipersecretia <strong>de</strong> ACTH, nelegata <strong>de</strong> boala<br />
Cushing<br />
Pubertate a<strong>de</strong>nocorticala precoce<br />
Exclu<strong>de</strong>: Sindromul Cushing (E24.-)<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E27.1 Insuficienta a<strong>de</strong>nocorticala primara<br />
Boala Addison<br />
Adrenalita autoimuna<br />
Exclu<strong>de</strong>: amiloidoza (E85.-)<br />
boala Addison tuberculoasa<br />
(A18.7)<br />
<strong>si</strong>ndromul Waterhouse-<br />
Fri<strong>de</strong>richsen (A39.1)<br />
E27.2 Criza addisoniana<br />
Criza adrenala<br />
Criza a<strong>de</strong>nocorticala<br />
E27.3 Insuficienta a<strong>de</strong>nocorticala primara<br />
indusa medicamentos<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul.<br />
E27.4 Insuficienta a<strong>de</strong>nocorticala, alta <strong>si</strong><br />
nespecificata<br />
Adrenal(a):<br />
- hemoragie<br />
- infarct<br />
Insuficienta a<strong>de</strong>nocorticala NOS<br />
Hipoaldosteronism<br />
Exclu<strong>de</strong>: leucodistrofia adrenala<br />
[Addison-Schil<strong>de</strong>r] (E71.3)<br />
<strong>si</strong>ndromul Waterhouse-<br />
Fri<strong>de</strong>richsen (A39.1)<br />
E27.5 Hiperfunctia adreno-medulara<br />
Hiperplazia adreno-medulara<br />
Hipersecretia catecolaminei<br />
E27.8 Alte tulburari specificate ale glan<strong>de</strong>i<br />
adrenale<br />
Anomalia cortizonului legand globulina<br />
E27.9 Tulburari ale glan<strong>de</strong>i adrenale,<br />
nespecificate<br />
E28 Disfunctia ovariana<br />
Exclu<strong>de</strong>: <strong>de</strong>ficienta izolatului in<br />
gonadotrofica (E23.0)<br />
insuficienta ovariana<br />
postprocedurala (E89.4)<br />
E28.0 Hiperestrogenia<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul, daca este indusa<br />
medicamentos.<br />
E28.1 Hiperandrogenia<br />
Hipersecretia <strong>de</strong> androgeni ovarieni<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul, daca este indusa<br />
medicamentos.<br />
E28.2 Sindrom ovarian polichistic<br />
Sindromul ovarian sclerochistic<br />
Sindromul Stein-Leventhal<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 87
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E28.3 Insuficienta ovariana primara<br />
Diminuarea estrogenilor<br />
Menopauza prematura NOS<br />
Sindromul ovarului rezistent<br />
Exclu<strong>de</strong>: tulburari <strong>de</strong> menopauza <strong>si</strong><br />
climacterium feminin (N95.1)<br />
88<br />
disgenezia gonadica pura<br />
(Q99.1)<br />
Sindromul Turner (Q96.-)<br />
E28.8 Alte disfunctii ovariene<br />
Hiperfunctia ovariana NOS<br />
E28.9 Disfunctia ovariana, nespecificata<br />
E29 Disfunctia testiculara<br />
Exclu<strong>de</strong>: <strong>si</strong>ndromul rezistentei la<br />
androgeni (E34.5)<br />
azoospermia sau oligospermia<br />
NOS (N46)<br />
insuficienta izolata <strong>de</strong><br />
gonadotropina (E23.0)<br />
<strong>si</strong>ndromul Klinefelter (Q98.0-<br />
Q98.2, Q98.4)<br />
hipofunctia testiculara<br />
postprocedurala (E89.5)<br />
<strong>si</strong>ndromul testicol feminizat<br />
(E34.5)<br />
E29.0 Hiperfunctia testiculara<br />
Hipersecretia <strong>de</strong> hormoni testiculari<br />
E29.1 Hipofunctia testiculara<br />
Deficit in 5-alfa-reductaza (cu<br />
pseudohermafrodism masculin)<br />
Bio<strong>si</strong>nteza <strong>de</strong>fectuoasa a hormonului<br />
androgen testicular NOS<br />
Hipogonadism testicular NOS<br />
Folo<strong>si</strong>ti un cod aditional <strong>de</strong> cauza externa<br />
(Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul, daca este indusa<br />
medicamentos.<br />
E29.8 Alte disfunctii testiculare<br />
E29.9 Disfunctia testiculara, nespecificata<br />
E30 Tulburarile pubertatii, necla<strong>si</strong>ficate<br />
altun<strong>de</strong>va<br />
E30.0 Pubertate intarziata<br />
Intarzierea <strong>de</strong>zvoltarii constitutionale<br />
Dezvoltare sexuala intarziata<br />
E30.1 Pubertate precoce<br />
Menstruatie precoce<br />
Exclu<strong>de</strong>: <strong>si</strong>ndromul Albright(McCune)(-<br />
Sternberg) (Q78.1)<br />
pubertate precoce centrala<br />
(E22.8)<br />
hiperplazia adrenala<br />
congenitala (E25.0)<br />
pseudopubertatea<br />
heterosexuala la femeie<br />
(E25.-)<br />
pseudopubertatea isosexuala<br />
precoce la barbat (E25.-)<br />
E30.8 Alte tulburari ale pubertatii<br />
Menarha prematura<br />
E30.9 Tulburare <strong>de</strong> pubertate, nespecificata<br />
E31 Disfunctiuni pluriglandulare<br />
Exclu<strong>de</strong>: ataxia teleangiectazica [Louis-<br />
Bar] (G11.3)<br />
distrofia miotonica [Steinert]<br />
(G71.1)<br />
pseudohipoparatiroidism<br />
(E20.1)<br />
E31.0 Insuficienta poliglandulara autoimuna<br />
Sindromul Schmidt<br />
E31.1 Hiperfunctia poliglandulara<br />
Exclu<strong>de</strong>: a<strong>de</strong>nomatoza multipla<br />
endocrina (D44.8)<br />
E31.8 Alte disfunctii poliglandulare<br />
E31.9 Disfunctii poliglandulare, nespecificate<br />
E32 <strong>Boli</strong>le timusului<br />
Exclu<strong>de</strong>: aplazia sau hipoplazia cu<br />
imuno<strong>de</strong>ficienta (D82.1)<br />
miastenia gravis (G70.0)<br />
E32.0 Hiperplazia per<strong>si</strong>stenta a timusului<br />
Hipertrofia timusului<br />
E32.1 Abcesul timusului<br />
E32.8 Alte boli ale timusului<br />
E32.9 Boala timusului, nespecificata<br />
E34 Alte tulburari <strong>endocrine</strong><br />
Exclu<strong>de</strong>: pseudohipoparatiroidism<br />
(E20.1)<br />
E34.0 Sindrom carcinoid<br />
Nota: Poate fi folo<strong>si</strong>t ca un cod aditional,<br />
daca se doreste a se i<strong>de</strong>ntifica<br />
activitatea functionala asociata<br />
cu o tumora carcinoida<br />
E34.1 Alte hipersecretii <strong>de</strong> hormoni intestinali<br />
E34.2 Secretia hormonala ectopica,<br />
necla<strong>si</strong>ficata altun<strong>de</strong>va<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E34.3 Insuficienta staturala, necla<strong>si</strong>ficata<br />
altun<strong>de</strong>va<br />
Insuficienta staturala:<br />
- constitutionala<br />
- tip Laron<br />
- NOS<br />
- p<strong>si</strong>hosociala<br />
Exclu<strong>de</strong>: progeria (E34.8)<br />
<strong>si</strong>ndromul Russell-Silver<br />
(Q87.15)<br />
insuficienta staturala:<br />
- achondroplazica (Q77.4)<br />
- hipochondroplazica (Q77.4)<br />
- in <strong>si</strong>ndromul <strong>de</strong> malformatie<br />
congenitala (Q78.1)<br />
- in <strong>si</strong>ndromul dismorfic<br />
specific - codificati <strong>si</strong>ndromul<br />
(vezi In<strong>de</strong>xul alfabetic)<br />
- nutritionala (E45)<br />
- pituitara (E23.0)<br />
- renala (N25.0)<br />
- imuno<strong>de</strong>ficienta cu<br />
micromelie (D82.2)<br />
E34.4 Statura inalta constitutionala<br />
Gigantism constitutional<br />
E34.5 Sindromul <strong>de</strong> rezistenta la androgeni<br />
Pseudohermafroditism masculin cu<br />
rezistenta la androgeni<br />
Tulburarea receptorilor hormonali<br />
periferici<br />
Sindromul Reifenstein<br />
Feminizare testiculara (<strong>si</strong>ndrom)<br />
E34.8 Alte tulburari hormonale specificate<br />
Disfunctia glan<strong>de</strong>i pineale<br />
Progeria<br />
E34.9 Tulburare endocrina, nespecificata<br />
Tulburare:<br />
- endocrina NOS<br />
- hormonala NOS<br />
E35* Tulburari ale glan<strong>de</strong>lor <strong>endocrine</strong> in<br />
boli cla<strong>si</strong>ficate altun<strong>de</strong>va<br />
E35.0* Tulburarile glan<strong>de</strong>i tiroi<strong>de</strong> in boli<br />
cla<strong>si</strong>ficate altun<strong>de</strong>va<br />
Tuberculoza glan<strong>de</strong>i tiroi<strong>de</strong> (A18.8†)<br />
E35.1* Tulburarile glan<strong>de</strong>i adrenale in boli<br />
cla<strong>si</strong>ficate altun<strong>de</strong>va<br />
Siondromul Waterhouse-Fri<strong>de</strong>richsen<br />
(meningococic) (A39.1†)<br />
E35.8* Tulburarile altor glan<strong>de</strong> <strong>endocrine</strong> in boli<br />
cla<strong>si</strong>ficate altun<strong>de</strong>va<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
Malnutritia (E40-E46)<br />
Nota: Gradul <strong>de</strong> mal<strong>nutritie</strong> se masoara <strong>de</strong><br />
obicei in termenii greutatii, exprimat<br />
in <strong>de</strong>viatii standard <strong>de</strong> la media<br />
populatiei <strong>de</strong> referinta relevante.<br />
Indicatorul <strong>de</strong> mal<strong>nutritie</strong> apare <strong>de</strong><br />
obicei atunci cand una sau mai multe<br />
din masuratorile anterioare sunt<br />
disponibile, lipsa castigului greutatii la<br />
copii sau evi<strong>de</strong>nta pier<strong>de</strong>rii greutatii la<br />
copii sau adulti. Cand numai o<br />
masuratoare este disponibila,<br />
diagnosticul se bazeaza pe<br />
probabilitati <strong>si</strong> nu este <strong>de</strong>finitiv fara<br />
alte teste clinice sau <strong>de</strong> laborator. In<br />
circumstante exceptionale in care nu<br />
este disponibila nici o masuratoare a<br />
greutatii, diagnosticul se va baza pe<br />
investigatiile clinice.<br />
Daca o greutate observata este sub<br />
valoarea medie a populatiei <strong>de</strong><br />
referinta, exista o probabilitate mare<br />
<strong>de</strong> mal<strong>nutritie</strong> severa atunci cand<br />
valoarea observata este <strong>si</strong>tuata cu 3<br />
sau mai multe <strong>de</strong>viatii standard sub<br />
valoarea medie a populatiei <strong>de</strong><br />
referinta; o mare probabilitate <strong>de</strong><br />
mal<strong>nutritie</strong> mo<strong>de</strong>rata pentru o valoare<br />
observata se <strong>si</strong>tueaza intre 2 <strong>si</strong> mai<br />
putin <strong>de</strong> 3 <strong>de</strong>viatii standard sub<br />
aceasta medie; <strong>si</strong> o probabilitate<br />
mare <strong>de</strong> mal<strong>nutritie</strong> usoara pentru o<br />
valoare observata, se localizeaza intre<br />
1 <strong>si</strong> mai putin <strong>de</strong> 2 <strong>de</strong>viatii standard<br />
sub aceasta medie.<br />
Exclu<strong>de</strong>: malabsorbtia intestinala (K90.-)<br />
anemii nutritionale (D50-D53)<br />
sechele ale mal<strong>nutritie</strong>i proteinoenergetice<br />
(E64.0)<br />
infometare (T73.0)<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 89<br />
E40<br />
E41<br />
E42<br />
Kwashiorkor<br />
Malnutritia severa cu e<strong>de</strong>m nutritional cu<br />
<strong>de</strong>pigmentarea pielii <strong>si</strong> a parului<br />
Exclu<strong>de</strong>: kwashiorkor <strong>de</strong> marasm (E42)<br />
Marasm nutritional<br />
Mal<strong>nutritie</strong> grava cu marasm<br />
Exclu<strong>de</strong>: kwashiorkor <strong>de</strong> marasm (E42)<br />
Kwashiorkor <strong>de</strong> marasm<br />
Mal<strong>nutritie</strong> proteino-energetica grava [ca la<br />
E43]:<br />
- forma intermediara<br />
- cu semne atat <strong>de</strong> kwashiorkor, cat <strong>si</strong> <strong>de</strong><br />
marasm
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E43<br />
90<br />
Malnutritia proteino-energetica<br />
grava, nespecificata<br />
Pier<strong>de</strong>rea severa in greutate [emaciere] la<br />
copii sau adulti, sau lipsa <strong>de</strong> castig pon<strong>de</strong>ral<br />
la copil, ajungand la o greutate observata<br />
care este cu cel putin 3 <strong>de</strong>viatii standard sub<br />
valoarea medie pentru populatia <strong>de</strong> referinta<br />
(sau la o pier<strong>de</strong>re <strong>si</strong>milara exprimata dupa<br />
alte meto<strong>de</strong> statistice). Cand nu dispunem<br />
<strong>de</strong>cat <strong>de</strong> o <strong>si</strong>ngura masuratoare, exista o<br />
probabilitate puternica <strong>de</strong> emaciere grava<br />
atunci cand greutatea este cu 3 sau mai<br />
multe <strong>de</strong>viatii standard sub media populatiei<br />
<strong>de</strong> referinta.<br />
E<strong>de</strong>m <strong>de</strong> infometare<br />
E44 Malnutritia proteino-energetica<br />
usoara sau mo<strong>de</strong>rata<br />
E44.0 Malnutritia proteino-energetica mo<strong>de</strong>rata<br />
Pier<strong>de</strong>rea greutatii la copii sau adulti sau<br />
lipsa castigului in greutate la copii ducand la<br />
o greutate observata care este <strong>de</strong> 2 sau mai<br />
mult dar ne<strong>de</strong>pa<strong>si</strong>nd 3 <strong>de</strong>viatii standard sub<br />
valoarea medie pentru populatia <strong>de</strong> referinta<br />
(sau o pier<strong>de</strong>re <strong>si</strong>milara exprimata prin alte<br />
abordari statistice). Atunci cand numai o<br />
masuratoare este disponibila, exista o<br />
probabilitate mare <strong>de</strong> mal<strong>nutritie</strong> proteinoenergetica<br />
mo<strong>de</strong>rata cand greutatea<br />
observata este <strong>de</strong> 2 sau mai mult, dar<br />
ne<strong>de</strong>pa<strong>si</strong>nd 3 <strong>de</strong>viatii standard sub media<br />
populatiei <strong>de</strong> referinta.<br />
E44.1 Malnutritia proteino-energetica usoara<br />
Pier<strong>de</strong>rea greutatii la copii sau adulti sau<br />
lipsa castigului in greutate la copii ducand la<br />
o greutate observata care este <strong>de</strong> 1sau mai<br />
mult dar ne<strong>de</strong>pa<strong>si</strong>nd 2 <strong>de</strong>viatii standard sub<br />
valoarea medie pentru populatia <strong>de</strong> referinta<br />
(sau o pier<strong>de</strong>re <strong>si</strong>milara exprimata prin alte<br />
abordari statistice). Atunci cand numai o<br />
masuratoare este disponibila, exista o<br />
probabilitate mare <strong>de</strong> mal<strong>nutritie</strong> proteinoenergetica<br />
mo<strong>de</strong>rata cand greutatea<br />
observata este <strong>de</strong> 1 sau mai mult, dar<br />
ne<strong>de</strong>pa<strong>si</strong>nd 2 <strong>de</strong>viatii standard sub media<br />
populatiei <strong>de</strong> referinta.<br />
E45<br />
E46<br />
Intarzierea <strong>de</strong> <strong>de</strong>zvoltare datorita<br />
mal<strong>nutritie</strong>i proteino-energetice<br />
Nutritionala:<br />
- insuficienta staturala<br />
- intreruperea cresterii<br />
Retardare p<strong>si</strong>hica datorita mal<strong>nutritie</strong>i<br />
Malnutritia proteino-energetica<br />
nespecificata<br />
Malnutritia NOS<br />
Dezechilibru proteino-energetic NOS<br />
Alte carente nutritionale (E50-E64)<br />
Exclu<strong>de</strong>: anemia nutritionala (D50-D53)<br />
E50 Avitaminoza A<br />
Exclu<strong>de</strong>: sechele ale avitaminozei A<br />
(E64.1)<br />
E50.0 Avitaminoza A cu xeroza conjunctivei<br />
E50.1 Avitaminoza A cu pete Bitot <strong>si</strong> xeroza<br />
conjunctivei<br />
Pete Bitot la copilul mic<br />
E50.2 Avitaminoza A cu xeroza corneei<br />
E50.3 Avitaminoza A cu ulceratia corneei <strong>si</strong><br />
xeroza<br />
E50.4 Avitaminoza A cu cheratomalacie<br />
E50.5 Avitaminoza A cu hemeralopie vesperala<br />
E50.6 Avitaminoza A cu cicatrice xeroftalmica a<br />
corneei<br />
E50.7 Alte manifestari oculare ale avitaminozei<br />
A<br />
Xeroftalmia NOS<br />
E50.8 Alte manifestari ale avitaminozei A<br />
Keratoza foliculara datorita avitaminozei A<br />
† (L86*)<br />
Xero<strong>de</strong>rmia datorita avitaminozei A† (L86*)<br />
E50.9 Avitaminoza A, nespecificata<br />
Hipovitaminoza A NOS<br />
E51 Carenta in tiamina<br />
Exclu<strong>de</strong>: sechele ale carentei <strong>de</strong> tiamina<br />
(E64.8)<br />
E51.1 Beriberi<br />
Beriberi:<br />
- uscat<br />
- umed† (I98.8*)<br />
E51.2 Encefalopatia Wernicke<br />
E51.8 Alte manifestari ale carentei in tiamina<br />
E51.9 Carenta in tiamina, nespecificata<br />
E52<br />
Carenta in acid nicotinic (pelagra)<br />
Carenta in:<br />
- acid nicotinic (-triptofan)<br />
- nicotinami<strong>de</strong><br />
Pelagra (alcoolica)<br />
Exclu<strong>de</strong>: sechele ale carentei in acid<br />
nicotinic (E64.8)<br />
E53 Alte avitaminoze din grupa B<br />
Exclu<strong>de</strong>: sechele ale avitaminozei B<br />
(E64.8)<br />
E53.0 Carenta in riboflavine<br />
Ariboflavinoza<br />
anemia prin carenta <strong>de</strong> vitamina<br />
B12 (D51.-)<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E53.1 Carenta in piridoxina<br />
Avitaminoza B6<br />
Exclu<strong>de</strong>: anemia <strong>si</strong><strong>de</strong>roblastica<br />
reactionand la piridoxina<br />
(D64.3)<br />
E53.8 Carenta <strong>de</strong> alte vitamine din grupa B<br />
Carenta <strong>de</strong>:<br />
- biotina<br />
- cianocobalmina<br />
- folat<br />
- acid folic<br />
- acid pantotenic<br />
- vitamina B12<br />
E53.9 Avitaminoze din grupa B, nespecificate<br />
E54<br />
Carenta <strong>de</strong> acid ascorbic<br />
Carenta <strong>de</strong> vitamina C<br />
Scorbut<br />
Exclu<strong>de</strong>: anemia in scorbut (D53.2)<br />
sechele ale avitaminozei C<br />
(E64.2)<br />
E55 Carenta <strong>de</strong> vitamina D<br />
Exclu<strong>de</strong>: osteomalacia adultului (M83.-)<br />
E55.0 Rahitism evolutiv<br />
Osteomalacia:<br />
- infantila<br />
- juvenila<br />
Exclu<strong>de</strong>: rahitism:<br />
osteoporoza (M80-M81)<br />
sechele ale rahitismului (E64.3)<br />
- celiac (K90.0)<br />
- Crohn (K50.-)<br />
- inactiv (E64.3)<br />
- renal (N25.0)<br />
- rezistent la vitamina D<br />
(E83.3)<br />
E55.9 Carenta <strong>de</strong> vitamina D, nespecificata<br />
Avitaminoza D<br />
E56 Alte avitaminoze<br />
Exclu<strong>de</strong>: sechele ale altor avitaminoze<br />
(E64.8)<br />
E56.0 Carenta <strong>de</strong> vitamina E<br />
E56.1 Carenta <strong>de</strong> vitamina K<br />
Exclu<strong>de</strong>: <strong>de</strong>ficienta factorului <strong>de</strong><br />
coagulare datorita carentei <strong>de</strong><br />
vitamina K (D68.4)<br />
<strong>de</strong>ficienta <strong>de</strong> vitamina K a nounascutului<br />
(P53)<br />
E56.8 Carenta <strong>de</strong> alte vitamine<br />
E56.9 Avitaminoza, nespecificata<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 91<br />
E58<br />
E59<br />
E60<br />
Carenta alimentara <strong>de</strong> calciu<br />
Exclu<strong>de</strong>: tulburari in <strong>metabolism</strong>ul<br />
calciului (E83.5)<br />
sechelele carentei <strong>de</strong> calciu<br />
(E64.8)<br />
Carenta alimentara <strong>de</strong> seleniu<br />
Boala Keshan<br />
Exclu<strong>de</strong>: sechele ale carentei <strong>de</strong> seleniu<br />
(E64.8)<br />
Carenta <strong>de</strong> zinc<br />
E61 Carenta <strong>de</strong> alte elemente<br />
nutritionale<br />
Folo<strong>si</strong>ti un cod aditional pentru cauza<br />
externa (Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul, daca este indusa<br />
medicamentos.<br />
Exclu<strong>de</strong>: tulburari ale <strong>metabolism</strong>ului<br />
sarurilor minerale (E83.-)<br />
tulburari tiroidiene legate <strong>de</strong><br />
carenta <strong>de</strong> iod (E00-E02)<br />
sechele ale mal<strong>nutritie</strong>i <strong>si</strong> altor<br />
carente nutritionale (E64.-)<br />
E61.0 Carenta <strong>de</strong> cupru<br />
E61.1 Carenta <strong>de</strong> fier<br />
Exclu<strong>de</strong>: anemia prin carenta <strong>de</strong> fier<br />
(D50.-)<br />
E61.2 Carenta <strong>de</strong> magneziu<br />
E61.3 Carenta <strong>de</strong> mangan<br />
E61.4 Carenta <strong>de</strong> crom<br />
E61.5 Carenta <strong>de</strong> molib<strong>de</strong>n<br />
E61.6 Carenta <strong>de</strong> vanadiu<br />
E61.7 Carenta mai multor elemente nutritionale<br />
E61.8 Carenta <strong>de</strong> alte elemente nutritionale<br />
specificate<br />
E61.9 Carenta <strong>de</strong> element nutritional,<br />
nespecificata<br />
E63 Alte carente nutritionale<br />
Exclu<strong>de</strong>: <strong>de</strong>shidratare (E86)<br />
insuficienta <strong>de</strong> <strong>de</strong>zvoltare<br />
(R62.8)<br />
tulburari nutritionale la nounascuta<br />
(P92.-)<br />
sechele ale mal<strong>nutritie</strong>i <strong>si</strong> alte<br />
carente nutritionale (E64.-)<br />
E63.0 Carenta <strong>de</strong> acizi gra<strong>si</strong> esentiali [EFA]<br />
E63.1 Dezechilibru constituentilor alimentari<br />
ingerati<br />
E63.8 Alte carente nutritionale specificate<br />
E63.9 Carenta nutritionala, nespecificata<br />
Cardiomiopatie nutritionala NOS† (I43.2*)
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E64<br />
<br />
0008<br />
92<br />
Sechele ale mal<strong>nutritie</strong>i <strong>si</strong> alte<br />
carente nutritionale<br />
E64.0 Sechele ale mal<strong>nutritie</strong>i proteinoenergetica<br />
Exclu<strong>de</strong>: intarziere <strong>de</strong> <strong>de</strong>zvoltare ca<br />
urmare a unei malnutritii<br />
proteino-energetice (E45)<br />
E64.1 Sechele ale avitaminozei A<br />
E64.2 Sechele ale avitaminozei C<br />
E64.3 Sechele <strong>de</strong> rahitism<br />
E64.8 Sechele ale altor carente nutritionale<br />
E64.9 Sechele <strong>de</strong> carente nutritionale<br />
nespecificate<br />
Obezitatea <strong>si</strong> alte tulburari prin<br />
exces <strong>de</strong> aport (E65-E68)<br />
E65<br />
Adipozitate localizata<br />
Sort abdominal sau proeminent<br />
Burelet adipos<br />
E66 Obezitate<br />
Exclu<strong>de</strong>: distrofia adiposogenitala (E23.6)<br />
lipomatoza:<br />
- dureroasa [Dercum] (E88.2)<br />
- NOS (E88.2)<br />
<strong>si</strong>ndromul Pra<strong>de</strong>r-Willi (Q87.14)<br />
E66.0 Obezitate datorita unui exces caloric<br />
E66.1 Obezitate indusa medicamentos<br />
Folo<strong>si</strong>ti un cod aditional pentru cauza<br />
externa (Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul<br />
E66.2 Obezitate extrema cu hipoventilatie<br />
alveolara<br />
Sindromul Pickwickian<br />
E66.8 Alte obezitati<br />
Obezitate morbida<br />
E66.9 Obezitate, nespecificata<br />
Obezitate <strong>si</strong>mpla NOS<br />
E67 Alte excese <strong>de</strong> aport<br />
Exclu<strong>de</strong>: hiperalimentatia NOS (N63.2)<br />
sechelele hiperalimentatiei (E68)<br />
E67.0 Hipervitaminoza A<br />
E67.1 Hipercarotenemia<br />
E67.2 Sindrom <strong>de</strong> hipervitaminoza B6<br />
E67.3 Hipervitaminoza D<br />
E67.8 Alte excese <strong>de</strong> aport specificate<br />
E68<br />
<br />
0008<br />
Sechele ale excesului <strong>de</strong> aport<br />
Tulburari <strong>de</strong> <strong>metabolism</strong> (E70-E89)<br />
Exclu<strong>de</strong>: <strong>de</strong>ficit <strong>de</strong> 5-alfa-reductaza (E29.1)<br />
<strong>si</strong>ndromul rezistentei la androgeni<br />
(E34.5)<br />
hiperplazia suprarenala congenitala<br />
(E25.0)<br />
<strong>si</strong>ndromul Ehlers-Danlos (Q79.6)<br />
anemia hemolitica datorita unor<br />
tulburari enzimatice (D55.-)<br />
<strong>si</strong>ndromul Marfan (Q87.4)<br />
E70 Tulburari <strong>de</strong> <strong>metabolism</strong> ale<br />
aminoacizilor aromatici<br />
E70.0 Fenilcetonuria cla<strong>si</strong>ca<br />
E70.1 Alte hiperfenilalanilemii<br />
E70.2 Tulburari in <strong>metabolism</strong>ul tirozinei<br />
Alcaptonuria<br />
Hipertiro<strong>si</strong>nemia<br />
Ocronoza<br />
Tiro<strong>si</strong>nemia<br />
Tiro<strong>si</strong>noza<br />
E70.3 Albinism<br />
Albinism:<br />
- ocular<br />
- cutaneo-ocular<br />
Sindromul:<br />
- Chediak(-Steinbrinck)-Higashi<br />
- Cross<br />
- Hermansky-Pudlak<br />
E70.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
aminoacizilor aromatici<br />
Tulburari <strong>de</strong>:<br />
- <strong>metabolism</strong>ul histidinei<br />
- <strong>metabolism</strong>ul triptofanului<br />
E70.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al aminoacizilori<br />
aromatici, nespecificate<br />
E71 Tulburari <strong>de</strong> <strong>metabolism</strong> ale<br />
aminoacizilor cu lant ramificat <strong>si</strong> ale<br />
<strong>metabolism</strong>ului acizilor gra<strong>si</strong><br />
E71.0 Boala urinei cu miros <strong>de</strong> <strong>si</strong>rop <strong>de</strong> artar<br />
E71.1 Alte tulburari <strong>de</strong> <strong>metabolism</strong> ale<br />
aminoacizilor cu lant ramificat<br />
Hiperleucine-izoleucinemia<br />
Hipervalinemia<br />
Aci<strong>de</strong>mia izovalerica<br />
Aci<strong>de</strong>mia metilmalonica<br />
Aci<strong>de</strong>mia propionica<br />
E71.2 Tulburari <strong>de</strong> <strong>metabolism</strong> al aminoacizilor<br />
cu lant ramificat, nespecificate<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E71.3 Tulburari <strong>de</strong> <strong>metabolism</strong> al acizilor gra<strong>si</strong><br />
A<strong>de</strong>noleucodistrofia [Addison-Schil<strong>de</strong>r]<br />
Insuficienta <strong>de</strong> carnitine palmitiltransferaza<br />
musculara<br />
Exclu<strong>de</strong>: boala Refsum (G60.1)<br />
boala Schil<strong>de</strong>r (G37.0)<br />
<strong>si</strong>ndromul Zellweger (Q87.83)<br />
E72 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
aminoacizilor<br />
Exclu<strong>de</strong>: rezultate anormale fara boala<br />
evi<strong>de</strong>nta (R70-R89)<br />
tulburari <strong>de</strong>:<br />
- <strong>metabolism</strong>ul acizilor<br />
aromatici (E70.-)<br />
- <strong>metabolism</strong>ul aminoacizilor<br />
cu lant ramificat ((E71.0-<br />
E71.1)<br />
- <strong>metabolism</strong>ul acizilor gra<strong>si</strong><br />
(E71.3)<br />
- <strong>metabolism</strong>ul purinelor <strong>si</strong><br />
pirimidinelor (E79.-)<br />
guta (M10.-)<br />
E72.0 Tulburari in transportul aminoacizilor<br />
Cistinoza<br />
Cistinuria<br />
Sindromul Fanconi(-<strong>de</strong> Toni)(-Debré)<br />
Boala Hartnup<br />
Sindromul Lowe<br />
Exclu<strong>de</strong>: tulburari ale <strong>metabolism</strong>ului<br />
triptofanului (E70.8)<br />
E72.1 Tulburari <strong>de</strong> <strong>metabolism</strong> al aminoacizilor<br />
sulfurati<br />
Cistationinuria<br />
Homocistinuria<br />
Metioninemia<br />
Deficit in sulfit oxidaza<br />
Exclu<strong>de</strong>: carenta <strong>de</strong> transcobalamin II<br />
(D51.2)<br />
E72.2 Tulburari <strong>de</strong> <strong>metabolism</strong> al ciclului ureei<br />
Arginemia<br />
Aciduria arginosuccinica<br />
Citrulinemia<br />
Hiperamonemia<br />
Exclu<strong>de</strong>: tulburari ale <strong>metabolism</strong>ului<br />
ornitinei (E72.4)<br />
E72.3 Tulburari <strong>de</strong> <strong>metabolism</strong> al lizinei <strong>si</strong><br />
hidroxilizinei<br />
Aciduria glutarica<br />
Hidroxilizinemia<br />
Hiperlizinemia<br />
E72.4 Tulburari <strong>de</strong> <strong>metabolism</strong> al ornitinei<br />
Ornitinemia (tip I, II)<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E72.5 Tulburari <strong>de</strong> <strong>metabolism</strong> al glicinei<br />
Hiperhidroxiprolinemia<br />
Hiperprolinemia (tip I, II)<br />
Hiperglicinemia noncetozica<br />
Sarco<strong>si</strong>nemia<br />
E72.8 Alte tulburari specificate <strong>de</strong> <strong>metabolism</strong><br />
al aminoacizilor<br />
Tulburari <strong>de</strong>:<br />
- <strong>metabolism</strong>ul aminoacidului ß<br />
- ciclului gammaglutamil<br />
E72.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
aminoacizilori, nespecificate<br />
E73 Intoleranta la lactoza<br />
E73.0 Deficit congenital in lactaza<br />
E73.1 Deficit secundar in lactaza<br />
E73.8 Alte intolerante la lactoza<br />
E73.9 Intoleranta la lactoza, nespecificata<br />
E74 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
carbohidratilor<br />
Exclu<strong>de</strong>: diabet mellitus (E10.E14)<br />
hipoglicemia NOS (E16.2)<br />
hipersecretia <strong>de</strong> glucagon<br />
(E16.3)<br />
mucopolizaharidoza (E76.0-<br />
E76.3)<br />
E74.0 Boala <strong>de</strong>pozitarii glicogenului<br />
Glicogenoza cardiaca<br />
Boala:<br />
- An<strong>de</strong>rsen<br />
- Cori<br />
- Forbes<br />
- Hers<br />
- McArdle<br />
- Pompe<br />
- Tauri<br />
- von Gierke<br />
Deficit in fosforilaza hepatica<br />
E74.1 Tulburari <strong>de</strong> <strong>metabolism</strong> al fructozei<br />
Fructozuria esentiala<br />
Deficit in fructoza-1,6-disfosfataza<br />
Intoleranta ereditara la fructoza<br />
E74.2 Tulburari <strong>de</strong> <strong>metabolism</strong> al galactozei<br />
Deficit <strong>de</strong> galactochinaza<br />
Galactosemia<br />
E74.3 Alte tulburari <strong>de</strong> absorbtie intestinala a<br />
carbohidratilor<br />
Malabsorbtia glucozo-galactoza<br />
Deficit <strong>de</strong> sucraza<br />
Exclu<strong>de</strong>: intoleranta la lactoza (E73.-)<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 93
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E74.4 Tulburari <strong>de</strong> <strong>metabolism</strong> al piruvatului <strong>si</strong><br />
al gluconeogenezei<br />
Deficit <strong>de</strong>:<br />
- carboxikinaza fosfoenolpiruvat<br />
- piruvat:<br />
- carboxilaza<br />
- <strong>de</strong>hidrogenaza<br />
Exclu<strong>de</strong>: cu anemie (D55.-)<br />
E74.8 Alte tulburari specificate <strong>de</strong> <strong>metabolism</strong><br />
al carbohidratilor<br />
Pentosuria esentiala<br />
Oxaloza<br />
Oxaluria<br />
Glicozuria renala<br />
E74.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
carbohidratilor, nespecificate<br />
E75 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
sfingolipi<strong>de</strong>lor <strong>si</strong> al altor lipi<strong>de</strong> <strong>de</strong><br />
rezerva<br />
Exclu<strong>de</strong>: mucolipidoza, tipuri I-III<br />
(E77.0-E77.1)<br />
94<br />
boala Refsum (G60.1)<br />
E75.0 Ganglio<strong>si</strong>doza GM2<br />
Boala:<br />
- Sandhoff<br />
- Tay-Sachs<br />
Ganglio<strong>si</strong>doza GM2:<br />
- la adult<br />
- juvenila<br />
- NOS<br />
E75.1 Alte ganglio<strong>si</strong>doze<br />
Ganglio<strong>si</strong>doze:<br />
- GM1<br />
- GM3<br />
- NOS<br />
Mucolipidoza IV<br />
E75.2 Alte sfingolipidoze<br />
Boala:<br />
- Fabry(-An<strong>de</strong>rson)<br />
- Gaucher<br />
- Krabbe<br />
- Niemann-Pick<br />
Sindromul Farber<br />
Leucodistrofia metacromatica<br />
Deficit <strong>de</strong> sulfataza<br />
Exclu<strong>de</strong>: adrenoleucodistrofia [Addison-<br />
Schil<strong>de</strong>r] (E71.3)<br />
E75.3 Sfincolipidoza, nespecificata<br />
E75.4 Lipofuscinoza cu ceroi<strong>de</strong> neuronale<br />
Boala:<br />
- Batten<br />
- Bielschowsky-Jansky<br />
- Kufs<br />
- Spielmeyer-Vogt<br />
E75.5 Alte tulburari ale lipi<strong>de</strong>lor <strong>de</strong> rezerva<br />
Colesteroza cerebrotendinoasa [van<br />
Bogaert-Scherer-Epstein]<br />
Boala Wolman<br />
E75.6 Tulburari ale lipi<strong>de</strong>lor <strong>de</strong> rezerva,<br />
nespecificate<br />
E76 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
glicosaminoglicani<br />
E76.0 Mucopolizaharidoze, tip I<br />
Sindrom:<br />
- Hurler<br />
- Hurler-Scheie<br />
- Scheie<br />
E76.1 Mucopolizaharidoza, tip II<br />
Sindromul Hunter<br />
E76.2 Alte mucopolizaharidoze<br />
Mucopolizaharidoza, tip III, IV, VI, VII<br />
Carenta <strong>de</strong> ß-glucoronidasa<br />
Sindrom:<br />
- Maroteaux-Lamy (usor)(sever)<br />
- Morquio(-asemanator)(cla<strong>si</strong>c)<br />
- Sanfilippo (tip B)(tip C)(tipD)<br />
E76.3 Mucopolizaharidoza, nespecificata<br />
E76.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
glicosaminoglicani<br />
E76.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
glicosaminoglicani, nespecificate<br />
E77 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
glicoproteinelor<br />
E77.0 Deficit <strong>de</strong> transformare posttraductionala<br />
a enzimelor lisosomale<br />
Mucolipidoza II [boala celulelor I]<br />
Mucolipidoza III [polidistrofia pseudo-<br />
Hurler]<br />
E77.1 Deficit <strong>de</strong> <strong>de</strong>gradare a glicoproteinelor<br />
Aspartilglucozaminurie<br />
Fucozidoza<br />
Manozidoza<br />
Sialidoza [mucolipidoza I]<br />
E77.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
glicoproteinelor<br />
E77.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
glicoproteinelor, nespecificate<br />
E78 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
lipoproteinelor <strong>si</strong> alte lipi<strong>de</strong>mii<br />
Exclu<strong>de</strong>: sfingolipidoza (E75.0-E75.3)<br />
E78.0 Hipercolesterolemie esentiala<br />
Hipercolesterolemie familiala<br />
Hiperlipoproteinemia Fredrickson, tip IIa<br />
Hiperbetalipoproteinemia<br />
Hiperlipi<strong>de</strong>mia, grupa A<br />
Hiperlipoproteinemia cu lipoproteine <strong>de</strong><br />
<strong>de</strong>n<strong>si</strong>tate joasa [LDL]<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E78.1 Hipergliceri<strong>de</strong>mia esentiala<br />
Hipergliceri<strong>de</strong>mia endogena<br />
Hiperlipoproteinemia Fredrickson, tip IV<br />
Hiperlipi<strong>de</strong>mia, grupa B<br />
Hiperbetalipoproteinemia<br />
Hiperlipoproteinemia cu lipoproteine <strong>de</strong><br />
<strong>de</strong>n<strong>si</strong>tate foarte joasa [VLDL]<br />
E78.2 Hiperlipi<strong>de</strong>mie mixta<br />
Betalipoproteinemia larga sau flotanta<br />
Hiperlipoproteinemia Fredrickson, tip IIb<br />
sau III<br />
Hiperbetalipoproteinemia cu<br />
prebetalipoproteinemie<br />
Hipercolesterolemia cu hipergliceri<strong>de</strong>mie<br />
endogena<br />
Hiperlipi<strong>de</strong>mia, grupa C<br />
Xantom tubero-eruptiv<br />
Xantom tuberos<br />
Exclu<strong>de</strong>: colesteroza cerebrotendinoasa<br />
[van Bogaert-Scherer-<br />
Epstein] (E75.5)<br />
E78.3 Hiperchilomicroanemie<br />
Hiperlipoproteinemia Fredrickson, tip I sau<br />
V<br />
Hiperlipi<strong>de</strong>mia, grupa D<br />
Hipergliceri<strong>de</strong>mia mixta<br />
E78.4 Alte hiperlipi<strong>de</strong>mii<br />
Hiperlipi<strong>de</strong>mia familiala combinata<br />
E78.5 Hiperlipi<strong>de</strong>mia, nespecificata<br />
E78.6 Deficit in lipoproteine<br />
Abetalipoproteinemia<br />
Deficienta <strong>de</strong> lipoproteine <strong>de</strong> <strong>de</strong>n<strong>si</strong>tate<br />
inalta<br />
Hipoalfalipoproteinemia<br />
Hipobetalipoproteinemia (familiala)<br />
Deficienta <strong>de</strong> lecitin colesterol<br />
aciltransferaza<br />
Boala Tangier<br />
E78.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
lipoproteinelor<br />
E78.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
lipoproteinelor, nespecificate<br />
E79 Tulburari <strong>de</strong> <strong>metabolism</strong> ale<br />
purinelor <strong>si</strong> pirimidinei<br />
Exclu<strong>de</strong>: litiaza renala (N20.0)<br />
tulburari imunitare combinate<br />
(D81.-)<br />
guta (M10.-)<br />
anemia cu orotacidurie (D53.0)<br />
xero<strong>de</strong>rma pigmentosum<br />
(Q82.1)<br />
E79.0 Hiperuricemia fara semne <strong>de</strong> artrita<br />
inflamatorie sau <strong>de</strong> boala tofacee<br />
Hiperuricemia a<strong>si</strong>mptomatica<br />
E79.1 Sindromul Lesch-Nyhan<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E79.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al purinelor<br />
<strong>si</strong> pirimidinei<br />
Xantinuria ereditara<br />
E79.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al purinelor <strong>si</strong><br />
pirimidinei, nespecificate<br />
E80 Tulburari <strong>de</strong> <strong>metabolism</strong> al porfirinei<br />
<strong>si</strong> bilirubinei<br />
Inclu<strong>de</strong>: <strong>de</strong>ficit in cantalaza <strong>si</strong> peroxidaza<br />
E80.0 Porfirie eritropoietica ereditara<br />
Porfirie eritropoietica congenitala<br />
Protoporfiria eritropoietica<br />
E80.1 Porfirie cutanata tardiva<br />
E80.2 Alte porfirii<br />
Coproporfiria ereditara<br />
Porfiria:<br />
- acuta periodica (hepatica)<br />
- NOS<br />
Folo<strong>si</strong>ti un cod aditional pentru cauza<br />
externa (Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
cauza<br />
E80.3 Deficit in catalaza <strong>si</strong> peroxidaza<br />
Acatalazia [Takahara]<br />
E80.4 Sindromul Gilbert<br />
E80.5 Sindromul Crigler-Najjar<br />
E80.6 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al bilirubinei<br />
Sindromul Dubin-Johnson<br />
Sindromul Rotor<br />
E80.7 Tulburari <strong>de</strong> <strong>metabolism</strong> al bilirubinei,<br />
nespecificate<br />
E83 Tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
mineralelor<br />
Exclu<strong>de</strong>: carenta alimentara <strong>de</strong> minerale<br />
(E58-E61)<br />
tulburari ale glan<strong>de</strong>i paratiroi<strong>de</strong><br />
(E20-E21)<br />
carenta <strong>de</strong> vitamina D (E55.-)<br />
E83.0 Tulburari <strong>de</strong> <strong>metabolism</strong> al cuprului<br />
Boala Menkes (par cret)(par otelit)<br />
Boala Wilson<br />
E83.1 Tulburari <strong>de</strong> <strong>metabolism</strong> al fierului<br />
Hemocromatoza<br />
Exclu<strong>de</strong>: anemia:<br />
- carenta <strong>de</strong> fier (D50.-)<br />
- <strong>si</strong><strong>de</strong>roblastica (D64.0-D64.3)<br />
E83.2 Tulburari <strong>de</strong> <strong>metabolism</strong> al zincului<br />
Acro<strong>de</strong>rmatita enteropatica<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 95
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E83.3 Tulburari <strong>de</strong> <strong>metabolism</strong> al fosforului<br />
Deficit in fosfataza acida<br />
Hipopotasemia familiala<br />
Hipofosfatazia<br />
Rezistent la vitamina D:<br />
- osteomalacia<br />
- rahitism<br />
Exclu<strong>de</strong>: osteomalacia adultului (M83.-)<br />
96<br />
osteoporoza (M80-M81)<br />
E83.4 Tulburari <strong>de</strong> <strong>metabolism</strong> al magneziului<br />
Hipermagnezemia<br />
Hipomagnezemia<br />
E83.5 Tulburari <strong>de</strong> <strong>metabolism</strong> al calciului<br />
Hipocalcemia hipocalciurica familiala<br />
Hipercalciuria idiopatica<br />
Exclu<strong>de</strong>: chondrocalcinoza (M11.1-<br />
M11.2)<br />
hiperparatiroidism (E21.0-<br />
E21.3)<br />
E83.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
mineralelor<br />
E83.9 Tulburari <strong>de</strong> <strong>metabolism</strong> al mineralelor,<br />
nespecificate<br />
E84<br />
<br />
0402<br />
Fibroza chistica<br />
Inclu<strong>de</strong>: mucoviscidoza<br />
E84.0 Fibroza chistica cu manifestari<br />
pulmonare<br />
E84.1 Fibroza chistica cu manifestari intestinale<br />
Ileus meconial† (P75*)<br />
Exclu<strong>de</strong>: obstructia meconiana in cazurile<br />
un<strong>de</strong> se stie ca fibroza<br />
chistica nu este prezenta<br />
(P76.0)<br />
E84.8 Fibroza chistica cu alte manifestari<br />
Fibroza chistica cu manifestari combinate<br />
E84.9 Fibroza chistica, nespecificata<br />
E85 Amiloidoza<br />
Exclu<strong>de</strong>: boala Alzheimer (G30.-)<br />
amiloidoza primara (D47.7)<br />
E85.0 Amiloidoza heredofamiliala<br />
nonneuropatica<br />
Febra familiala mediteraneana<br />
Nefropatia amiloida ereditara<br />
E85.1 Amiloidoza heredofamiliala neuropatica<br />
Polineuropatia amiloida (portugheza)<br />
E85.2 Amiloidoza heredofamiliara, nespecificata<br />
E85.3<br />
<br />
1426<br />
Amiloidoza <strong>si</strong>stemica secundara<br />
Amiloidoza asociata cu hemodializa<br />
E85.4 Amiloidoza la unul sau mai multe organe<br />
Amiloidoza localizata<br />
E85.8 Alte amiloidoze<br />
E85.9 Amiloidoza, nespecificata<br />
E86<br />
Hipovolemia, <strong>de</strong>shidratarea<br />
Deshidratare<br />
Depletia volumului <strong>de</strong> plasma sau a<br />
lichidului extracelular<br />
Hipovolemia<br />
Exclu<strong>de</strong>: <strong>de</strong>shidratarea nou-nascutului<br />
(P74.1)<br />
soc hipovolemic:<br />
- NOS (R57.1)<br />
- postprocedural (T81.1)<br />
- traumatic (T79.4)<br />
E87 Alte tulburari <strong>de</strong> echilibru acidobazic,<br />
hidric <strong>si</strong> electrolitic<br />
E87.0 Hiperosmolaritate <strong>si</strong> hipernatremie<br />
Exces <strong>de</strong> sodiu [Na]<br />
Supraincarcare cu sodiu [Na]<br />
Exclu<strong>de</strong>: cu diabet mellitus (E1 - E14 <strong>de</strong><br />
obicei cu al patrulea caracter .0)<br />
E87.1 Hipoosmolaritate <strong>si</strong> hiponatremie<br />
Carenta <strong>de</strong> sodiu [Na]<br />
Exclu<strong>de</strong>: <strong>si</strong>ndromul <strong>de</strong> secretie anormala<br />
a hormonului antidiuretic<br />
(E22.2)<br />
E87.2 Acidoza<br />
Acidoza:<br />
- lactica<br />
- metabolica<br />
- NOS<br />
- respiratorie<br />
Exclu<strong>de</strong>: acidoza diabetica (E10 - E14 <strong>de</strong><br />
obicei cu al patrulea caracter .1)<br />
E87.3 Alcaloza<br />
Alcaloza:<br />
- metabolica<br />
- NOS<br />
- respiratorie<br />
E87.4 Tulburari mixte ale echilibrului acidobazic<br />
E87.5 Hiperpotasemie<br />
Exces <strong>de</strong> pota<strong>si</strong>u [K]<br />
Supraincarcare cu pota<strong>si</strong>u [K]<br />
E87.6 Hipopotasemie<br />
Carenta <strong>de</strong> pota<strong>si</strong>u [K]<br />
E87.7 Supraincarcare cu lichi<strong>de</strong><br />
Exclu<strong>de</strong>: e<strong>de</strong>m (R60.-)<br />
E87.8 Alte tulburari hidrice <strong>si</strong> electrolitice,<br />
necla<strong>si</strong>ficate altun<strong>de</strong>va<br />
Dezechilibru electrolitic NOS<br />
Hipercloremia<br />
Hipocloremia<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002
E88 Alte tulburari <strong>de</strong> <strong>metabolism</strong><br />
Folo<strong>si</strong>ti un cod aditional pentru cauza<br />
externa (Capitolul XX) pentru a i<strong>de</strong>ntifica<br />
medicamentul, daca sunt induse<br />
medicamentos.<br />
Exclu<strong>de</strong>: histiocitoza X (cronica) (D76.0)<br />
E88.0 Tulburari <strong>de</strong> <strong>metabolism</strong> al alfaproteinelor,<br />
necla<strong>si</strong>ficate altun<strong>de</strong>va<br />
Deficit <strong>de</strong> alfa-1-antitrip<strong>si</strong>na<br />
Bisalbuminemia<br />
Exclu<strong>de</strong>: tulburari <strong>de</strong> <strong>metabolism</strong> al<br />
lipoproteinelor (E78.-)<br />
gammapatia monoclonala<br />
(D47.2)<br />
hipergammaglobulinemia<br />
policlonala (D89.0)<br />
macroglobulinemia<br />
Wal<strong>de</strong>nström (C88.0)<br />
E88.1 Lipodistrofia, necla<strong>si</strong>ficata altun<strong>de</strong>va<br />
Lipodistrofia NOS<br />
Exclu<strong>de</strong>: Boala Whipple (K90.8)<br />
E88.2 Lipomatoza, necla<strong>si</strong>ficata altun<strong>de</strong>va<br />
Lipomatoza:<br />
- dureroasa [Dercum]<br />
- NOS<br />
E88.8 Alte tulburari <strong>de</strong> <strong>metabolism</strong> specificate<br />
Defecte ale canalului respirator<br />
mitocondrial:<br />
- stergerea DNA mitocondrial<br />
- <strong>de</strong>ficienta <strong>de</strong> NADH-coenzima Q<br />
reductaza<br />
- NOS<br />
- <strong>de</strong>ficienta <strong>de</strong> coenzima Q-citocroma<br />
reductaza<br />
- <strong>de</strong>ficienta <strong>de</strong> succinat coenzima Q<br />
reductaza<br />
Boala Hoffa-Kastert<br />
A<strong>de</strong>nolipomatoza Launois-Bensau<strong>de</strong><br />
Mitocondrial(a):<br />
- citopatia NOS<br />
- <strong>de</strong>fect NOS<br />
- boala NOS<br />
- tulburare NOS<br />
- <strong>si</strong>ndrom NOS<br />
Trimetillaminuria<br />
Codificati mai intai manifestarea(arile), daca<br />
este cunoscuta.<br />
E88.9 Tulburari metabolice, nespecificate<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
E89 Tulburari postprocedurale <strong>endocrine</strong><br />
<strong>si</strong> metabolice, necla<strong>si</strong>ficate<br />
altun<strong>de</strong>va<br />
E89.0 Hipotiroidism postprocedural<br />
Hipotiroidism dupa iradiere<br />
E89.1<br />
<br />
0401<br />
Hipoinsulinemia postprocedurala<br />
Hiperglicemia dupa pancreatectomie<br />
E89.2 Hipoparatiroidism postprocedural<br />
Tetania paratireopriva<br />
E89.3 Hipopituitarism postprocedural<br />
Hipopituitarism dupa iradiere<br />
E89.4 Insuficienta ovariana postprocedurala<br />
E89.5 Hipofunctiunea testiculara<br />
postprocedurala<br />
E89.6 Hipofunctiunea adrenocorticala<br />
(medulara) postprocedurala<br />
E89.8 Alte tulburari metabolice <strong>si</strong> endrocrine<br />
postprocedurale<br />
E89.9 Tulburari metabolice <strong>si</strong> endrocrine<br />
postprocedurale, nespecificate<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 97