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How reliable are metabolite measurements in IEM - ERNDIM

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<strong>in</strong>terlab CV for quantitative schemes 2005<br />

Scheme Best Worst<br />

Am<strong>in</strong>o Acids 6.4 % (Val<strong>in</strong>e) 253 % (hydroxyprol<strong>in</strong>e)<br />

Special assays Ur<strong>in</strong>e 12.7 % (Carnit<strong>in</strong>e) 198 % (sodium thiosulfate)<br />

Special Assays Serum 3.5 % (Uric Acid) 190 % (cis-4-decanoic acid)<br />

Organic Acids 42.5 % (ethylmalonate<br />

( ethylmalonate) ) 619 % (4-OH (4 OH-Butyric Butyric acid)<br />

Pur<strong>in</strong>es & Pyrimid<strong>in</strong>es 6.1% (creat<strong>in</strong><strong>in</strong>e) 234 % (dihydro-uracil)<br />

Cyst<strong>in</strong>e 12 % (prote<strong>in</strong>) 104 % (cyst<strong>in</strong>e)

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