Il bambino con sindrome di Prader-Willi - Societa' Italiana Obesità ...
Il bambino con sindrome di Prader-Willi - Societa' Italiana Obesità ...
Il bambino con sindrome di Prader-Willi - Societa' Italiana Obesità ...
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Manifestations and management:<br />
respiratory<br />
In<strong>di</strong>viduals with PWS are at risk of breathing<br />
problems for a variety of reasons :<br />
toracic muscle weakness and hypotonia<br />
reduced muscle tone in the pharynx and upper<br />
airways<br />
obesity<br />
scoliosis<br />
(Nixon & Brouillette, 2002)<br />
Manifestations and management:<br />
respiratory<br />
Evaluation<br />
history<br />
polysomnography<br />
spirometry<br />
Treatment<br />
weight management and avoidance of obesity<br />
regular exercise<br />
nighttime CPAP<br />
treatment with GH leads to<br />
improvement in ventilation