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Določanje encimske aktivnosti v klinične namene

Določanje encimske aktivnosti v klinične namene

Določanje encimske aktivnosti v klinične namene

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fenilalanin <br />

feniketonurija <br />

CH 2 CHCOOH<br />

CH<br />

CH 2 CHCOOH<br />

2 CHCOOH<br />

CH 2 CHCOOH<br />

NH 2<br />

NH<br />

NH 2 2<br />

HO<br />

NH 2<br />

HO<br />

fenilalanin <br />

4-­‐monooksigenaza <br />

CH 2 CHCOOH<br />

CH<br />

CH 2 CHCOOH<br />

2 CHCOOH<br />

CH 2 CHCOOH<br />

NH 2<br />

NH 2<br />

HO<br />

NH 2<br />

HO NH 2<br />

tirozin <br />

CH 2 CCOOH<br />

CH 2 CCOOH<br />

O<br />

O<br />

CH<br />

CH 2 CCOOH<br />

2 CCOOH<br />

O<br />

O HO<br />

HO<br />

CH 2 CCOOH<br />

CH 2 CCOOH<br />

O<br />

HO<br />

HO<br />

O<br />

CH<br />

CH 2 CCOOH<br />

2 CCOOH<br />

O<br />

O<br />

hidroksifenilpiruvat <br />

fenilpiruvat <br />

OH<br />

OH<br />

OH<br />

OH<br />

CH 2 COOH<br />

CH 2 COOH<br />

CH<br />

CH 2 COOH<br />

2 COOH<br />

OH<br />

OH<br />

OH<br />

OH<br />

fumarat <br />

+ <br />

acetoacetat <br />

O<br />

O<br />

COO -<br />

COO<br />

COO - -<br />

COO -<br />

O<br />

O<br />

O<br />

C<br />

CH<br />

O<br />

2 OCH 2 -COOCH - C<br />

C<br />

C O CH 2 CH 2 -COO -<br />

2 CH 2 -COO -<br />

CH 2 CH 2 -COO -<br />

maleilacetoacetat

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