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Boli endocrine, de nutritie si metabolism

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E34.3 Insuficienta staturala, necla<strong>si</strong>ficata<br />

altun<strong>de</strong>va<br />

Insuficienta staturala:<br />

- constitutionala<br />

- tip Laron<br />

- NOS<br />

- p<strong>si</strong>hosociala<br />

Exclu<strong>de</strong>: progeria (E34.8)<br />

<strong>si</strong>ndromul Russell-Silver<br />

(Q87.15)<br />

insuficienta staturala:<br />

- achondroplazica (Q77.4)<br />

- hipochondroplazica (Q77.4)<br />

- in <strong>si</strong>ndromul <strong>de</strong> malformatie<br />

congenitala (Q78.1)<br />

- in <strong>si</strong>ndromul dismorfic<br />

specific - codificati <strong>si</strong>ndromul<br />

(vezi In<strong>de</strong>xul alfabetic)<br />

- nutritionala (E45)<br />

- pituitara (E23.0)<br />

- renala (N25.0)<br />

- imuno<strong>de</strong>ficienta cu<br />

micromelie (D82.2)<br />

E34.4 Statura inalta constitutionala<br />

Gigantism constitutional<br />

E34.5 Sindromul <strong>de</strong> rezistenta la androgeni<br />

Pseudohermafroditism masculin cu<br />

rezistenta la androgeni<br />

Tulburarea receptorilor hormonali<br />

periferici<br />

Sindromul Reifenstein<br />

Feminizare testiculara (<strong>si</strong>ndrom)<br />

E34.8 Alte tulburari hormonale specificate<br />

Disfunctia glan<strong>de</strong>i pineale<br />

Progeria<br />

E34.9 Tulburare endocrina, nespecificata<br />

Tulburare:<br />

- endocrina NOS<br />

- hormonala NOS<br />

E35* Tulburari ale glan<strong>de</strong>lor <strong>endocrine</strong> in<br />

boli cla<strong>si</strong>ficate altun<strong>de</strong>va<br />

E35.0* Tulburarile glan<strong>de</strong>i tiroi<strong>de</strong> in boli<br />

cla<strong>si</strong>ficate altun<strong>de</strong>va<br />

Tuberculoza glan<strong>de</strong>i tiroi<strong>de</strong> (A18.8†)<br />

E35.1* Tulburarile glan<strong>de</strong>i adrenale in boli<br />

cla<strong>si</strong>ficate altun<strong>de</strong>va<br />

Siondromul Waterhouse-Fri<strong>de</strong>richsen<br />

(meningococic) (A39.1†)<br />

E35.8* Tulburarile altor glan<strong>de</strong> <strong>endocrine</strong> in boli<br />

cla<strong>si</strong>ficate altun<strong>de</strong>va<br />

<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />

Malnutritia (E40-E46)<br />

Nota: Gradul <strong>de</strong> mal<strong>nutritie</strong> se masoara <strong>de</strong><br />

obicei in termenii greutatii, exprimat<br />

in <strong>de</strong>viatii standard <strong>de</strong> la media<br />

populatiei <strong>de</strong> referinta relevante.<br />

Indicatorul <strong>de</strong> mal<strong>nutritie</strong> apare <strong>de</strong><br />

obicei atunci cand una sau mai multe<br />

din masuratorile anterioare sunt<br />

disponibile, lipsa castigului greutatii la<br />

copii sau evi<strong>de</strong>nta pier<strong>de</strong>rii greutatii la<br />

copii sau adulti. Cand numai o<br />

masuratoare este disponibila,<br />

diagnosticul se bazeaza pe<br />

probabilitati <strong>si</strong> nu este <strong>de</strong>finitiv fara<br />

alte teste clinice sau <strong>de</strong> laborator. In<br />

circumstante exceptionale in care nu<br />

este disponibila nici o masuratoare a<br />

greutatii, diagnosticul se va baza pe<br />

investigatiile clinice.<br />

Daca o greutate observata este sub<br />

valoarea medie a populatiei <strong>de</strong><br />

referinta, exista o probabilitate mare<br />

<strong>de</strong> mal<strong>nutritie</strong> severa atunci cand<br />

valoarea observata este <strong>si</strong>tuata cu 3<br />

sau mai multe <strong>de</strong>viatii standard sub<br />

valoarea medie a populatiei <strong>de</strong><br />

referinta; o mare probabilitate <strong>de</strong><br />

mal<strong>nutritie</strong> mo<strong>de</strong>rata pentru o valoare<br />

observata se <strong>si</strong>tueaza intre 2 <strong>si</strong> mai<br />

putin <strong>de</strong> 3 <strong>de</strong>viatii standard sub<br />

aceasta medie; <strong>si</strong> o probabilitate<br />

mare <strong>de</strong> mal<strong>nutritie</strong> usoara pentru o<br />

valoare observata, se localizeaza intre<br />

1 <strong>si</strong> mai putin <strong>de</strong> 2 <strong>de</strong>viatii standard<br />

sub aceasta medie.<br />

Exclu<strong>de</strong>: malabsorbtia intestinala (K90.-)<br />

anemii nutritionale (D50-D53)<br />

sechele ale mal<strong>nutritie</strong>i proteinoenergetice<br />

(E64.0)<br />

infometare (T73.0)<br />

Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 89<br />

E40<br />

E41<br />

E42<br />

Kwashiorkor<br />

Malnutritia severa cu e<strong>de</strong>m nutritional cu<br />

<strong>de</strong>pigmentarea pielii <strong>si</strong> a parului<br />

Exclu<strong>de</strong>: kwashiorkor <strong>de</strong> marasm (E42)<br />

Marasm nutritional<br />

Mal<strong>nutritie</strong> grava cu marasm<br />

Exclu<strong>de</strong>: kwashiorkor <strong>de</strong> marasm (E42)<br />

Kwashiorkor <strong>de</strong> marasm<br />

Mal<strong>nutritie</strong> proteino-energetica grava [ca la<br />

E43]:<br />

- forma intermediara<br />

- cu semne atat <strong>de</strong> kwashiorkor, cat <strong>si</strong> <strong>de</strong><br />

marasm

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