Boli endocrine, de nutritie si metabolism
Boli endocrine, de nutritie si metabolism
Boli endocrine, de nutritie si metabolism
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E34.3 Insuficienta staturala, necla<strong>si</strong>ficata<br />
altun<strong>de</strong>va<br />
Insuficienta staturala:<br />
- constitutionala<br />
- tip Laron<br />
- NOS<br />
- p<strong>si</strong>hosociala<br />
Exclu<strong>de</strong>: progeria (E34.8)<br />
<strong>si</strong>ndromul Russell-Silver<br />
(Q87.15)<br />
insuficienta staturala:<br />
- achondroplazica (Q77.4)<br />
- hipochondroplazica (Q77.4)<br />
- in <strong>si</strong>ndromul <strong>de</strong> malformatie<br />
congenitala (Q78.1)<br />
- in <strong>si</strong>ndromul dismorfic<br />
specific - codificati <strong>si</strong>ndromul<br />
(vezi In<strong>de</strong>xul alfabetic)<br />
- nutritionala (E45)<br />
- pituitara (E23.0)<br />
- renala (N25.0)<br />
- imuno<strong>de</strong>ficienta cu<br />
micromelie (D82.2)<br />
E34.4 Statura inalta constitutionala<br />
Gigantism constitutional<br />
E34.5 Sindromul <strong>de</strong> rezistenta la androgeni<br />
Pseudohermafroditism masculin cu<br />
rezistenta la androgeni<br />
Tulburarea receptorilor hormonali<br />
periferici<br />
Sindromul Reifenstein<br />
Feminizare testiculara (<strong>si</strong>ndrom)<br />
E34.8 Alte tulburari hormonale specificate<br />
Disfunctia glan<strong>de</strong>i pineale<br />
Progeria<br />
E34.9 Tulburare endocrina, nespecificata<br />
Tulburare:<br />
- endocrina NOS<br />
- hormonala NOS<br />
E35* Tulburari ale glan<strong>de</strong>lor <strong>endocrine</strong> in<br />
boli cla<strong>si</strong>ficate altun<strong>de</strong>va<br />
E35.0* Tulburarile glan<strong>de</strong>i tiroi<strong>de</strong> in boli<br />
cla<strong>si</strong>ficate altun<strong>de</strong>va<br />
Tuberculoza glan<strong>de</strong>i tiroi<strong>de</strong> (A18.8†)<br />
E35.1* Tulburarile glan<strong>de</strong>i adrenale in boli<br />
cla<strong>si</strong>ficate altun<strong>de</strong>va<br />
Siondromul Waterhouse-Fri<strong>de</strong>richsen<br />
(meningococic) (A39.1†)<br />
E35.8* Tulburarile altor glan<strong>de</strong> <strong>endocrine</strong> in boli<br />
cla<strong>si</strong>ficate altun<strong>de</strong>va<br />
<strong>Boli</strong> <strong>endocrine</strong>, <strong>de</strong> <strong>nutritie</strong> <strong>si</strong> <strong>metabolism</strong><br />
Malnutritia (E40-E46)<br />
Nota: Gradul <strong>de</strong> mal<strong>nutritie</strong> se masoara <strong>de</strong><br />
obicei in termenii greutatii, exprimat<br />
in <strong>de</strong>viatii standard <strong>de</strong> la media<br />
populatiei <strong>de</strong> referinta relevante.<br />
Indicatorul <strong>de</strong> mal<strong>nutritie</strong> apare <strong>de</strong><br />
obicei atunci cand una sau mai multe<br />
din masuratorile anterioare sunt<br />
disponibile, lipsa castigului greutatii la<br />
copii sau evi<strong>de</strong>nta pier<strong>de</strong>rii greutatii la<br />
copii sau adulti. Cand numai o<br />
masuratoare este disponibila,<br />
diagnosticul se bazeaza pe<br />
probabilitati <strong>si</strong> nu este <strong>de</strong>finitiv fara<br />
alte teste clinice sau <strong>de</strong> laborator. In<br />
circumstante exceptionale in care nu<br />
este disponibila nici o masuratoare a<br />
greutatii, diagnosticul se va baza pe<br />
investigatiile clinice.<br />
Daca o greutate observata este sub<br />
valoarea medie a populatiei <strong>de</strong><br />
referinta, exista o probabilitate mare<br />
<strong>de</strong> mal<strong>nutritie</strong> severa atunci cand<br />
valoarea observata este <strong>si</strong>tuata cu 3<br />
sau mai multe <strong>de</strong>viatii standard sub<br />
valoarea medie a populatiei <strong>de</strong><br />
referinta; o mare probabilitate <strong>de</strong><br />
mal<strong>nutritie</strong> mo<strong>de</strong>rata pentru o valoare<br />
observata se <strong>si</strong>tueaza intre 2 <strong>si</strong> mai<br />
putin <strong>de</strong> 3 <strong>de</strong>viatii standard sub<br />
aceasta medie; <strong>si</strong> o probabilitate<br />
mare <strong>de</strong> mal<strong>nutritie</strong> usoara pentru o<br />
valoare observata, se localizeaza intre<br />
1 <strong>si</strong> mai putin <strong>de</strong> 2 <strong>de</strong>viatii standard<br />
sub aceasta medie.<br />
Exclu<strong>de</strong>: malabsorbtia intestinala (K90.-)<br />
anemii nutritionale (D50-D53)<br />
sechele ale mal<strong>nutritie</strong>i proteinoenergetice<br />
(E64.0)<br />
infometare (T73.0)<br />
Lista Tabelară a <strong>Boli</strong>lor ICD-10-AM 2002 89<br />
E40<br />
E41<br />
E42<br />
Kwashiorkor<br />
Malnutritia severa cu e<strong>de</strong>m nutritional cu<br />
<strong>de</strong>pigmentarea pielii <strong>si</strong> a parului<br />
Exclu<strong>de</strong>: kwashiorkor <strong>de</strong> marasm (E42)<br />
Marasm nutritional<br />
Mal<strong>nutritie</strong> grava cu marasm<br />
Exclu<strong>de</strong>: kwashiorkor <strong>de</strong> marasm (E42)<br />
Kwashiorkor <strong>de</strong> marasm<br />
Mal<strong>nutritie</strong> proteino-energetica grava [ca la<br />
E43]:<br />
- forma intermediara<br />
- cu semne atat <strong>de</strong> kwashiorkor, cat <strong>si</strong> <strong>de</strong><br />
marasm