MRCPCH 1: Essential Questions in Paediatrics - PasTest

2CARDIOLOGY – QUESTIONS1.5 The following statements about transposition of the greatarteries are true: A there is an association with coarctation of the aorta B arterial switch is the operation of choice, undertaken before2 weeks C the condition is detected antenatally in 50% of cases D presentation can occur upon closure of the ductus arteriosus E the arrangement of the coronary arteries is a major factor in determiningthe success of the surgical repair1.6 The following is true of Eisenmenger syndrome: A affected children are typically teenagers B it can be seen in children with Down syndrome C it is usually secondary to an untreated ventricular septal defect oratrioventricular septal defect D the pulmonary component of the second heart sound is quiet onauscultation E the ECG shows left ventricular hypertrophyBest of Five Questions1.7 You are asked to review an ECG of a baby on the intensive careunit. The baby was well at birth, but soon became unwell andcyanosed. There was no heart murmur. ECG findings reveal asuperior axis, absent right ventricular voltages, and a largeP wave. What is the MOST likely diagnosis? A Complete atrioventricular septal defect B Tricuspid atresia C Critical pulmonary stenosis D Transposition of the great arteries E Total anomalous pulmonary venous connection (TAPVC)1.8 You are asked to see in clinic a 6-year-old girl with a diagnosis ofright atrial isomerism. Which one of the following features wouldyou expect her to have? A Asplenia and a midline liver B Polysplenia C Two functional left lungs D T-cell deficiency E Trisomy 21