Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy

History/EpidemiologyNewly recognized disease, clinical profile first publish in1982Autosomal dominant with penetrance in family members25-30% and 50% in Northern region of Italy.Exact incidence and prevalence is unknown, estimated1:5000– One group of patients diagnosed based on symptoms, EKGchanges and arrhythmias– Other group of clinically silent disease and asymptomatic untilthey manifest as sudden cardiac death– Pt that with CHF where dysplasia was not considered can bemistakenly diagnosed for idiopathic dilated cardiomyopathy