International Classification of Diseases (ICD) - IHE Wiki

System DesignProjekt: SprichWortReferenznummer: 143376-LLP-1-2008-1-SI-KA2-KA2MPVerantwortlicher Partner: IICM, TU GrazLeiter: Univ. Doz. Dr. DI Denis Helic

Option 1: E 1 D 2 1 3 .E 4 E 5 Option 2A: E 1 D 2 D 3 .E 4 E 5 Option 2B: E 1 D 2 D 3 .E 4 E 5“Behaviour”/stage:“Behaviour”/ stage/recurrence:“Behaviour”/ stage/recurrence:0: Benign1: Borderline2: In situ / Stage 03: Invasive, stage NOS4: Invasive Stage I5: Invasive Stage II6: Secondary Stage III7: Secondary Stage IV8: Systemic9: Unknown, unspec, notapp0: Benign1: Borderline2: In situ / Stage 03:Invasive, stage NOS4: Invasive Stage I5: Invasive Stage II6: Secondary Stage III7: Secondary Stage IV8: Systemic9: Unknown, unspec, notappA: Remission/Free ofdiseaseB: Local disease(recurrence/persistent)C: regional disease(recurrence persistent)D: distant disease(recurrence/persistent)E: local and regionalF: local and distantG: regional and distantH: local, regional, anddistant0: Benign1: Borderline2: In situ / Stage 03: Invasive, stage NOS4: Invasive Stage I5: Invasive Stage II6: Secondary Stage III7: Secondary Stage IV8: Systemic9: Unknown, unspec, notappA: Remission/Free ofdiseaseB: Persistent diseaseC: rStageID: rStageIIE: rStageIIIF: rStageIVThe proposed arrangement would facilitate routine case-finding/clinical follow-up. It alsomoves “behaviour” within anatomy rather than the reverse as in ICD-10; all “behaviours” havethe same degree of topographic detail.Char 4:Organ subsite: As in ICD-10, plus alignment with T definition (see oral cavity/pharynx) of TNM.Needs systematic examination of every site and comparison with TNM.Char 5 (pending evaluation by Hematology TAG):Morphology groups: the major ones defined in ICD-O for solid tumors and utilized as aninternational rule to define multiple primary tumours within a patient, with the addition of- 7 -

melanoma (any site). Groups ‘lymphomas’ and ‘leukaemia’ are replaced with 12-15 entitiesfrom the new WHOBB classification of haematopoietic and lymphoid tissues (pending details of‘NOS’ groups to be defined):Morphology groups- 8 -ICD-O M codes1 Squamous carcinomas M 805 - 808, M-812 - 8132 Basal cell carcinomas M-809 – 8113 Adenocarcinomas M 814, M 816, M 819 - 822, M 826- 833, M-835 - 855, M 857, M 8944 Other specific carcinomas M 803 804, M 815, M 817 - 818,M-823, M 824, M-825, M-834, M856, M 858 - 8675 Unspecified carcinomas (NOS) M 801, M 8026 Sarcomas and soft tissue tumors M 868 - 871, M 880 - 892, M 899,M 904, M 912 - 913, M 915 - 925,M 937, M 954 - 9587 Kaposi’s sarcoma M-9148 Mesothelioma M-9059 Melanoma M 872 – 879AMyeloproliferative neoplasms including abnormalitiesof PDGFRA, PDGFRB OR FGFR1 (first two groupsin WHOBB)Pending mapping of ICD-O McodesC Myelodisplastic/myeloproliferative neoplasms Pending mapping of ICD-O McodesD Myelodysplastic syndromes Pending mapping of ICD-O McodesE Acute myeloid leukaemia (AML) Pending mapping of ICD-O McodesF Acute leukaemias of ambiguous lineage Pending mapping of ICD-O McodesG Precursor lymphoid neoplasms Pending mapping of ICD-O McodesH Mature B-cell neoplasms Pending mapping of ICD-O McodesJ Mature T-cell and NL-cell neoplasms Pending mapping of ICD-O McodesK Hodgkin lymphoma Pending mapping of ICD-O McodesL Histiocytic and dendritic cell neoplasms Pending mapping of ICD-O McodesM Post-transplant lymphoproliferative disorders, PTLDNOSPending mapping of ICD-O McodesS Unspecified cell lineage Pending mapping of ICD-O M

codesT Unclassifiable/undetermined Pending: define NOS entities bycell lineage/diagnostic degree ofinvestigationW Other specified types of cancer M 893, M 895 - 898, M 900 - 903,M 906 - 911, M 926 - 936, M 938 -953, M 973 - 975, M-976Z Unspecified types of cancer M 800, M-997If there is the option of a further digit (but the TAG does not feel strongly about this):Char 6: Histopathologic grade- 9 -

specified. The values 1-X are reserved for indicating that additional information is coded, andindicating a simple grammar for linking related clusters of coded information.g. The inclusion of a forced number (1 3 ) is to preclude spelling possible “4-letter words”literally, in any language.h. The requirement that the second digit D 2 be alpha, is to ensure visual distinction ofICD11 linearization codes from ICD10 codes.2. It is desirable that various linearizations should share a common code base, if possible,(i.e. , the first three digits of the code: e.g., ED1. section of the code) which indicates the samegroup of concepts. This way of coding is referred to as STYLE 1 (aka “the Russian doll model”)which allows telescopically nested linearizations for mortality, morbidity, primary care, verbalautopsy, and some short lists. The purpose of STYLE 1 is to facilitate the understanding of thecorrespondence among different linearizations and uses of ICD, within certain bounds.3. In STYLE 2, different linearizations use different codes to represent similar-but-notidentical-concepts.For example, Myocardial Infarction in Verbal Autopsy is not exactly thesame concept in the Morbidity Linearization. Linking similar concepts across varyinglinearizations will be done through the Foundation Layer via their corresponding identifiers.The equivalence of two concepts is created computationally through of Code-Coderelationships across linearizations.a. In STYLE 2 distinguishing among various ICD linearizations would be done using 2-letter prefix codes, (e.g. PC- Primary Care; VA- Verbal Autopsy etc.).4. It is recognized that some linearizations would, however, have a totally different codingscheme and post-coordination, as is currently the case for External Causes and Injury chapter.5. ICD Foundation Component – Linearization system will allow representation ofalternative structures, for example emulation of the US ICD-10-CM, e.g. A11.1111 where Acorresponds to the base 26 Alpha characters (A-Z). This would be an exception that wouldrequire the use of a prefix.Approval status:DEADLINE: 15 February 2012RSG SEG DECISION: to be ApprovedWHO DECISION: to be ApprovedNote: major changes in this version include:a) The truncation of digits from seven to five, recognizing that a multi-dimensional codingspace will, by design, require a smaller coding space.b) Forcing the second digit to be alphac) Clarifying that inheritance is a property of the Foundation Layer and can be visuallyrendered, though linearizations will attempt some reasonable inheritance where practical.d) Introduction of a new set of residual categories (1-X), which form clustering grammarsfor linking multidimensional codes.e) Acknowledging Z codes are a reserved set for modifier- 11 -

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