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Reumatiska sjukdomar med lungengagemang

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Progressiv systemisk skleros<br />

Incidens 4.5-12/1 4.5 12/1 000 000/år 000/<br />

Lungengagemang 70%<br />

Alveolit (dSSc ( dSSc)<br />

Fibros<br />

PAH (lSSc ( lSSc) ) – ung 35%<br />

30% dör d r pga <strong>lungengagemang</strong>

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