28 Wilson's Disease

More documents

Recommendations

Info

• 2 phases – Removal of copper Treatment – Preventing re-accumulation • Evaluation of siblings
• D-penicillamine – Cu chelating moiety Chelators – Reduces the affinity of proteins for copper, allowing previously protein bound copper to bind penicillamine – Excretion via urination – 30% of pts do not tolerate long term 2/2 SE – Early SE- drug sensitivity reactions – Late SE: nephrotic syndrome, bone marrow toxicity, hepatotoxicity, Goodpasture
Page 1 and 2: Morning Report Chief Residents July
Page 3 and 4: • 1 wk of RUQ pain, NV, fatigue
Page 5 and 6: Physical Exam Vitals: T36.6 HR67 RR
Page 7: Wilson’s Disease • AR defect in
Page 10: 2 diseases involving Cu transport W
Page 13 and 14: Fatty infiltration and portal fibro
Page 15 and 16: Our patient’s slit lamp exam
Page 18 and 19: Diagnosis • Coomb’s negative he
Page 22 and 23: • Trientine - Cu chelator Chelato
Page 24 and 25: Dietary Recommendations • Limit i
Page 26 and 27: Liver Transplant Complications •
Page 28 and 29: Back to our patient…. Listed as 1

28 Wilson's Disease

Create successful ePaper yourself

Delete template?

Save as template?