Volume 2 - Issue 2 - IJMD

Case ReportFig 2. Fig 3.Fig 5.Fig 4.Nails appear normal. Scanty eyebrows were seen. Areasof hyperpigmentation were seen around ala of nose(Fig 2). Intra orally patient was partially edentulous.Tooth number 51,61,53,63,83 appears conical (Fig 3).Tooth number 52,62,72,72,81,82 are missing. Upperand lower alveolar ridges appear normal. Her OPGwas relevant to the above findings (Fig 5). So withthe above clinical findings we came to an diagnosis ofHypohidrotic(Anhidrotic) ectodermal dysplasia.DiscussionCurrent classification of ectodermal dysplasias is basedon clinical features. Pure ectodermal dysplasias aremanifested by defects in ectodermal structures alone,while ectodermal dysplasia syndromes are defined bythe combination of ectodermal defects in associationwith other anomalies.Freire-Maia and Pinheiro proposed the first classificationsystem of the ectodermal dysplasias in 1982, 5 withadditional updates in 1994 and 2001. 6,7 Their originalclassification system stratified the ectodermal dysplasiasinto different subgroups according to the presence orabsence of 1 hair anomalies or trichodysplasias, 2 dentalabnormalities, 3 nail abnormalities or onychodysplasias,and 4 eccrine gland dysfunction or dyshidrosis. 6,7Overall, the ectodermal dysplasias were classified intoeither group A disorders, which were manifested bydefects in at least 2 of the 4 classic ectodermal structuresas defined above, with or without other defects, andgroup B disorders, which were manifested by a defectin one classic ectodermal structure (1-4 from above)in combination with 5 a defect in one other ectodermalstructure (ie, ears, lips, dermatoglyphics). Eleven466Indian Journal of Multidisciplinary Dentistry, Vol. 2, Issue 2, February-April 2012