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GANGLIOGLIOMA (WHO I) GANGLIOGLIOMA (WHO I)

GANGLIOGLIOMA (WHO I) GANGLIOGLIOMA (WHO I)

GANGLIOGLIOMA (WHO I) GANGLIOGLIOMA (WHO I)

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Primitive Neoplasms<br />

S-PNET Medullo pPNET/ES AT/RT<br />

Neuronal ± glial Neuronal ± glial Limited neuronal Polyphenotypic<br />

phenotype phenotype phenotype (EMA, SMA,<br />

O13 (CD99) (CD99)- O13 (CD99) (CD99)- O13 (CD99)+ (CD99) VIM, O13)<br />

?-14q, -19q i(17q) t(11;22)<br />

EWS-FLI-1<br />

35% 5-year<br />

survival<br />

70% 5-year<br />

survival<br />

AT/RT, <strong>WHO</strong> IV<br />

40% 5-year<br />

survival<br />

-22q<br />

INI-1 mutations<br />

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