GANGLIOGLIOMA (WHO I) GANGLIOGLIOMA (WHO I)
GANGLIOGLIOMA (WHO I) GANGLIOGLIOMA (WHO I)
GANGLIOGLIOMA (WHO I) GANGLIOGLIOMA (WHO I)
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Primitive Neoplasms<br />
S-PNET Medullo pPNET/ES AT/RT<br />
Neuronal ± glial Neuronal ± glial Limited neuronal Polyphenotypic<br />
phenotype phenotype phenotype (EMA, SMA,<br />
O13 (CD99) (CD99)- O13 (CD99) (CD99)- O13 (CD99)+ (CD99) VIM, O13)<br />
?-14q, -19q i(17q) t(11;22)<br />
EWS-FLI-1<br />
35% 5-year<br />
survival<br />
70% 5-year<br />
survival<br />
AT/RT, <strong>WHO</strong> IV<br />
40% 5-year<br />
survival<br />
-22q<br />
INI-1 mutations<br />