Final Program in it's entirety - MyGirlsBlood
Final Program in it's entirety - MyGirlsBlood
Final Program in it's entirety - MyGirlsBlood
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Posters, Tuesday and Wednesday<br />
Index of Poster Presenters cont’d<br />
17P56<br />
Impact of Acute Bleed<strong>in</strong>g Episodes and Bypass<strong>in</strong>g Agent<br />
(BPA) Adm<strong>in</strong>istration on Patient/Caregiver/Family Daily<br />
Activities <strong>in</strong> Congenital Hemophilia with Inhibitors: Analysis<br />
of the Dos<strong>in</strong>g Observational Study <strong>in</strong> Hemophilia (DOSE)<br />
Recht M1 , Neufeld E2 , Sharma V3 , Cooper D4 , Wilke C5 , Gut R4 1Oregon Health and Science University, Portland, OR, U.S.A.,<br />
2 3 Childrens Hospital of Boston, MA, U.S.A., Brown Cancer<br />
Center, Louisville, KY, U.S.A., 4Novo Nordisk Inc., Pr<strong>in</strong>ceton,<br />
NJ, U.S.A., 5University of Ill<strong>in</strong>ois, Chicago, IL, U.S.A.<br />
17P57<br />
Polymorphisms <strong>in</strong> the VWF Gene and Development of FVIII<br />
Inhibitors <strong>in</strong> Patients with Severe Hemophilia A<br />
Repesse Y1 , De Loncamps A1 , Costa C2 , Kaveri S3 , Borel-<br />
Derlon A1 , Lacroix-Desmazes S3 1Laboratoire d’hematologie, CHU de Caen, Caen, France,<br />
2AP-HP, Groupe Henri Mondor-Albert Chenevier, Service de<br />
Biochimie, UF de Genetique Moleculaire, INSERM Unité 84,<br />
Creteil, France., 3Centre de Recherche des Cordeliers, eq<br />
16, Université Pierre et Marie Curie, Paris, France<br />
17P58<br />
The Natural History of Factor VIII Inhibitors <strong>in</strong> Patients with<br />
Congenital Hemophilia A without Immunotolerance Induction<br />
Rezende S1 , Caram C2 , de Souza R3 , de Sousa J4 , Cerqueira<br />
A5 , van der Bom J6 1Universidade Federal de M<strong>in</strong>as Gerais, Belo Horizonte,<br />
Brazil,<br />
2Grupo de Estudo da Hemostasia e Trombose –<br />
GETHe/UFMG, 3Prefeitura de Pará de M<strong>in</strong>as, 4Target M&E<br />
Consultoria, and 5Fundação HEMOMINAS, Belo Horizonte,<br />
Brazil, 6Leiden University Medical Center, Leiden, the<br />
Netherlands<br />
17P59<br />
The Haemophilia RER Network: Characteristics of Patients<br />
with Inhibitor <strong>in</strong> the Registry<br />
Rivolta G1 , Tagliaferri A1 , Biasoli C2 , Pedrazzi P3 , Valdrè L4 ,<br />
Arbasi M5 1Regional Reference Centre For Inherited Bleed<strong>in</strong>g Disorders,<br />
University-Hospital of Parma, Parma. Italy, 2Haemophilia Centre of Cesena, Cesena. Italy, 3Haemophilia Centre of<br />
Modena, Modena. Italy, 4Haemophilia Centre of Bologna,<br />
Bologna. Italy, 5Haemophilia Centre of Piacenza, Piacenza,<br />
Italy<br />
17P60<br />
Factor VIII and IX Genotype Characterisation of Hemophilia<br />
Patients with Transient or Permanent Inhibitors <strong>in</strong> Argent<strong>in</strong>a<br />
Rossetti L1 , Szurkalo I1 , Primiani L2, 3 , Neme D2, 3 ,<br />
Candela M1, 2, 3 , Pérez Bianco R1, 2, 3<br />
1Instituto de Investigaciones Hematológicas Mariano R<br />
Castex, Academia Nacional de Medic<strong>in</strong>a de Buenos Aires,<br />
2 3 Fundación de la Hemofilia Alfredo Pavlovsky, Grupo<br />
Argent<strong>in</strong>o de Estudio de Inhibidores en Hemofilia (GADEI),<br />
Buenos Aires, Argent<strong>in</strong>a<br />
72<br />
17P61<br />
Address<strong>in</strong>g Cl<strong>in</strong>ical Issues Related to FVIII Inhibitors Us<strong>in</strong>g a<br />
Human BCR Transgenic Mouse: The Model<br />
Benhida A 1 , VanderElst L 1 , Ectors F 2 , Gilles JG 1 , Jacquem<strong>in</strong><br />
M 1 , Sa<strong>in</strong>t-Remy JM 1<br />
1 Center for Molecular and Vascular Biology, University of<br />
Leuven, and 2 GIGA, University of Liège, Belgium<br />
17P62<br />
Address<strong>in</strong>g Cl<strong>in</strong>ical Issues Related to FVIII Inhibitors Us<strong>in</strong>g a<br />
Human BCR Transgenic Mouse: Formation and Suppression<br />
of FVIII Inhibitors<br />
Carlier V, Grailly S, Benhida A, Gilles JG, Jacquem<strong>in</strong> M, Sa<strong>in</strong>t-<br />
Remy JM<br />
Center for Molecular and Vascular Biology, University of<br />
Leuven, Belgium<br />
17P63<br />
European Initiative to Prevent Jo<strong>in</strong>t Damage <strong>in</strong> Hemophilia<br />
Children with Inhibitors (ENJOIH) – A Prospective Study<br />
Santagost<strong>in</strong>o E1 , Auerswald G2 , Jimenez-Yuste V3 , Ljung R4 ,<br />
Morf<strong>in</strong>i M5 , Roc<strong>in</strong>o A6 , Young G7 1A. Bianchi Bonomi Hemophilia and Thrombosis Center,<br />
IRCCS Cà Granda Foundation, Policl<strong>in</strong>icoMaggiore Hospital,<br />
Milan, Italy, 2Prof. Hess Children’s Hospital, Kl<strong>in</strong>ikum Bremen-<br />
Mitte, Bremen, Germany, 3Haematology Department,<br />
Hospital Universitario La Paz, Madrid, Spa<strong>in</strong>, 4Department of Paediatrics and Coagulation Disorders, University Hospital,<br />
Malmö, Sweden, 5Agency for Hemophilia, Reference Center<br />
for Inherited Bleed<strong>in</strong>g Disorders of Tuscany, Department of<br />
Emergency and Reception, Azienda Ospedaliero Universitaria<br />
Careggi, Florence, Italy, 6Haemophilia and Thrombosis<br />
Center, S.Giovanni Bosco Hospital, Naples, Italy, 7Children’s Hospital of Orange County, Orange, CA, U.S.A.<br />
17P64<br />
The Dist<strong>in</strong>ct Role of the Hemostatic Components <strong>in</strong> the<br />
Mode of Action of FEIBA ®<br />
Varadi K, Schoppmann A, Turecek P, Gritsch H, Ehrlich H,<br />
Schwarz H<br />
Baxter BioScience, Vienna, Austria<br />
17P65<br />
[18-F] Fluorodeoxyglucose (FDG) Positron Emission<br />
Tomography (PET) Imag<strong>in</strong>g for Detection of Hemophilic<br />
Arthropathy <strong>in</strong> a Rabbit Model<br />
Shammas A1 , Charron M1 , Metser U2 , Amirabadi A1 , Zhong<br />
A1 , Doria A1 1 2 The Hospital For Sick Children, and Pr<strong>in</strong>cess Margaret<br />
Hospital, Toronto, Canada