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LESIONES ELEMENTALES - Facultad de Ciencias Médicas

LESIONES ELEMENTALES - Facultad de Ciencias Médicas

LESIONES ELEMENTALES - Facultad de Ciencias Médicas

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Poiquilo<strong>de</strong>rmiaPrimaria: Sme. <strong>de</strong> Rothmund-Thomson,disqueratosis congénita, nita, <strong>de</strong> Men<strong>de</strong>s da Costa,poiquilo<strong>de</strong>rmia acroqueratóticatica hereditaria <strong>de</strong> Weary(ampollas acrales, <strong>de</strong>rmatitis eczematiforme,poiquilo<strong>de</strong>rmia y acroqueratosis), síndrome s<strong>de</strong>Kindler, xero<strong>de</strong>ma pigmentoso, anemia <strong>de</strong> Fanconi,Bloom, Franceschetti Jadassohn, Dubowitz y <strong>de</strong>Degos-Touraine, progeria, acrogeria, metageria,Werner, síndrome s<strong>de</strong> Cockayne y la displasia familiarmandíbulobulo-acral. Otros raros síndromes scomo el ABCD(discromatosis braquial cutánea adquirida), el PARC(Poiquilo<strong>de</strong>rmia, Alopecia, Retrognatismo y Cleft:paladar hendido) y el <strong>de</strong> Imerslund-Grasbeck(malabsorción n selectiva <strong>de</strong> vitamina B12 conproteinuria)

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