Vasculitis - Langford.pdf - AInotes
Vasculitis - Langford.pdf - AInotes
Vasculitis - Langford.pdf - AInotes
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Wegener’s Granulomatosis<br />
Treatment<br />
Outcome<br />
Prednisone + daily cyclophosphamide<br />
Prednisone + methotrexate (for mild disease)<br />
• Untreated disease – median survival time 5 months<br />
Mortality from pulmonary or renal failure<br />
• 80% survival with treatment<br />
• Relapse occurs in 50%