Vasculitis - Langford.pdf - AInotes
Vasculitis - Langford.pdf - AInotes
Vasculitis - Langford.pdf - AInotes
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Churg-Strauss Syndrome<br />
Treatment<br />
Outcome<br />
Prednisone<br />
Severe disease: prednisone + daily cyclophosphamide<br />
• Prognosis influenced by factors of severe disease (GI, renal, cardiac, c<br />
CNS)<br />
Cardiac involvement main cause of patient mortality<br />
• Vasculitic relapses occur in 26%<br />
• Relapses of asthma are frequent and may limit ability to taper prednisonep