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Maligna lymfom, WHO-klassifikation<br />

KLL diagnoser SNOMED T/NK-cellslymfom/leukemier SNOMED<br />

Kronisk lymfatisk leukemi, B-cellstyp........................................... 982336 Prekursor T lymfoblastlymfom .................................................... 97293<br />

Kronisk lymfatisk leukemi, T-cellstyp........................................... 982335 Granulär lymfatisk leukemi ........................................................... 98313<br />

Kronisk lymfatisk leukemi, UNS ................................................... 98233 Aggressiv NK-cellsleukemi ........................................................... 99483<br />

B-prolymfocytleukemi.................................................................... 98333 Adult T-cellsleukemi/lymfom ....................................................... 98273<br />

T-prolymfocytleukemmi................................................................. 98343 Mycosis fungoides ......................................................................... 97003<br />

Prolymfocytleukemi UNS .............................................................. 98323 Sézarys syndrom ............................................................................ 97013<br />

Primärt kutant anaplastiskt storcelligt lymfom .............................. 97183<br />

B-cellslymfom/leukemier<br />

Lymfomatoid papulos .................................................................... 97181<br />

Prekursor B lymfoblastlymfom ....................................................... 97283 NK/T-cellslymfom, nasal typ ........................................................ 97193<br />

Lymfocytiskt lymfom ...................................................................... 96703 T-cellslymfom, enteropatityp ........................................................ 97173<br />

Lymfoplasmacytiskt lymfom ........................................................... 96713 Hepatospleniskt T-cellslymfom ..................................................... 97163<br />

Waldenströms makroglobulinemi..................................................... 97613 Subkutant pannikulit-liknande T-cellslymfom ............................. 97083<br />

Spleniskt marginalzonslymfom ....................................................... 96893 Angioimmunoblastiskt T-cellslymfom .......................................... 97053<br />

Hårcellsleukemi ............................................................................... 99403 Perifert T-cellslymfom, ospecif. .................................................... 97023<br />

Extranodalt marginalzonslymfom (MALT-lymfom) ...................... 96993 Anaplastiskt storcelligt lymfom ................................................... 971435<br />

Nodalt marginalzonslymfom ........................................................... 96993 Blastiskt NK-cellslymfom ............................................................. 97273<br />

Follikulärt lymfom ........................................................................... 96903 Hodgkinlymfom<br />

grad I ............................................................................................ 96913 Nodulärt lymfocytdominerat Hodgkinlymfom .............................. 96593<br />

grad II ........................................................................................... 96953 Klassiskt Hodgkinlymfom UNS..................................................... 96503<br />

grad III .......................................................................................... 96983 HL, nodulärskleros ......................................................................... 96633<br />

Mantelcellslymfom .......................................................................... 96733 HL, lymfocytrik typ ....................................................................... 96513<br />

Diffust storcelligt B-cellslymfom .................................................... 96803 HL, blandad typ ............................................................................. 96523<br />

Mediastinalt (thymiskt) storcelligt B-cellslymfom ......................... 96793<br />

Intravaskulärt storcelligt B-cellslymfom ......................................... 96803<br />

HL, lymfocytfattig typ ................................................................... 96533<br />

Primärt effusionslymfom ................................................................. 96783 Ospecificerade koder:<br />

Burkittlymfom ................................................................................. 96873 Malignt lymfom uns ....................................................................... 95903<br />

Lymfomatoid granulomatos ............................................................. 97661 Non-Hodgkinlymfom uns (NHL) .................................................. 95913<br />

Polymorf posttransplantationsrelaterad lymfoprolliferativ<br />

sjukdom ............................................................................................ 99701<br />

Småcelligt/indolent NHL ............................................................. 959131<br />

Blastiskt/aggressivt NHL ............................................................. 959133<br />

B-cellslymfom .............................................................................. 959136<br />

T-cellslymfom .............................................................................. 959135<br />

Småcelligt/indolent NHL, B-cellslymfom............... 959131 och 959136<br />

Småcelligt och indolent och T-cellslymfom............. 959131 och 959135<br />

Blastiskt/aggressivt NHL, B-cellslymfom................ 959133 och 959136<br />

Blastiskt aggressivt NHL, T-cellslymfom................ 959133 och 959135<br />

Rai stadium<br />

0 Lymfocytos enbart<br />

I Lymfoadenopati<br />

II Hepato- och/eller splenomegali +/- lymfadenopati<br />

III Hb

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