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Alport Sendromu

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Steroide rezistan idiopatik NS<br />

• 3 aylık-5 yaşında başlayan NS<br />

• Böbrek yetmezliğine hızlı gidiş<br />

• Sorumlu gen: NPHS2 (1q25-31)<br />

• Podosit-spesifik protein podosin’i kodlar

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