Program Book

not associated with severity of RB.
Conclusions. Directing awareness campaigns to low SES groups may be
of benefit in the UK but ethnicity was not a factor.
Financial disclosure. None
352 RBp113
NEUROPSYCHOMOTOR DEVELOPMENT OF EYE
ENUCLEATED CHILDREN WITH RETINOBLASTOMA
Marcela Bagnatori Braga, Juliana dos Santos Soares, Carla R. Donato
Macedo, Walquyria de Almeida Santos (mabagnatori@uol.com.br)
Purpose. Retinoblastoma is the most common malignant ocular tumor
of childhood, usually presenting before four years of age. The incidence
in Brazil shows an average of 3 to 5 cases/million in children younger
than 14 years old.
Currently, the cure rates of Retinoblastoma are higher because
of the advances in diagnosis and treatment. However, aesthetic,
ophthalmologic, neurocognitive and social effects, as well as visual
impairment, makes eye enucleated children with Retinoblastoma
likely to show deficits in Neuropsychomotor Development and/or
Sensory Integration. The Purpose is present the possible changes in
Neuropsychomotor Development and/or Sensory Integration of eye
enucleated children with Retinoblastoma.
Methods. A study was made at the Pediatric Oncology Institute - GRAACC
/ UNIFESP - São Paulo - Brazil. Two assessment tools were used, the
PEDI and the Sensory Profile.
Results. It was possible to check that children in this sample showed
deficits in Neuropsychomotor Development and/or Sensory Integration.
These changes were graduated from minimal to maximum – following
the assessments used.
Conclusions. From this study was contested an alteration in
Neuropsychomotor Development and/or Sensory Integration of these
children related to the disease, treatment and consequences in the
sensorial and motor system of this population.
Financial disclosure. None
345 RBp114
NURSING GUIDELINES FOR SELF-CARE OF PATIENTS
WITH PROSTHETIC RETINOBLASTOMA: AN EXPERI-
ENCE REPORT
Juliana dos Santos Soares, Carla R.D. Macedo, Adriana M. Duarte
(js_soares3@hotmail.com)
Purpose. Retinoblastoma (RB) is a rare cancer in retina, representing
about 4% of all malignancies of childhood. The treatment modalities
include chemotherapy, focal therapy, radiation and enucleation,
according to the stage of disease. Upon receiving news of the
enucleation, child and family tend to be fragile and frightened by the
surgical procedure, the change in self-image and lifestyle after surgery.
In this context, the role of nurse has great value in educating the patient
and family providing support to deal with the new situation. The Purpose
is to report the experience lived by a Nurse at a Brazilian Hospital of
Pediatric Oncology with the orientation of a child with RB and her family
for self-care after enucleation.
Methods. It is an experience report. About 19 queries were held with
the child and her family immediately after enucleation indication and
throughout the adaptation process in the period from September
2010 to July 2011. With appropriate language for the child age and
RETINOBLASTOMA
Posters
52
parents understanding, graphics and ocular prosthesis models were
used for explanation of the whole procedure and required care after
enucleation.
Results. Subjects discussed in the meetings varies since surgery
procedure to prosthetic eye care. After 10 months of starting the treatment,
child and family became more calm and confident when talking about the
experience of enucleation. The child showed to be able to perform selfcare
under supervision of her mother.
Conclusions. The sections were productive, with effective participation
of patient and parents. As a result of these encounters, a plan for
systematic and individualized care was prepared, with quality, by
identifying the real needs of the child submitted to enucleation and her family.
Financial disclosure. None
33 RBp115
EYE SALVAGE RATE IN 166 PATIENTS WITH INTRAOC-
ULAR RETINOBLASTOMA
Luiz F. Teixeira1,2, Carla R. Donato Macedo2, Virginia L. L Torres1,2,
Camila H. Hashimoto2, Rubens Belfort Neto1,2, Juliana dos Santos
Soares2, Clelia M. Erwenne1,2 (luizfteixeira@hotmail.com)
1. Depatment of Ophthalmology, Federal University of Sao Paulo-
UNIFESP
2. Pediatric Oncology Institute/GRAACC/UNIFESP
Purpose. To evaluate the eye salvage rate in 166 patients with
intraocular retinoblastoma.
Methods. Retrospective review of 217 consecutive eyes with intraocular
retinoblastoma (115 unilateral cases and 51 bilateral cases).
Results. A total of 217 eyes, 9 group A eyes (4%), 22 group B eyes
(10%), 17 group C eyes (8%), 53 group D eyes (24%) and 116 group E
eyes (54%) were treated.
112 eyes (52%), (10 eyes (19%) of group D and 102 eyes (88%) of group
E) were treated with enucleation as primary treatment.
Systemic chemotherapy and/or local therapy were performed as first
treatment in 105 eyes (46%), (9 group A, 22 group B, 17 group C, 43
group D and 14 group E). External beam radiotherapy (EBRT) was used
for major tumor recurrence. Analysing conservative therapies the eye
salvage rate considering all forms of treatments and excluding EBRT
was respectively: 100%/100% for group A, 95%/95% for group B,
88%/82% for group C, 49%/40% for group D and 28%/14% for group
E.
From 217 eyes diagnosed with intraocular disease, 70 eyes (32%) were
saved.
The final eye salvage rate was 100% for group A (n=9), 95% for group
B (n=21), 88% for group C (n=15), 40% for group D (n=21) and 3% for
group E (n=4).
Conclusions. Advanced intraocular disease, group D and E represent
more than 70% of the intraocular disease treated in our institution
with a high rate of primary or secondary enucleation. Groups A, B and
C present excellent outcomes but represent only 28% of the eyes.
Financial disclosure. None
933 RBp116
SYSTEMIC CHEMOTHERAPY IN THE MANAGEMENT
OF RETINOBLASTOMA
John D. McKenzie1, Nisha Sachdev1, Sandra Staffieri1,4, Kary Suen1 , James
E. Elder1,2, John Heath2,3, Peter Downie3 (jdmckenzieonline@gmail.com)