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Chapter 96

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intrapericardial GCT and cardiac GCT. Intrapericardial GCT<br />

occurs most commonly in infants who are less than 12 months old<br />

and present with findings of cardiac tamponade and congestive<br />

heart failure; as most are benign, they are treated with primary<br />

resection. They can have a very complicated intraoperative course<br />

because they often compress the adjacent atria and ascending aorta.<br />

Cardiac GCTs, which are malignant in 25% of the cases, present<br />

with congestive heart failure and/or arrhythmias (as intraventricular<br />

block) and are most commonly located in the right side<br />

of the heart. They are associated with congenital heart disease<br />

(atrial and ventricular septal defects). Although primary surgical<br />

resection is indicated to avert complete cardiac outflow<br />

obstruction, there are times when the GCT is unresectable, making<br />

cardiac transplantation an option. 24<br />

CHAPTER <strong>96</strong> ■ Thoracic Surgery: Surgical Considerations 1645<br />

Lymphangioma<br />

Although these lesions are also referred to as cystic hygromas, the<br />

more current term is lymphangioma. They have an incidence of<br />

1 in 12,000 births and approximately 50 to 65% of them are present<br />

at birth; the vast majority becomes clinically evident before 2 years<br />

of life. 25 They develop as a result of the failure of primitive<br />

lymphatic buds to form communications with adjacent developing<br />

veins; these buds dilate into lymphatic cysts which subsequently<br />

become lymphangiomas. Anatomically, they are most commonly<br />

found in the neck (75%) and less commonly in the mediastinum<br />

(

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