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Le malattie autoinfiammatorie in pediatria-Brachi.pdf

Le malattie autoinfiammatorie in pediatria-Brachi.pdf

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FEBBRE MEDITERRANEA FAMILIARE<br />

(FMF)<br />

E’ la più comune febbre periodica monogenica<br />

Etnicamente circoscritta (popolazioni mediterranee:<br />

armeni, turchi, ebrei, arabi)<br />

Elevata frequenza di portatori: 1/5 - 1/10<br />

Malattia autosomica recessiva

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