Le malattie autoinfiammatorie in pediatria-Brachi.pdf
Le malattie autoinfiammatorie in pediatria-Brachi.pdf
Le malattie autoinfiammatorie in pediatria-Brachi.pdf
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SINDROME DI BLAU<br />
Cl<strong>in</strong>ica: - Artrite<br />
- Rash cutaneo<br />
(esantema ittiosiforme, eritemato-papulare, eritemato papulare, simil orticarioide)<br />
- Uveite<br />
Terapia controversa: steroidi, MTX, Ciclospor<strong>in</strong>a<br />
Diagnosi: genetica. Se genetica negativa, procedere a<br />
biopsia s<strong>in</strong>oviale e/o cutanea (granulomi)<br />
DD con AIG e artriti <strong>in</strong>fettive