Soins maternels intensifs (Maternal Intensive Care) en Belgique - KCE
Soins maternels intensifs (Maternal Intensive Care) en Belgique - KCE
Soins maternels intensifs (Maternal Intensive Care) en Belgique - KCE
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<strong>KCE</strong> Reports 94 <strong>Maternal</strong> <strong>Int<strong>en</strong>sive</strong> <strong>Care</strong> in Belgium 149<br />
Connective tissues disorders<br />
• Every disorder labelled as low-risk by an<br />
connective tissue specialist but not specified as a<br />
disorder requiring a level of intermediate care<br />
Skeletal disorders<br />
• Osteog<strong>en</strong>esis imperfecta ffff type I<br />
• Every disorder labelled as low-risk by an<br />
orthopaedist but not specified as a disorder<br />
requiring a level of intermediate care<br />
Neuromuscular disorders<br />
• Every disorder labelled as low-risk by an<br />
neurologist but not specified as a disorder<br />
requiring a level of intermediate care<br />
Connective tissues disorders<br />
Skeletal disorders<br />
Neuromuscular disorders<br />
• Well equilibrated epileptic pati<strong>en</strong>t (or no active<br />
medical treatm<strong>en</strong>t)<br />
Connective tissues disorders<br />
• Marfan’s disease (G<strong>en</strong>t nosology bbbbccccdddd )<br />
• Ehlers-Danlos’ disease (type I – XI eeee )<br />
• Every disorder labelled as high-risk by a connective<br />
tissue specialist but not specified as a disorder<br />
requiring a level of standard care<br />
Skeletal disorders<br />
• Osteog<strong>en</strong>esis imperfecta: type II-VII<br />
• Every disorder labelled as high-risk by a orthopaedist<br />
but not specified as a disorder requiring a level of<br />
standard care<br />
Neuromuscular disorders<br />
• Epileptic pati<strong>en</strong>t gggg (with active medical treatm<strong>en</strong>t)<br />
• Myasth<strong>en</strong>ia gravis (class I – IVb)<br />
• Steinert’s disease<br />
• Amyotrophic lateral sclerosis<br />
• Hemi-/para-/tetraplegy<br />
• Spina bifida<br />
• Multiple sclerosis hhhh<br />
• Severe neuromuscular infections<br />
• Every disorder labelled as high-risk by a neurologist<br />
but not specified as a disorder requiring a level of<br />
standard care<br />
bbbb Dean, J. et al (2003). The Scottish clinical guidelines and integrated care pathways for Marfan’s syndrome. Retrieved June 1, 2007 from cebam, National guideline clearinghouse<br />
http://www.g<strong>en</strong>isys.hw.ac.uk/g<strong>en</strong>isysDR/NVC/72/Download/msguide.pdf<br />
cccc De Paepe A, Devereux RB, Dietz HC, H<strong>en</strong>nekam RC, Pyeritz RE (1996). Revised diagnostic criteria for the Marfan Syndrome. Am J Med G<strong>en</strong>et; 62: 417-426.<br />
dddd Beighton, P., De Paepe, A., Steinmann, B., Tsipouras, P. & W<strong>en</strong>strup, R. (1998). Ehler-Danlos Syndromes: revised nosology, Villefranche, 1997. American Journal of Medical g<strong>en</strong>etics, 77,<br />
31-37.<br />
eeee Ceccolini, E. (2006). Ehler-Danlos syndrome. Retrieved June 5, 2007 from cebam, emedecine : http://www.emedicine.com/derm/topic696.htm.<br />
ffff Rauch, F. & Glorieux, F.H. (2004). Osteog<strong>en</strong>esis Imperfecta. Lancet. 363(9418):1377-85.<br />
I Mild non-deforming: Normal height or mild short stature; blue sclera; no d<strong>en</strong>tinog<strong>en</strong>esis imperfecta.; II Perinatal lethal: Multiple rib and long-bone fractures at birth;<br />
pronounced deformities; broad long bones; low d<strong>en</strong>sity of skull bones on radiographs; dark sclera; III Severely deforming: Very short; triangular face; severe scoliosis; greyish<br />
sclera; IV Moderately deforming: Moderately short; mild to moderate scoliosis; greyish or white sclera; d<strong>en</strong>tinog<strong>en</strong>esis imperfecta; V Moderately deforming: Mild to moderate<br />
short stature; dislocation of radial head; mineralised interosseous membrane; hyperplastic callus; white sclera; no d<strong>en</strong>tinog<strong>en</strong>esis imperfecta; VI Moderately to severely: Moderately<br />
short; scoliosis; accumulation of osteoid in bone tissue, fish-scale pattern of deforming bone lamellation; white sclera; no d<strong>en</strong>tinog<strong>en</strong>esis imperfecta; VII Moderately deforming: Mild<br />
short stature; short humeri and femora; coxa vara; white sclera; no d<strong>en</strong>tinog<strong>en</strong>esis imperfecta<br />
gggg National collaborating c<strong>en</strong>tre for wom<strong>en</strong>’s and childr<strong>en</strong>’s health. Ant<strong>en</strong>atal care routine care for the healthy pregnant woman, Clinical guideline 23. Retrieved June 18, 2007 from cebam,<br />
rcog: http://www.rcog.org.uk/resources/Public/pdf/Ant<strong>en</strong>atal_<strong>Care</strong>.pdf.