Disease staging: CliniCal anD CoDeD Criteria - HCUP

Clinical Criteria with Description, Diagnostic Findings and ICD-9-CM codes
DXCat Number: END16
MultiStage: No
DXCat Label: Primary Amyloidosis Specificity: A
Etiology: Idiopathic
Stage Description Diagnostic findings ICD-9-CM Codes
1.01 Amyloidosis Primary amyloidosis [operative/pathology report]
DX 2773-27739;
2.01 with hepatosplenomegaly Stage 1.01
STAGE 1.01 + (DX 5718, 7891-
AND hepatomegaly [physical examination or liver/spleen scan or CT scan or MRI report]
7892);
OR splenomegaly [physical examination or liver/spleen scan or CT scan
or MRI report]
2.02 with nephrotic syndrome Stage 1.01-2.01
AND hypoalbuminemia:
AND urine protein > 3 gm/24 hrs [urine chemistry report]
STAGE 1.01-2.01 + DX 58381;
STAGE 1.01-2.01 + GROUP
HYPOALBUMIN + DX 7910;
2.03 with pulmonary involvement Stage 1.01-2.02
AND pulmonary amyloidosis [operative/pathology report or biopsy report]
2.04 with intestinal obstruction Stage 1.01-2.03
AND large bowel obstruction [KUB x-ray report or operative/pathology report]
OR small bowel obstruction [KUB x-ray report or operative/pathology report]
3.01 Amyloidosis of the heart Stage 1.01-2.04
AND cardiac amyloidosis [echocardiogram report]
3.02 with renal failure Stage 2.01-3.01
AND renal failure:
3.03 with congestive heart failure Stage 3.01
AND congestive heart failure:
3.04 with respiratory failure Stage 2.01-3.03
AND respiratory failure:
3.05 with shock Stage 2.01-3.04
AND shock:
4.00 with death Stage 2.01-3.05
AND death
STAGE 1.01-2.02 + DX 5178;
STAGE 1.01-2.03 + (DX 5373,
56089, 5609);
STAGE 1.01-2.04 + DX 4257;
STAGE 1.01-3.01 + GROUP
REN_FAIL_ACU;
STAGE 1.01-3.02 + GROUP
CHF__NON_HTN;
STAGE 1.01-3.03 + GROUP
RESP_FAIL;
STAGE 1.01-3.04 + (GROUP
SHOCKC OR GROUP SHOCKN) ;
NO;
References:
Adelman DC, Terr A. Amyloidosis. In: Tierney Jr LM, McPhee SJ Papadakis MA, eds. Current Medical Diagnosis & Treatment. Stamford, CT: Appleton & Lange; 1998:750-751.
Falk RH, Comenzo RL, Skinner M. The systemic amyloidoses. N Engl J Med. 1997;337(13):898-909.
Kushwaha SS, Fallon JT, Fuster V. Restrictive cardiomyopathy. N Engl J Med. 1997;336(4):267-276.
Sipe JD, Cohen AS. Amyloidosis. In: Fauci AS, Braunwald E, Isselbacher KJ, Wilson JD, Martin JB, Kasper DL, Hauser SL, Longo, DL, eds. Harrison’s Principles of Internal
Medicine. 14th ed. New York, NY: McGraw-Hill; 1998:1856-1860.
Thursday, January 07, 2010 9:21:28 AM
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