Disease staging: CliniCal anD CoDeD Criteria - HCUP

Clinical Criteria with Description, Diagnostic Findings and ICD-9-CM codes
DXCat Number: HEP13
MultiStage: No
DXCat Label: Wilson's Disease Specificity: A
Etiology: Metabolic
Stage Description Diagnostic findings ICD-9-CM Codes
1.01 Wilson's disease or hepatolenticular urinary copper excretion ≥ 100mg/24 hrs [urine chemistry report]
DX 2751;
degeneration
OR serum ceruloplasmin ≤ 200 mg/l [chemistry report]
AND Kayser-Fleischer ring [slit lamp ophthalmoscopy report]
OR hepatic copper ≥ 250ug/g dry liver weight [biopsy report]
OR defect chromosome 13 ATP7B gene [genetics report]
2.01 with hepatitis or splenomegaly Stage 1.01
AND splenomegaly
OR hepatitis:
2.02 with CNS disorders Stage 1.01-2.01
AND fine tremors of upper extremities
OR choreoathetosis
OR muscular rigidity
OR dysarthria
2.03 with hemolyic anemia Stage 1.01-2.02
AND hemolysis:
2.04 Chronic active hepatitis Stage 1.01-2.03
AND chronic active hepatitis [operative/pathology report]
2.05 with coagulation defects Stage 1.01-2.04
AND coagulation defects:
3.01 with renal failure Stage 1.01-2.05
AND renal failure:
3.02 with hepatic coma Stage 1.01-3.01
AND hepatic coma:
OR acute hepatic necrosis [operative/ pathology report]
3.03 with shock Stage 1.01-3.02
AND shock:
4.00 with death Stage 1.01-3.02
AND death
STAGE 1.01 + (DXCAT HEP10 OR
DX 7824, 7894);
STAGE 1.01-2.01 + (DX 3331-
3333, 3335-3336, 33371, 33379,
33381-33382, 33394, 7845);
STAGE 1.01-2.01 + (DX 28310,
28319, 2839);
STAGE 1.01-2.03 + DX 57149;
STAGE 1.01-2.04 + GROUP
COAG_DEFECT;
STAGE 1.01-2.05 + GROUP
REN_FAIL_ACU;
STAGE 1.01-3.01 + (DX 07041,
07044, 07071, 5722) ;
STAGE 1.01-3.02 + (GROUP
SHOCKC OR GROUP SHOCKN) ;
NO;
Thursday, January 07, 2010 9:22:19 AM
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