Disease staging: CliniCal anD CoDeD Criteria - HCUP

Clinical Criteria with Description, Diagnostic Findings and ICD-9-CM codes
DXCat Number: MUS39
MultiStage: No
DXCat Label: Progressive Systemic Sclerosis Specificity: A
Etiology: Immune
Stage Description Diagnostic findings ICD-9-CM Codes
1.01 Progressive systemic sclerosis, scleroderma Scleroderma [skin biopsy report]
DX 7101-7102;
or CREST syndrome
OR CREST syndrome:
OR calcinosis
AND Raynaud’s phenomenon
AND dysphagia
AND sclerodactyly
AND telangiectasias
Presumptive Diagnostic Findings:
Raynaud’s phenomenon
AND thickening of the skin proximal to the metacarpal-phalangeal joints
OR swelling of acral portions of the digits
1.02 with flexion contractures of the hands or
arthralgias
Stage 1.01
AND flexion contractures of one or both hands
OR polyarthralgia
2.01 with trophic ulcers of the hands Stage 1.01-1.02
AND trophic skin ulcers of the hand
2.02 with gastroesophageal reflux or Stage 1.01-2.01
pneumatosis intestinalis
AND reflux esophagitis [endoscopy report or UGI series report]
OR pneumatosis cystoides intestinalis [abdominal x-ray report]
2.03 with biliary cirrhosis or jaundice Stage 1.01-2.02
AND biliary cirrhosis [liver biopsy report]
OR jaundice:
2.04 with lung fibrosis Stage 1.01-2.03
AND lung fibrosis [x-ray report or CT scan report]
2.05 with cardiac conduction abnormalities Stage 1.01-2.04
AND cardiac conduction abnormalities:
2.06 with hypertension Stage 1.01-2.05
AND hypertension:
3.01 with renal failure Stage 1.01-2.06
AND renal failure:
3.02 with pulmonary hypertension Stage 1.01-3.01
AND pulmonary artery pressure > 30.5 mmHg [cardiac catheterization report]
STAGE 1.01 + (DX 71844, 71944,
71949);
STAGE 1.01-1.02 + DX 7078;
STAGE 1.01-2.01 + (DX 53011,
53081, 56989);
STAGE 1.01-2.02 + (DX 5716,
7824);
STAGE 1.01-2.03 + (DX 5163,
5178);
DX 5172;
STAGE 1.01-2.04 + GROUP
COND_BBBS;
STAGE 1.01-2.05 + DXCAT CVS13;
STAGE 1.01-2.06 + (GROUP
REN_FAIL_ACU OR GROUP
REN_FAIL_CHR);
STAGE 1.01-3.01 + DX 4168;
Thursday, January 07, 2010 9:22:41 AM
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