Disease staging: CliniCal anD CoDeD Criteria - HCUP

Clinical Criteria with Description, Diagnostic Findings and ICD-9-CM codes
DXCat Number: RES08
MultiStage: No
DXCat Label: Cystic Fibrosis Specificity: A
Etiology: Genetic (or hereditary)
Stage Description Diagnostic findings ICD-9-CM Codes
0.00 Cystic fibrosis genetic carrier Added stage 5/8/06 cb
DX V8381;
1.01 Cystic fibrosis History of Mendelian inheritance pattern, autosomal recessive, for cystic fibrosis
DX 27700, 27709;
OR linkage markers for cystic fibrosis on chromosome 7 [chromosome study report]
AND Sweat chloride concentration above> 80 meq/L ≥ age 20 on two occasions
[quantitative pilocarpine iontophoresis sweat test]
AND Sweat chloride concentration above> 60 meq/L ≤ age 20 on two occasions
[quantitative pilocarpine iontophoresis sweat test]
1.02 with chronic Pseudomonas aeruginosa or
Staphylococcus aureus bronchitis
Stage 1.01
AND loss of cilia and destruction and fibrosis of bronchial walls [operative/pathology report]
OR bronchiectasis [bronchogram x-ray report or CT scan report]
OR hyperinflation [chest x-ray report]Stage 1.01
AND productive cough which ≥ 3 months/ year ≥ 2 consecutive years
AND Pseudomonas aeruginosa in sputum [culture report]
OR Staphylococcus aureus in sputum [culture report]
STAGE 1.01 + (DX 490, 4910, 4911-
4912, 49120, 49121, 49122, 4918,
4919) + (DX 04111-04112, 0417);
DX 27702;
1.03 with bronchiectasis or hyperinflation Stage 1.01-1.02
AND loss of cilia and destruction and fibrosis of bronchial walls [operative/pathology report]
OR bronchiectasis [bronchogram x-ray report or CT scan report]
OR hyperinflation [chest x-ray report]
2.01 with chronic obstructive pulmonary disease
or chronic restrictive lung disease
Stage 1.01-1.03
AND COPD:
OR
restrictive lung disease:
2.02 with pancreatic insufficiency Stage 1.02-2.01
AND pancreatic insufficiency:
2.03 with diabetes mellitus Stage 1.02-2.02
AND diabetes mellitus:
2.04 with meconium ileus Stage 1.02-2.03
AND abnormally thick, tenacious and stringy meconium
OR undigested albumin in stool (meconium/water, 1:1, mixture with trichloroacetic
acid test yields precipitate)
AND ileus pattern [KUB x-ray report]
2.05 with pneumonia Stage 1.02-2.04
AND pneumonia:
STAGE 1.01-1.02 + (DX 4940,
4941);
STAGE 1.01-1.03 + DX 496;
STAGE 1.01-2.01 + GROUP
PANCR_INSUFF;
STAGE 1.01-2.02 + (DXCAT END04
OR DXCAT END05);
DX 27701;
STAGE 1.01-2.04 + (DXCAT RES15
OR DXCAT RES16 OR DXCAT
RES17 OR DXCAT RES12 OR
DXCAT RES19) ;
Thursday, January 07, 2010 9:23:10 AM
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