BNF for Children 2011-2012

784 A2.7 Nutritional supplements for metabolic diseases BNFC 2011–2012Appendix 2: Borderline substancesDocOmega c (Vitaflo)Powder, protein (cows’ milk, soya) 100 mg, carbohydrate3.2 g, fat 500 mg (of which docosahexaenoic acid 200 mg),fibre nil, energy 74 kJ (18 kcal)/4 g, with minerals, net price30 x 4-g sachets = £32.20Nutritional supplement for the dietary management of inbornerrors of metabolism for adults and children from birthEAA c Supplement (Vitaflo)Powder, protein equivalent (essential amino acids) 5 g,carbohydrate 4 g, fat nil, energy 151 kJ (36 kcal)/12.5 g, withvitamins, minerals, and trace elements. Tropical flavour, netprice 50 12.5-g sachets = £174.48Nutritional supplement for the dietary management of disordersof protein metabolism including urea cycle disorders in childrenover 3 yearsKeyOmega c (Vitaflo)Powder, protein (cows’ milk, soya) 170 mg, carbohydrate2.8 g, fat 800 mg (of which arachidonic acid 200 mg, docosahexaenoicacid 100 mg), energy 80 kJ (19 kcal)/4 g, netprice 30 4-g sachet = £32.92Nutritional supplement for the dietary management of inbornerrors of metabolismLeucine Amino Acid Supplement (Vitaflo)Powder, leucine 100 mg, carbohydrate 4 g, fat nil, energy64 kJ (15 kcal)/4 g, net price 30 4-g sachets = £44.48Nutritional supplement for the dietary management of inbornerrors of amino acid metabolism in children over 1 yearLow protein drink (Milupa )Powder, protein (cows’ milk) 4.5 g (phenylalanine 100 mg),carbohydrate 59.5 g, fat 29.9 g, fibre nil, energy 2194 kJ(528 kcal)/100 g, with vitamins, minerals, and trace elements.Contains lactose. Net price 400 g = £7.76 (5-g measuringscoop provided)Nutritional supplement for the dietary management of inbornerrors of amino acid metabolism in adults and children over 1 yearNote Termed Milupa c lp-drink by manufacturerPhenylalanine Amino Acid Supplement (Vitaflo)Powder, phenylalanine 50 mg, carbohydrate 3.8 g, energy64 kJ (15 kcal)/4 g, net price 30 4-g sachets = £43.18Nutritional supplement for use in the dietary management ofinborn errors of metabolism onlyProZero c (Vitaflo)Liquid, carbohydrate 8.1 g (of which sugars 3.5 g), fat 3.8 g,energy 278 kJ (66 kcal)/100 mL. Contains lactose. Net price18 250 mL = £22.50; 6 1 litre = £30.00A protein-free nutritional supplement for the dietary managementof inborn errors of metabolism in children over 6 months andadultsPhenylketonuriaAdd-Ins c (SHS)Powder, protein equivalent (containing essential and nonessentialamino acids except phenylalanine) 10 g, carbohydratenil, fat 5.1 g, energy 359 kJ (86 kcal)/18.2-g sachet,with vitamins, minerals, and trace elements. Unflavoured,net price 60 18.2-g sachets = £315.60Nutritional supplement for the dietary management of provenphenylketonuria in children over 4 yearsEasiphen c (SHS)Liquid, protein equivalent (containing essential and nonessentialamino acids except phenylalanine) 6.7 g, carbohydrate5.1 g, fat 2 g, energy 275 kJ (65 kcal)/100 mL withvitamins, minerals, and trace elements. Forest berries ororange flavour, net price 250-mL carton = £8.11Nutritional supplement for the dietary management of provenphenylketonuria in children over 8 yearsLophlex c (SHS)Powder, protein equivalent (essential and non-essentialamino acids except phenylalanine) 20 g, carbohydrate 2.5 g,fat 60 mg, fibre 220 mg, energy 385 kJ (91 kcal)/27.8-gsachet, with vitamins, minerals, and trace elements. Flavours:berry, orange, or unflavoured, net price 30 x 27.8-gsachets = £243.60Nutritional supplement for the dietary management of provenphenylketonuria in children over 8 years and adults includingpregnant womenLoprofin c PKU Drink (SHS)Liquid, protein (cows’ milk) 400 mg (phenylalanine 10 mg),lactose 9.4 g, fat 2 g, energy 165 kJ (40 kcal)/100 mL. Netprice 200-mL carton = 61pNutritional supplement for the dietary management of phenylketonuriain children over 1 yearMilupa PKU 2-prima c (Milupa)Powder, protein equivalent (essential and non-essentialamino acids except phenylalanine) 60 g, carbohydrate 10 g,fat nil, energy 1190 kJ (280 kcal)/100 g, with vitamins,minerals, and trace elements. Vanilla flavour, net price 500 g= £131.68Nutritional supplement for the dietary management of phenylketonuriain children 1–8 yearsMilupa PKU 2-secunda c (Milupa)Powder, protein equivalent (essential and non-essentialamino acids except phenylalanine) 70 g, carbohydrate 6.8 g,fat nil, energy 1306 kJ (307 kcal)/100 g, with vitamins,minerals, and trace elements. Vanilla flavour, net price 500 g= £153.62Nutritional supplement for the dietary management of phenylketonuriain children 9–15 yearsMilupa PKU 3-advanta c (Milupa)Powder, protein equivalent (essential and non-essentialamino acids except phenylalanine) 70 g, carbohydrate 4.7 g,fat nil, energy 1270 kJ (299 kcal)/100 g, with vitamins,minerals, and trace elements. Vanilla flavour, net price 500 g= £153.62Nutritional supplement for the dietary management of phenylketonuriain children over 15 yearsPhlexy-10 c Exchange System (SHS)Capsules, protein equivalent (essential and non-essentialamino acids except phenylalanine) 416.5 mg/capsule, netprice 200-cap pack = £35.77Tablets, protein equivalent (essential and non-essentialamino acids except phenylalanine) 833 mg tablet, net price75-tab pack = £23.17Drink Mix, powder, protein equivalent (essential and nonessentialamino acids except phenylalanine) 8.33 g, carbohydrate8.8 g/20-g sachet. Apple-black currant, citrus, ortropical flavour, net price 30 20-g sachet = £107.86Nutritional supplement for the dietary management of phenylketonuriaPhlexy-Vits c (SHS)Powder, vitamins, minerals, and trace elements, net price 30 7-g sachets = £60.00Tablets, vitamins, minerals, and trace elements, net price180-tab pack = £68.26For use as a vitamin and mineral component of restricted therapeuticdiets in children over 11 years and adults with phenylketonuriaand similar amino acid abnormalitiesPK Aid 4 c (SHS)Powder, protein equivalent (essential and non-essentialamino acids except phenylalanine) 79 g, carbohydrate 4.5 g,fat nil, energy 1420 kJ (334 kcal)/100 g. Unflavoured,(flavouring: see Modjul c Flavour System, p. 777), net price500 g = £120.24 (5-g measuring scoop provided)Nutritional supplement for the dietary management of phenylketonuriain children and adults