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Protocols - Hemorio

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SUMMARY:<br />

PART I - CLINICAL PROTOCOLS ON HEMATOLOGICAL DISEASES .................................................... 7<br />

SICKLE CELL DISEASE .............................................................................................................................................................................................. 8<br />

MAJOR AND INTERMIDIATE THALASSEMIA ......................................................................................................................................................... 40<br />

HEREDIRATY SPHEROCYTOSIS ............................................................................................................................................................................ 42<br />

G6PD DEFICIENCY ................................................................................................................................................................................................... 44<br />

APLASTIC ANEMIA ................................................................................................................................................................................................... 46<br />

SELFIMMUNE HEMOLYTIC ANEMIA ....................................................................................................................................................................... 48<br />

IMMUNE THROMBOCYTOPENIC PURPURA ........................................................................................................................................................ 51<br />

IMMUNE THROMBOCYTOPENIC PURPURA ........................................................................................................................................................ 52<br />

THROMBOTIC THROMBOCYTOPENIC PURPURA ................................................................................................................................................ 54<br />

HEMORRHAGIC SYNDROME .................................................................................................................................................................................. 56<br />

PAROXYSMAL NOCTURNAL HEMOGLOBINURIA ................................................................................................................................................. 81<br />

GAUCHER DISEASE ................................................................................................................................................................................................. 83<br />

MYELODISPLASIC SYNDROME .............................................................................................................................................................................. 86<br />

ACUTE MYELOID LEUKEMIA ................................................................................................................................................................................... 90<br />

LMA IN CHILDREN AND TEENAGERS .................................................................................................................................................................... 98<br />

CHRONIC MYELOID LEUKEMIA ............................................................................................................................................................................ 103<br />

POLYCYTHEMIA VERA .......................................................................................................................................................................................... 106<br />

ESSENTIAL THROMBOCYTHEMIA ....................................................................................................................................................................... 107<br />

PRIMARY MYELOFIBROSIS .................................................................................................................................................................................. 109<br />

ACUTE LYMPHOID LEUKEMIA .............................................................................................................................................................................. 110<br />

NON-B ACUTE LYMPHOID LEUKEMIA AND LYMPHOBLAST LNH (CHILD) ...................................................................................................... 115<br />

CHRONIC LYMPHOCYTIC LEUKEMIA .................................................................................................................................................................. 120<br />

TRICHOLEUKEMIA ................................................................................................................................................................................................. 124<br />

HODGKIN’S LYMPHOMA ........................................................................................................................................................................................ 125<br />

NON-HODGKIN’S LYMPHOMA .............................................................................................................................................................................. 127<br />

PROGNOSIS – FLIPI CRITERION .......................................................................................................................................................................... 128<br />

LEUKEMIA / T-CELLS LYMPHOMA OF THE ADULT ............................................................................................................................................ 140<br />

FUNGOID MYCOSIS AND SÉZARY SYNDROME ................................................................................................................................................. 141<br />

MULTIPLE MYELOMA ............................................................................................................................................................................................. 144<br />

WALDENSTRON MACROGLOBULINEMIA............................................................................................................................................................ 148<br />

BONE MARROW TRANSPLANT ............................................................................................................................................................................ 149<br />

PART II - TRANSFUSIONAL PROTOCOLS AT THE HEMATOLOGICAL DISEASES .......................... 158<br />

MAIN BLOOD COMPONENTS ................................................................................................................................................................................ 159<br />

TRANSFUSION OF RED BLOOD CELLS, PLATELETS, FROZEN FRESH PLASMA AND GENERAL INDICATIONS ...................................... 162<br />

GENERAL INDICATIONS ........................................................................................................................................................................................ 162<br />

TRANSFUSIONAL INDICATIONS AT THE HEMATOLOGICAL DISEASES ......................................................................................................... 169<br />

SPECIAL PROCEDURES ........................................................................................................................................................................................ 177<br />

TRANSFUSIONAL REACTIONS ............................................................................................................................................................................. 179<br />

HEMOVIGILANCE AND TRANSFUSIONAL COMMITTEE .................................................................................................................................... 183<br />

PRACTICAL ASPECTS OF THE TRANSFUSION .................................................................................................................................................. 183<br />

ATTACHMENTS....................................................................................................................................... 185<br />

ATTACHMENT I – HEMATOLOGICAL CLINICAL SCREENING ........................................................................................................................... 186<br />

ATTACHMENT II – HEMORIO’S DISCHARGE CRITERIA .................................................................................................................................... 193<br />

ATTACHMENT III – HEMATOLOGY SPECIAL TECHNIQUES .............................................................................................................................. 194<br />

ATTACHMENT IV – PAIN APPROACH ROUTINE ................................................................................................................................................. 198<br />

ATTACHMENT V – CHEMOTHERAPY SUBJECTS CARE ................................................................................................................................... 212<br />

ATTACHMENT VI – RENAL AND HEPATIC ADJUSTMENT OF THE MOST USED DRUGS IN HEMATOLOGY ............................................... 213<br />

ATTACHMENT VII – IRON CHELATION ................................................................................................................................................................ 214<br />

ATTACHMENT VIII – SEDATION IN CHILDREN ................................................................................................................................................... 218<br />

ATTACHMENT IX – TRANSFUSION OF PLATELETS CONCENTRATE .............................................................................................................. 219<br />

AT THE HEMORRHAGIC DENGUE ....................................................................................................................................................................... 219

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