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S - Nederlandse Vereniging voor Klinische Neurofysiologie

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viii Inhoudsopgave<br />

9 Het naald EMG . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 69<br />

Machiel Zwarts<br />

9.1 Inleiding.................................................................... 69<br />

9.2 Rustactiviteit ................................................................ 69<br />

9.2.1 Normale rustactiviteit ................................................ 69<br />

9.2.2 Abnormale spontane activiteit ........................................ 70<br />

9.3 Het meten van de MUAP in de praktijk ....................................... 72<br />

9.3.1 EMG-bevindingen nadenervatie/re-innervatie ........................ 76<br />

9.3.2 EMG-bevindingen naspierverlies ..................................... 76<br />

9.4 Praktische aspecten .......................................................... 77<br />

9.4.1 Procedure ........................................................... 77<br />

9.4.2 Pijn ................................................................. 77<br />

9.4.3 Welke spieren? ...................................................... 78<br />

9.4.4 Kinderen............................................................ 78<br />

9.4.5 Valkuilen............................................................ 78<br />

9.5 Conclusie ................................................................... 79<br />

Referenties ........................................................................ 79<br />

10 Diagnostiek van de neuromusculaire overgang: klinische bliken bibbers . . . . . . . . . . . 81<br />

Jan Verschuuren and DénesTavy<br />

10.1 Inleiding.................................................................... 81<br />

10.1.1 Hoe vaak komt myasthenie <strong>voor</strong>? ..................................... 81<br />

10.1.2 Hoe ismyasthenie teherkennen: ptosis en dubbelzien .................. 82<br />

10.1.3 Hoe ismyasthenie teherkennen: ledemaatzwakte ...................... 83<br />

10.2 <strong>Neurofysiologie</strong> bij Myasthenie en LEMS ...................................... 84<br />

10.2.1 Fysiologie Neuromusculaire Synaps................................... 84<br />

10.2.2 Repetitieve zenuwstimulatie.......................................... 84<br />

10.2.3 Single fiber EMG (SFEMG) ........................................... 87<br />

10.3 Onderzoekstrategie.......................................................... 89<br />

10.3.1 Myasthenia Gravis................................................... 89<br />

10.3.2 Lambert Eaton Myastheen Syndroom ................................. 92<br />

Referenties ........................................................................ 94<br />

11 Aan het werk met botulinetoxine . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 97<br />

Hans Koelman en Humphrey Morré<br />

11.1 Inleiding.................................................................... 97<br />

11.2 Indicatiegebieden............................................................ 98<br />

11.2.1 Cervicale dystonie ................................................... 98<br />

11.2.2 Blefarospasme ....................................................... 99<br />

11.2.3 Hemifacialis spasme .................................................100<br />

11.3 Extensor digitorum brevis (EDB)test..........................................100<br />

11.4 Conflicts of interest ..........................................................100<br />

Referenties ........................................................................101<br />

Index .................................................................................103

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