Escalas en Neurología - Sociedade Galega de Neuroloxia

12-ESCALAS (225-262) 3/6/08 12:54 Página 242
I.J. POSADA, J. GONZÁLEZ DE LA ALEJA, J. BENITO-LEÓN, F. BERMEJO PAREJA, P. MARTÍNEZ-MARTÍN
Escala 74c. UNIFIED HUNTINGTON'S DISEASE RATING SCALE
Motor assessment
Ocular pursuit (horizontal and vertical)
Complete (normal) . . . . . . . . . . . . . . . . . . . . 0
Jerky movement . . . . . . . . . . . . . . . . . . . . . . . 1
Interrupted pursuits/full range . . . . . . . . . . 2
Incomplete range . . . . . . . . . . . . . . . . . . . . . 3
Cannot pursue . . . . . . . . . . . . . . . . . . . . . . . . 4
Saccade initiation (horizontal and vertical)
Normal . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 0
Increased latency only . . . . . . . . . . . . . . . . . 1
Suppressable blinks or head movements
to initiate . . . . . . . . . . . . . . . . . . . . . . . . . . . 2
Unsupressable head movements . . . . . . . . 3
Cannot initiate saccades . . . . . . . . . . . . . . . 4
Saccade velocity (horizontal and vertical)
Normal . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 0
Mild slowing . . . . . . . . . . . . . . . . . . . . . . . . . . 1
Moderate slowing . . . . . . . . . . . . . . . . . . . . . 2
Severely slow. full range . . . . . . . . . . . . . . . 3
Incomplete range . . . . . . . . . . . . . . . . . . . . . 4
Dysarthria
Normal . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 0
Unclear, no need to repeat . . . . . . . . . . . . . 1
Must repeat to be understood . . . . . . . . . . 2
Mostly incomprehensible . . . . . . . . . . . . . . 3
Mute . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 4
Tongue protusion
Can hold tongue fully protruded for
10 seconds . . . . . . . . . . . . . . . . . . . . . . . . . . 0
Cannot keep fully protruded for
10 seconds . . . . . . . . . . . . . . . . . . . . . . . . . . 1
Cannot keep fully protruded for
5 seconds . . . . . . . . . . . . . . . . . . . . . . . . . . . 2
Cannot fully protrude tongue . . . . . . . . . . 3
Cannot protrude tongue beyond lips . . . 4
Maximal dystonia (trunk and extremities)
Absent . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 0
Slight/intermittent . . . . . . . . . . . . . . . . . . . . . 1
Mild/common or moderate/intermittent . 2
Moderate/common . . . . . . . . . . . . . . . . . . . . 3
Marked/prolonged . . . . . . . . . . . . . . . . . . . . . 4
Maximal chorea (face, mouth, trunk and extremities)
Absent . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 0
Slight/intermittent . . . . . . . . . . . . . . . . . . . . . 1
Score Score
� 242 �
Mild/common or moderate/intermittent . 2
Moderate/common . . . . . . . . . . . . . . . . . . . . 3
Marked/prolonged . . . . . . . . . . . . . . . . . . . . . 4
Retropulsion pull test
Normal . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 0
Recovers spontaneously . . . . . . . . . . . . . . . 1
Would fall if not caught . . . . . . . . . . . . . . . . 2
Tends to fall spontaneously . . . . . . . . . . . . 3
Cannot stand . . . . . . . . . . . . . . . . . . . . . . . . . 4
Finger taps (right and left)
Normal (≥I 5/5 s) . . . . . . . . . . . . . . . . . . . . . . 0
Mild slowing and or reduction in
amplitude (11-14/5 s) . . . . . . . . . . . . . . . . . 1
Moderately impaired. Definite and
early fatiguing. May have occasional
arrests in movements . . . . . . . . . . . . . . . . 2
Severely impaired. Frequent hesitation
in initiating movements or arrests
in ongoing movements (3-6/5 s) . . . . . . . 3
Can rarely perform the task (0-2/5 s) . . . . 4
Pronate/supinate-hands (right and left)
Normal . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 0
Mild slowing and/or irregular . . . . . . . . . . . 1
Moderate slowing and irregular . . . . . . . . 2
Severe slowing and irregular . . . . . . . . . . . 3
Cannot perform . . . . . . . . . . . . . . . . . . . . . . . 4
Luria (first-hand-palm test)
≥4 in 10 seconds, no cue . . . . . . . . . . . . . . . 0